Dermatofibrosarcoma protuberans, version 1.2014.


Journal Article

Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors.

Full Text

Cited Authors

  • Bichakjian, CK; Olencki, T; Alam, M; Andersen, JS; Berg, D; Bowen, GM; Cheney, RT; Daniels, GA; Glass, LF; Grekin, RC; Grossman, K; Ho, AL; Lewis, KD; Lydiatt, DD; Morrison, WH; Nehal, KS; Nelson, KC; Nghiem, P; Perlis, CS; Shaha, AR; Thorstad, WL; Tuli, M; Urist, MM; Wang, TS; Werchniak, AE; Wong, SL; Zic, JA; McMillian, N; Hoffman, K; Ho, M

Published Date

  • June 2014

Published In

Volume / Issue

  • 12 / 6

Start / End Page

  • 863 - 868

PubMed ID

  • 24925197

Pubmed Central ID

  • 24925197

Electronic International Standard Serial Number (EISSN)

  • 1540-1413

International Standard Serial Number (ISSN)

  • 1540-1405

Digital Object Identifier (DOI)

  • 10.6004/jnccn.2014.0081


  • eng