Granulomatous Disease, Chronic

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  Subject Areas on Research

  • Activation of monocyte and granulocyte antibody-dependent cytotoxicity by phorbol myristate acetate. 
  • Allogeneic Hematopoietic Cell Transplantation for Chronic Granulomatous Disease: Controversies and State of the Art. 
  • Anterior uveitis following collagen crosslinking in a patient with X-linked chronic granulomatous disease. 
  • Burkholderia glumae infection in an infant with chronic granulomatous disease. 
  • Chronic Granulomatous Disease-Associated IBD Resolves and Does Not Adversely Impact Survival Following Allogeneic HCT. 
  • Chronic granulomatous disease. Report on a national registry of 368 patients. 
  • Concentrated RD114-pseudotyped MFGS-gp91phox vector achieves high levels of functional correction of the chronic granulomatous disease oxidase defect in NOD/SCID/beta -microglobulin-/- repopulating mobilized human peripheral blood CD34+ cells. 
  • Correction of chronic granulomatous disease after second unrelated-donor umbilical cord blood transplantation. 
  • Enhanced bactericidal activity of phagocytes from patients with chronic granulomatous disease in the presence of sulphisoxazole. 
  • Fungal infection in chronic granulomatous disease. The importance of the phagocyte in defense against fungi. 
  • Immunodeficiency diseases. 
  • Inefficient dystrophin expression after cord blood transplantation in Duchenne muscular dystrophy. 
  • Inflammasomes Coordinate Pyroptosis and Natural Killer Cell Cytotoxicity to Clear Infection by a Ubiquitous Environmental Bacterium. 
  • Low-dose total-body irradiation and alemtuzumab-based reduced-intensity conditioning regimen results in durable engraftment and correction of clinical disease among children with chronic granulomatous disease. 
  • Lymphocyte reconstitution following non-myeloablative hematopoietic stem cell transplantation follows two patterns depending on age and donor/recipient chimerism. 
  • Mechanisms of regulating the respiratory burst in leukocytes. 
  • Myeloablative transplantation using either cord blood or bone marrow leads to immune recovery, high long-term donor chimerism and excellent survival in chronic granulomatous disease. 
  • Patients with chronic granulomatous disease have a reduced peripheral blood memory B cell compartment. 
  • Psychrobacter immobilis septicemia in a boy with X-linked chronic granulomatous disease and fulminant hepatic failure. 
  • Pulmonary coin lesion caused by Neisseria mucosa in a child with chronic granulomatous disease. 
  • Pulmonary complications of primary immunodeficiencies. 
  • Stem-cell transplantation for chronic granulomatous disease. 
  • Successful renal transplantation in patients with chronic granulomatous disease. 
  • The role of superoxide anion generation in phagocytic bactericidal activity. Studies with normal and chronic granulomatous disease leukocytes. 
  • Treatment of chronic granulomatous disease with nonmyeloablative conditioning and a T-cell-depleted hematopoietic allograft. 
  • Voriconazole in the treatment of aspergillosis, scedosporiosis and other invasive fungal infections in children. 
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  Keywords of People

  • Buckley, Rebecca Hatcher, James Buren Sidbury Distinguished Professor Emeritus of Pediatrics, in the School of Medicine, Pediatrics, Allergy and Immunology