Pediatric Research

• 

  Publication Venue For

  • DNA methylation in former extremely low birth weight newborns: association with cardiovascular and endocrine function 2021
  • Markers of maternal and infant metabolism are associated with ventricular dysfunction in infants of obese women with type 2 diabetes.  82:768-775. 2017
  • Quality improvement in pediatrics: past, present, and future..  81:156-161. 2017
  • Erratum: Pharmacokinetics and safety of a single intravenous dose of myo-inositol in preterm infants of 23-29 wk (Pediatric Research (2013) 74 (721-729) DOI:10.1038/pr.2013.162).  75:803. 2014
  • CLN3p impacts galactosylceramide transport, raft morphology, and lipid content..  63:625-631. 2008
  • A zebrafish model for the Shwachman-Diamond syndrome (SDS)..  63:348-352. 2008
  • Coronary constriction to angiotensin II is enhanced by endothelial superoxide production in sheep programmed by dexamethasone..  63:370-374. 2008
  • Proteomic biomarkers of intra-amniotic inflammation: relationship with funisitis and early-onset sepsis in the premature neonate..  61:318-324. 2007
  • Neuronal ceroid lipofuscinosis: a common pathway?.  61:146-152. 2007
  • Development and cardiac contractility: cardiac troponin T isoforms and cytosolic calcium in rabbit..  60:276-281. 2006
  • Variations in IBD (ACAD8) in children with elevated C4-carnitine detected by tandem mass spectrometry newborn screening..  60:315-320. 2006
  • A novel inhaled organic nitrate that affects pulmonary vascular tone in a piglet model of hypoxia-induced pulmonary hypertension..  58:531-536. 2005
  • Cyclicity of neonatal sleep behaviors at 25 to 30 weeks' postconceptional age..  57:879-882. 2005
  • Androgen and estrogen treatment, alone or in combination, differentially influences bone maturation and hypothalamic mechanisms that time puberty in the male rhesus monkey (Macaca mulatta)..  57:141-148. 2005
  • Nonspecific interstitial pneumonia, alveolar proteinosis, and abnormal proprotein trafficking resulting from a spontaneous mutation in the surfactant protein C gene..  57:89-98. 2005
  • Reduction in death or moderate/severe disability by whole body hypothermia for hypoxic-ischemic encephalopathy (hie): 340.  58:413. 2005
  • A galactosylceramide binding domain is involved in trafficking of CLN3 from Golgi to rafts via recycling endosomes..  56:449-463. 2004
  • Childhood vaccine development: an overview..  55:347-356. 2004
  • Rare disorders of metabolism with elevated butyryl- and isobutyryl-carnitine detected by tandem mass spectrometry newborn screening..  54:219-223. 2003
  • Developmental pathways in musculoskeletal neoplasia: involvement of the Indian Hedgehog-parathyroid hormone-related protein pathway..  53:539-543. 2003
  • 2002 E. Mead Johnson Award for Research in Pediatrics Lecture: the molecular biology of the anemia of chronic disease: a hypothesis..  53:507-512. 2003
  • Effect of maternal smoking on fetal catecholamine concentrations at birth..  53:119-124. 2003
  • Synergistic effect of influenza a virus on endotoxin-induced mortality in rat pups: a potential model for sudden infant death syndrome..  52:481-490. 2002
  • A pharmacologic and genetic model for investigating the role of the mammalian target of rapamycin in the control of cell growth and proliferation.  51:254A-254A. 2002
