A 13-year-old boy is being evaluated for syncope. At the time of the syncopal event, he was a national, junior tennis champion, but had recently complained of increased fatigue and shortness of breath while playing tennis. One month previously, his brother collapsed and died suddenly while running in his driveway at home. The patient's paternal grandfather had also died suddenly just days before his brother. The 13-year-old boy's ECG is shown below (Fig. 130.1). Representative echocardiographic images are also shown (Figs. 130.2 and 130.3). Of note, there was no LV outflow obstruction noted at rest or with provocative maneuvers What is your diagnosis? What is an appropriate management strategy? © Springer-Verlag London Limited 2011.
Sawyer, TJ; Hall, BW; Daubert, JP
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