alpha 1-Antitrypsin Deficiency

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  Subject Areas on Research

  • Alpha 1-antitrypsin deficiency and pregnancy. 
  • Alpha-1-antitrypsin globules in hepatocytes of elderly persons with liver disease. 
  • Deficiency of α-1-antitrypsin influences systemic iron homeostasis. 
  • Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration. 
  • Increased production of sonic hedgehog by ballooned hepatocytes. 
  • Neutrophil elastase increases airway epithelial nonheme iron levels. 
  • Pathophysiology of Alpha-1 Antitrypsin Lung Disease. 
  • Survival after lung transplantation in recipients with alpha-1-antitrypsin deficiency compared to other forms of chronic obstructive pulmonary disease: a national cohort study.