  • Analysis and significance of the genetic polymorphism of the glutathione S-transferase P1 gene locus in pediatric tumors.  51:233A-233A. 2002
  • Apolipoprotein E 3/3 genotype is protective against severe brain injury but not retinopathy of prematurity in premature infants.  51:367A-367A. 2002
  • Bronchiolitis management preferences and the influence of pulse oximetry and respiratory rate on the decision to admit.  51:100A-100A. 2002
  • Effects of a metalloporphyrin catalytic antioxidant in a murine model of closed head injury.  51:48A-48A. 2002
  • Longitudinal study of the progression of secondary sexual characteristics in children with cerebral palsy.  51:26A-26A. 2002
  • Stability of nutrition and growth in children with moderate/severe cerebral palsy.  51:438A-438A. 2002
  • American Pediatric Society Presidential Address 2000: reflections on the 20th and 21st centuries..  51:119-123. 2002
  • American Pediatric Society John Howland Award 2000: acceptance. A mentor's joys and responsibilities..  49:725-727. 2001
  • Safety and efficacy of succimer in toddlers with blood lead levels of 20-44 microg/dL. Treatment of Lead-Exposed Children (TLC) Trial Group..  48:593-599. 2000
  • Glucose-6-phosphatase mutation G188R confers an atypical glycogen storage disease type 1b phenotype..  48:329-334. 2000
  • 2-Methylbutyryl-coenzyme A dehydrogenase deficiency: a new inborn error of L-isoleucine metabolism..  47:830-833. 2000
  • Clinical and molecular diagnosis of Nager syndrome in a preterm infant (27 week gestation) - A case report.  47:81A-81A. 2000
  • Office Preparedness for Pediatric Emergencies: A randomized controlled trial of an office-based training program.  47:104A-104A. 2000
  • Overexpression of four anti-apoptotic genes in association with resistance to apoptosis observed in bone marrow failure syndromes.  47:254A-254A. 2000
  • Oxygenation and pulmonary hypertension improve at varying rates with inhaled nitric oxide (NO) in a piglet model of acute respiratory distress syndrome (ARDS).  47:370A-370A. 2000
  • Prenatal oxygen tension regulates the expression and localization of extracellular superoxide dismutase in neonatal rabbit lungs.  47:477A-477A. 2000
  • Prenatal exposure to toluene results in abnormal neurogenesis and migration in rat somatosensory cortex..  47:362-368. 2000
  • Constitutive expression of placental lactogen in pancreatic beta cells: effects on cell morphology, growth, and gene expression..  47:136-142. 2000
  • Diagnosis of mitochondrial trifunctional protein deficiency in a blood spot from the newborn screening card by tandem mass spectrometry and DNA analysis..  46:45-49. 1999
  • Extracellular Superoxide Dismutase Secretion and Activity during Development.  45:44A-44A. 1999
  • Integration of Clinical Decision Support with On-Line Encounter Documentation for Well Child Care at the Point of Care.  45:130A-130A. 1999
  • Nicotine and/or cocaine alters postnatal ventilatory control in the rat pup gestationally exposed.  45:51A-51A. 1999
  • Virologic and CD4 Response to Treatment with Nelfinavir in Therapy Experienced, Protease Inhibitor Naive HIV-Infected Children: 48 Week Follow-Up.  45:168A-168A. 1999
  • Persistent c-fos induction by nicotine in developing rat brain regions: interaction with hypoxia..  45:38-45. 1999
  • T cell activation deficiency associated with an aberrant pattern of protein tyrosine phosphorylation after CD3 perturbation in Down's syndrome..  44:252-258. 1998
  • Recombinant human acid alpha-glucosidase corrects acid alpha-glucosidase-deficient human fibroblasts, quail fibroblasts, and quail myoblasts..  43:374-380. 1998
  • A critical period for the role of thyroid hormone in development of renal alpha-adrenergic receptors..  42:93-102. 1997
  • Neuronal control of cardiac and hepatic macromolecule synthesis in the neonatal rat: effects of sympathectomy..  41:359-363. 1997
  • Effects of treatment with pentoxifylline on the cardiovascular manifestations of group B streptococcal sepsis in the piglet..  40:469-474. 1996
  • Development of a rat model of toluene-abuse embryopathy..  40:82-87. 1996
  • Atypical regulation of hepatic adenylyl cyclase and adrenergic receptors during a critical developmental period: agonists evoke supersensitivity accompanied by failure of receptor down-regulation..  39:697-707. 1996
  • Effects of ATP-magnesium chloride on the cardiopulmonary manifestations of group B streptococcal sepsis in the piglet..  39:609-615. 1996
  • Human severe combined immunodeficiency (SCID): Genetic, phenotypic and functional diversity in 95 infants..  39:41-41. 1996
  • Stavudine (D4T, ZERIT(TM)) sensitivities in clinical HIV isolates obtained from a pediatric population..  39:1029-1029. 1996
  • Effects of environmental tobacco smoke exposure in utero and/or postnatally on brain development..  39:494-498. 1996
  • Neurokinin subtype receptors mediating substance P contraction in immature rabbit airways..  39:120-126. 1996
  • Effect of an interleukin-1 receptor antagonist on the hemodynamic manifestations of group B streptococcal sepsis..  38:704-708. 1995
  • Oral transforming growth factor-alpha enhances jejunal mucosal recovery and electrical resistance in piglet rotavirus enteritis..  38:173-181. 1995
  • DIFFERENTIATION AMONG MYCOBACTERIUM-AVIUM COMPLEX STRAINS BY AUTOMATED SEQUENCING OF THE HSP63-GENE.  37:A189-A189. 1995
  • HEMATOLOGIC EFFECTS OF HIV-INFECTION IN CHILDREN LESS-THAN 2 YEARS OLD.  37:A183-A183. 1995
  • LONG-TERM SURVIVAL IN PEDIATRIC HIV.  37:A178-A178. 1995
  • PRENATAL COCAINE AND NICOTINE EXPOSURE IN RATS - EFFECTS ON LONG-TERM COGNITIVE OUTCOME AND SEXUAL-DIFFERENTIATION.  37:A14-A14. 1995
  • The effects of high-dose toluene on embryonic development in the rat..  36:811-815. 1994
  • Erythroid transcription factor NF-E2 coordinates hemoglobin synthesis..  36:419-423. 1994
  • Prenatal dexamethasone exposure causes loss of neonatal hypoxia tolerance: cellular mechanisms..  35:515-522. 1994
  • AN ASSOCIATION BETWEEN HIV-INFECTION, EPSTEIN-BARR-VIRUS (EBV) IMMUNE STATUS, CARDIOMYOPATHY, AND LYMPHOCYTIC INTERSTITIAL PNEUMONIA (LIP).  35:A199-A199. 1994
  • DECREASED RECOMBINATION IN OOGENESIS IN A FAMILY WITH A LARGE PERICENTRIC X-CHROMOSOME INVERSION.  35:A154-A154. 1994
  • MARKERS PROGNOSTIC FOR SURVIVAL IN ZIDOVUDINE TREATED, HIV-INFECTED CHILDREN.  35:A187-A187. 1994
  • PATENT DUCTUS-ARTERIOSUS IN PREMATURE-INFANTS GREATER-THAN 2 WEEKS OF AGE - UTILITY OF ECHOCARDIOGRAPHIC EXAMINATION.  35:A218-A218. 1994
  • POLYCLONAL MATERNAL T-LYMPHOCYTES ARE PRESENT IN INFANTS WITH SEVERE COMBINED IMMUNODEFICIENCY (SCID) PRIOR TO BONE-MARROW TRANSPLANTATION (BMT).  35:A11-A11. 1994
  • Intravenous L-carnitine and acetyl-L-carnitine in medium-chain acyl-coenzyme A dehydrogenase deficiency and isovaleric acidemia..  35:96-101. 1994
  • Brainstem bilirubin toxicity in the newborn primate may be promoted and reversed by modulating PCO2..  34:6-9. 1993
  • Enzyme Replacement Therapy with Polyethylene Glycol-Adenosine Deaminase in Adenosine Deaminase Deficiency: Overview and Case Reports of Three Patients, Including Two Now Receiving Gene Therapy.  33:S42-S48. 1993
  • Development of gene therapy for immunodeficiency: adenosine deaminase deficiency..  33:S49-S53. 1993
  • Enzyme replacement therapy with polyethylene glycol-adenosine deaminase in adenosine deaminase deficiency: Overview and case reports of three patients, including two now receiving gene therapy.  33:S42-S48. 1993
  • Enzyme replacement therapy with polyethylene glycol-adenosine deaminase in adenosine deaminase deficiency: overview and case reports of three patients, including two now receiving gene therapy..  33:S42-S47. 1993
  • Molecular dissection of lymphocyte signal transduction pathways..  33:S9-13. 1993
  • T-cell abnormalities in common variable immunodeficiency..  33:S24-S27. 1993
  • Binding of placental lactogen and growth hormone to fetal sheep fibroblasts..  32:200-203. 1992
  • Effects of pentoxifylline on the cardiovascular manifestations of group B streptococcal sepsis in the piglet..  31:596-600. 1992
  • Effect of cyclooxygenase inhibition on retinal and choroidal blood flow during hypercarbia in newborn piglets..  31:127-130. 1992
  • Hypercalciuria due to combined growth hormone and calcitriol therapy in uremia: effects of growth hormone on mineral homeostasis in 75% nephrectomized weanling rats..  30:528-533. 1991
  • Effects of nursing on growth and development of small bowel mucosa in newborn piglets..  30:337-341. 1991
  • CD-4+ LYMPHOCYTES IN CHILDREN UNDER 2-YEARS OLD - ESTABLISHMENT OF NORMAL VALUES IN A POPULATION AT RISK FOR HIV AND PROGNOSTIC APPLICATION TO INFECTED CHILDREN.  29:A178-A178. 1991
  • HEMATOLOGIC ABNORMALITIES IN HUMAN-IMMUNODEFICIENCY-VIRUS (HIV) INFECTED CHILDREN AND NONINFECTED BUT HIV ANTIBODY POSITIVE CONTROLS.  29:A178-A178. 1991
  • ISOLATION OF IMMATURE HEMATOPOIETIC PROGENITOR CELLS (HPC) FROM HUMAN UMBILICAL-CORD BLOOD (UCB).  29:A139-A139. 1991
  • NEURODEVELOPMENTAL (ND) EFFECTS OF PEDIATRIC HIV-INFECTION AND TREATMENT WITH ORAL ZIDOVUDINE.  29:A181-A181. 1991
  • THE ROLE OF HOSPITAL BASED MICROCOMPUTERS IN A STATEWIDE NEONATAL SCREENING-PROGRAM.  29:A254-A254. 1991
  • Comparison of red cell transfusion and polyethylene glycol-modified adenosine deaminase therapy in an adenosine deaminase-deficient child: measurement of erythrocyte deoxyadenosine triphosphate as a useful tool..  28:127-130. 1990
  • MELPHALAN (L-PAM)-INDUCED TOXICITY IN NUDE-MICE PRETREATED WITH BUTHIONINE SULFOXIMINE (BSO).  27:A150-A150. 1990
  • NUCLEAR FACTOR BINDING-SITES IN THE INTERLEUKIN (IL-3) PROMOTER.  27:A138-A138. 1990
  • THE EPIDEMIOLOGIC INTERSECTION IN CHILDREN OF SEXUAL ABUSE AND AIDS.  27:A172-A172. 1990
  • Undernutrition and overnutrition in the neonatal rat: long-term effects on noradrenergic pathways in brain regions..  27:191-197. 1990
  • Antibody-dependent cell-mediated cytotoxicity (ADCC) in HIV-1 infected pregnant-women.  27:A186-A186. 1990
  • Effects of prenatal dexamethasone or terbutaline exposure on development of neural and intrinsic control of heart rate..  26:554-557. 1989
  • The effects of exogenous rat growth hormone therapy on growth of uremic rats fed an 8% protein diet..  26:204-207. 1989
  • Effects of prenatal terbutaline exposure on cellular development in lung and liver of neonatal rat: ornithine decarboxylase activity and macromolecules..  25:617-622. 1989
  • EXPRESSION OF EARLY ACTIVATION ANTIGEN, EA-1, ON HUMAN-FETAL AND POST-NATAL THYMUS.  25:A164-A164. 1989
  • Processing of one-chain to two-chain renin in the mouse submandibular gland is influenced by androgen..  25:332-335. 1989
  • Short-chain acyl-coenzyme A dehydrogenase deficiency in mice..  25:38-43. 1989
  • Nutritional influences on adrenal chromaffin cell development: comparison with central neurons..  24:583-587. 1988
  • Effects of prenatal dexamethasone on development of ornithine decarboxylase activity in brain and peripheral tissues of rats..  24:465-469. 1988
  • Neonatal nutritional deprivation or enhancement: the cardiac-sympathetic axis and its role in cardiac growth and stress responses..  23:423-427. 1988
  • Biochemical determinants of growth sparing during neonatal nutritional deprivation or enhancement: ornithine decarboxylase, polyamines, and macromolecules in brain regions and heart..  22:599-604. 1987
  • Cysteine and glutathione levels in developing rat kidney and liver..  22:605-608. 1987
  • Epidermal growth factor (EGF)-like transforming growth factor (TGF) activity and EGF receptors in ovine fetal tissues: possible role for TGF in ovine fetal development..  22:609-615. 1987
  • Effect of cyclooxygenase and lipoxygenase products on pulmonary function in group B streptococcal sepsis..  22:478-482. 1987
  • Alterations of surfactant pools in fetal and newborn rat lungs..  21:5-9. 1987
  • Effects of a leukotriene antagonist on the early hemodynamic manifestations of group B streptococcal sepsis in piglets..  20:1004-1008. 1986
  • Developmental aspects of cystine transport in the dog..  20:593-597. 1986
  • A COMMON TRANSDUCTION PATHWAY FOR LEUKOCYTE CHEMOATTRACTANT RECEPTORS - PHOSPHOLIPASE-C ACTIVATION BY A GUANINE-NUCLEOTIDE REGULATORY PROTEIN.  20:A325-A325. 1986
  • CELL-MEDIATED IMMUNE (CMI) RESPONSE TO ECHOVIRUS 12 (E12) INFECTION IN HUMANS.  20:A297-A297. 1986
  • CLINICAL SUMMARY OF 41 PATIENTS WITH CHRONIC ENTEROVIRAL MENINGOENCEPHALITIS AND AGAMMAGLOBULINEMIA (CEMA).  20:A316-A316. 1986
  • ELEVATED TROUGH AMIKACIN CONCENTRATIONS IN INFANTS LESS-THAN 1000 GRAMS.  20:A203-A203. 1986
  • EXPRESSION OF GENE DEFECT IN X-LINKED AGAMMAGLOBULINEMIA (XLA) IS INTRINSIC TO THE B-CELL LINEAGE.  20:A301-A301. 1986
  • MONOCLONAL-ANTIBODIES TO T11, LFA-2, AND LFA-3 ANTIGENS INHIBIT BINDING OF HUMAN THYMOCYTES TO AUTOLOGOUS THYMIC EPITHELIAL-CELLS.  20:A303-A303. 1986
  • SUBDURAL EMPYEMA (SE) COMPLICATING BACTERIAL-MENINGITIS (MEN).  20:A308-A308. 1986
  • THE USE OF INTRAVENOUS IMMUNOGLOBULIN (IVIG) PREPARATIONS IN THE TREATMENT OF CHRONIC ENTEROVIRAL INFECTIONS.  20:A297-A297. 1986
  • Influence of an antagonist of slow-reacting substance of anaphylaxis on the cardiovascular manifestations of hypoxia in piglets..  19:1201-1205. 1985
  • Diagnostic and therapeutic implications of medium-chain acylcarnitines in the medium-chain acyl-coA dehydrogenase deficiency..  19:459-466. 1985
  • 1086 LONGITUDINAL ASSESSMENT OF ANTIBODY RESPONSE OF CHILDREN WITH RENAL DISEASE TO PNEUMOCOCCAL VACCINE.  19:291A-291A. 1985
  • 1087 USE OF A MICOCOMPUTER IN A DIAGNOSTIC VIROLOGY LABORATORY.  19:292A-292A. 1985
  • 1110 URINARY TRACT INFECTIONS IN CEREBRAL PALSY PATIENTS.  19:295A-295A. 1985
  • 1140 THE EFFECT OF AN ANTIVIRAL AGENT (WIN 51,711) ON COXSACKIEVIRUS A9 INFECTION IN SUCKLING MICE.  19:300A-300A. 1985
  • 960 DEVELOPMENT OF IMMUNITY IN SEVERE PRIMARY T CELL DEFICIENCY FOLLOWING HAPLOIDENTICAL STEM CELL TRANSPLANTATION.  19:270A-270A. 1985
  • SUCCESSFUL TREATMENT OF AUTOIMMUNE HEMOLYTIC-ANEMIA (AIHA) IN COMMON VARIABLE IMMUNODEFICIENCY (CVID) WITH HIGH-DOSE INTRAVENOUS IMMUNE GLOBULIN (IVIG).  19:A278-A278. 1985
  • The effect of calcium antagonists on hypoxic pulmonary hypertension in the piglet..  18:1262-1265. 1984
  • Cardiovascular changes in group B streptococcal sepsis in the piglet: response to indomethacin and relationship to prostacyclin and thromboxane A2..  18:874-878. 1984
  • Developmental aspects of sugar transport by isolated dog renal cortical tubules..  18:719-723. 1984
  • Resistance of the male gonad to a high galactose diet..  18:345-348. 1984
  • Growth, morphology, and chemotherapeutic response of medulloblastoma (MBT) in athymic mice.  16. 1982
  • Pharmacokinetic properties of thiopental in the asphyxiated neonate.  16. 1982
  • Unique sensitivity of HB Zurich to oxidative injury by phenazopyridine: Reversal of the effect by elevating carboxyhemoglobin levels in vivo and in vitro.  16. 1982
  • 1225 AN ASSOCIATION BETWEEN BRACHYCEPHALY & EUSTACHIAN TUBE (ET) DYSFUNCTION.  15:647-647. 1981
  • 1467 CREATINE KINASE BRAIN ISOENZYME CONCENTRATION CKBB IN CEREBROSPINAL FLUID(CSF) OF NEWBORNS.  15:687-687. 1981
  • 967 EFFECTS HYDROCORTISONE AND THEOPHYLLINE CN MONONUCLEAR CELL SUPERNATANT IgE CONCENTRATIONS.  15:603-603. 1981
  • Effects of hydrocortisone and theophylline on mononuclear cell supernatant IgE concentrations.  15:967. 1981
  • Effects of arginine infusion in homocystinuria.  14. 1980
  • HEAD CIRCUMFERENCE-(HC) AT BIRTH AND GROWTH AT 6 WEEKS AS PREDICTORS OF DEVELOPMENTAL OUTCOME IN VERY LOW BIRTHWEIGHT-(VLBW) INFANTS.  14:434-434. 1980
  • Methotrexate therapy for relapsed acute lymphocytic leukemia (ALL).  14. 1980
  • Nephropathic cystinosis: Management with cysteamine.  14. 1980
  • Urinary clearance of amylase in children treated with L-asparaginase.  14. 1980
  • ELEVATED IMMUNOGLOBULIN IGA IN MILK FROM MOTHERS DELIVERING PRETERM INFANTS.  13:449-449. 1979
  • Effects of actinomycin D therapy (AMD) on polymorphonuclear (PMN) leukocyte chemotactic activity.  13. 1979
  • Iron deficiency (Fe Def): Alterations in red blood cell deformability and membrane pitting.  13. 1979
  • O2 consumption of premature infants in the first 10 weeks of life: The responses to transfusion (Tx).  13. 1979
  • Primaquine induced hemolysis in glucose-6-phosphate dehydrogenase (G6PD) deficiency, effect of vitamin E.  13. 1979
  • Aspirin-induced hemolysis: the role of concomitant oxidant (H2O2) challenge..  12:927-931. 1978
  • 702 EVIDENCE FOR EXCESSIVE T SUPPRESSOR CELL ACTIVITY IN X-LINKED IMMUNODEFICIENCY WITH HYPER-IgM.  12:480-480. 1978
  • Aspirin (ASA) and hydrogen peroxide (H2O2 induced red blood cell injury, membrane protein alterations.  12. 1978
  • Effects of cholestyramine on small intestinal mucosa.  12. 1978
  • Unilateral optic nerve disease, a complication of chemotherapy of acute lymphatic leukemia (ALL).  12. 1978
  • Gamma cisternography: determination of adequacy of intrathecal therapy in leukemic disease.  11. 1977
  • OPTIMAL CONDITIONS TO AVOID SELECTIVE LOSSES OF T CELLS ON BOUYANT DENSITY GRADIENTS.  10:383-383. 1976
  • Aspirin (ASA) induced hemolysis: the need for concomitant oxidant (H2O2) challenge.  9. 1975
  • FETAL LIVER-TRANSPLANTATION IN SEVERE COMBINED IMMUNODEFICIENCY (SCID) - SUCCESS AND GRAFT VERSUS HOST (G-V-H) DISEASE.  9:336-336. 1975
  • PROLONGED CNS VIRAL-INFECTION WITH ECHO 30 IN AN AGAMMAGLOBULINEMIC CHILD WITH INTACT CELL-MEDIATED-IMMUNITY.  9:336-336. 1975
  • Jet injection of local anesthesia for bone marrow aspirations.  8:409. 1974
  • Vincristine (VCR) therapy and inappropriate antidiuretic hormone secretion.  8:410. 1974
  • Hereditary alterations in the immune response: coexistence of "agammaglobulinemia", acquired hypogammaglobulinemia and selective immunoglobulin deficiency in a sibship..  2:72-84. 1968
  • Early gestation dexamethasone-exposure programs tissue-specific alterations in reactive oxygen species production 2005
  • Early Gestation Dexamethasone Exposure Alters Coronary Artery Reactivity in Newborn Lambs. 2004
  • An organic nitrate affects pulmonary function and regulates pulmonary vascular tone 2004
  • Apolipoprotein E-mimetic peptide reduces brain injury in a neonatal hypoxia-ischemia model 2004
  • Coronary Artery NAD(P)H oxidase expression and superoxide anion production is enhanced by early gestation glucocorticoid exposure 2004
  • Early gestation glucocorticoid exposure enhances postnatal coronary artery vasoconstriction 2004
  • Improved neuro-developmental outcomes following long-term suppressive oral acyclovir in infants with disseminated/encephalitic herpes simplex disease 2004
  • International formula-based nutritional intervention for infants born to HIV-infected women 2004
  • International formula-based nutritional intervention for infants born to HIV-infected women 2004
  • Mortality following blood culture in premature infants: Increased with Gram-negative bacteremia and candidemia, but not Gram-positive bacteremia 2004
  • Nonfebrile provoked seizures: A unique seizure category? 2004
  • Polysomnogram findings in Pompe disease 2004
  • Proof of principle: Globoid cell leukodystrophy late onset: Effective therapeutic intervention in disease course by use of hematopoietic stem cell transplantation 2004
  • Pulmonary function findings in Pompe disease 2004
  • Resolution of proteinuda using Enalapril and hydroxyurea in pediatric patientswith sickle nephropathy 2004
  • Programming of coronary artery dysfunction by early gestation dexamethasone exposure 2003
  • "Does this child have Acute Otitis Media (AOM)?" - An evidence-based appraisal of clinical diagnosis 2003
  • Development of a hybrid adenovirus/adeno-associated virus vector for gene therapy in glycogen storage disease type II 2003
  • Empirical therapy for neonatal candidemia: Evaluation of 21,233 blood cultures 2003
  • Factors affecting early neurobehavioral and sleep outcomes in preterm infants 2003
  • Hospitalization trends among pediatric patients with HIV infection and acquired immunodeficiency syndrome 2003
  • Pelger-Huet anomaly in a child with 1q42.3-44 deletion 2003
  • Pulmonary vasoconstriction to alpha(1)-adrenergic receptors inhibited by S-nitroglutathione 2003
  • Smoking and parents: Convincing parents to quit 2002
  • Smoking and parents: What do they know? 2002
  • A novel SIV vaccine based on Venezuelan equine encephalitis virus (VEE) replicons 2000
  • Assessment of Psychiatric Comorbidity in Children Infected with Human Immunodeficiency Virus, Type 1 1999
  • Prenatal Exposure to Toluene Results in Abnormal Neuronal Proliferation and Migration 1999
  • RV contractility and pulmonary vascular mechanics: Effects of catecholamines in an immature animal model of RV injury. 1996
  • CARNITINE ACYLCARNITINE TRANSLOCASE DEFICIENCY - BENIGN COURSE WITHOUT CARDIAC INVOLVEMENT 1995
  • EFFECTS OF ENVIRONMENTAL TOBACCO-SMOKE EXPOSURE IN-UTERO AND OR POSTNATALLY ON BRAIN-DEVELOPMENT 1995
  • NONSENSE MUTATIONS DESTABILIZE ADA MESSENGER-RNA TRANSCRIPTS AT THE NUCLEAR-LEVEL 1995
  • AUTISTIC BEHAVIORS OF YOUNG GIRLS WITH FRAGILE X-SYNDROME 1994
  • GENE-THERAPY FOR NEONATES WITH ADENOSINE-DEAMINASE (ADA) DEFICIENT SCID BY RETROVIRAL-MEDIATED TRANSFER OF THE HUMAN ADA CDNA INTO UMBILICAL-CORD CD34+ CELLS 1994
  • THE EFFECT OF INSPIRATORY TIME ON CARDIOPULMONARY INTERACTIONS IN A NORMAL AND INJURED LUNG MODEL 1994
  • TRANSPORT EFFICIENCY IS AN INDICATOR OF INCREASED RIGHT-VENTRICULAR WORK IN A LUNG INJURY MODEL 1994
  • ENZYME REPLACEMENT THERAPY WITH POLYETHYLENE GLYCOL-ADENOSINE DEAMINASE IN ADENOSINE-DEAMINASE DEFICIENCY - OVERVIEW AND CASE-REPORTS OF 3 PATIENTS, INCLUDING 2 NOW RECEIVING GENE-THERAPY 1993
  • DEVELOPMENT OF AN ANIMAL-MODEL OF TOLUENE EMBRYOPATHY (FETAL SOLVENTS SYNDROME) 1991
  • ABERRANT BEHAVIORS OF YOUNG BOYS WITH FRAGILE X-SYNDROME 1990
  • COMBINED USE OF SITE DIRECTED MUTAGENESIS AND POLYETHYLENE-GLYCOL (PEG) MODIFICATION TO DEVELOP ENZYME THERAPY FOR METABOLIC DISORDERS 1990
  • IMMUNE-RESPONSE TO POLYETHYLENE GLYCOL-MODIFIED BOVINE ADENOSINE-DEAMINASE (PEG-ADA) 1990
  • SELF LIMITED THROMBOCYTOPENIA IN A PATIENT TREATED WITH POLYETHYLENE-GLYCOL (PEG) MODIFIED ADENOSINE-DEAMINASE (ADA) 1990
  • SUPPRESSION OF AN INHIBITORY ANTIBODY TO BOVINE ADENOSINE-DEAMINASE (ADA) AND IMPROVED CELLULAR-IMMUNITY FOLLOWING INTRAVENOUS IMMUNOGLOBULIN AND PREDNISONE IN A SCID-ADA DEFICIENT CHILD RECEIVING POLYETHYLENE-GLYCOL-ADA (PEG-ADA) 1990
  • 54 ADENOSINE DEAMINASE (ADA) EXPRESSED AT HIGH LEVEL IN T LYMPHOCYTES OF A PATIENT WITH ADA DEFICIENCY AND SEVERE COMBINED IMMUNE DEFICIENCY DISEASE (SCID) 1988
  • A HIERARCHY OF T-CELL GENE REARRANGEMENTS IS PRESENT IN LEUKEMIAS OF THE T-CELL SERIES 1986
  • A LYMPHOHEMATOPOIETIC STEM CELL MODEL FOR ADENOSINEDEAMINASE (ADA) DEFICIENCY: 105 1985
  • HEMOLYTIC ANEMIA AND LOW RED CELL ATP/dATP RATIO IN GENETIC ADENOSINE DEAMINASE DEFICIENCY: 86 1985