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Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery?

Publication ,  Journal Article
Robich, MP; Stewart, RD; Zahka, KG; Krasuski, RA; Hanna, M; Blackstone, EH; Pettersson, GB
Published in: World J Pediatr Congenit Heart Surg
January 2016

Two cases of Shone syndrome with severe mitral and aortic valve problems and pulmonary hypertension were referred for heart-lung transplantation. Severely elevated pulmonary vascular resistance (PVR) was confirmed as was severe periprosthetic mitral and aortic regurgitation. Based on the severity of the valve lesions in both patients, surgery was decided upon and undertaken. Both experienced early pulmonary hypertensive crises, one more than the other, that gradually subsided, followed by excellent recovery and reversal of pulmonary hypertension and PVR. These cases illustrate Braunwald's concept that pulmonary hypertension secondary to left-sided valve disease is reversible.

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Published In

World J Pediatr Congenit Heart Surg

DOI

EISSN

2150-136X

Publication Date

January 2016

Volume

7

Issue

1

Start / End Page

100 / 103

Location

United States

Related Subject Headings

  • Young Adult
  • Vascular Resistance
  • Syndrome
  • Mitral Valve Stenosis
  • Male
  • Lung Transplantation
  • Hypertension, Pulmonary
  • Humans
  • Heart Valve Prosthesis Implantation
  • Heart Transplantation
 

Citation

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MLA
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Robich, M. P., Stewart, R. D., Zahka, K. G., Krasuski, R. A., Hanna, M., Blackstone, E. H., & Pettersson, G. B. (2016). Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery? World J Pediatr Congenit Heart Surg, 7(1), 100–103. https://doi.org/10.1177/2150135115577671
Robich, Michael P., Robert D. Stewart, Kenneth G. Zahka, Richard A. Krasuski, Mazen Hanna, Eugene H. Blackstone, and Gosta B. Pettersson. “Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery?World J Pediatr Congenit Heart Surg 7, no. 1 (January 2016): 100–103. https://doi.org/10.1177/2150135115577671.
Robich MP, Stewart RD, Zahka KG, Krasuski RA, Hanna M, Blackstone EH, et al. Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery? World J Pediatr Congenit Heart Surg. 2016 Jan;7(1):100–3.
Robich, Michael P., et al. “Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery?World J Pediatr Congenit Heart Surg, vol. 7, no. 1, Jan. 2016, pp. 100–03. Pubmed, doi:10.1177/2150135115577671.
Robich MP, Stewart RD, Zahka KG, Krasuski RA, Hanna M, Blackstone EH, Pettersson GB. Two Cases of Late Shone Syndrome With Pulmonary Hypertension: Heart-Lung Transplant or Valve Surgery? World J Pediatr Congenit Heart Surg. 2016 Jan;7(1):100–103.

Published In

World J Pediatr Congenit Heart Surg

DOI

EISSN

2150-136X

Publication Date

January 2016

Volume

7

Issue

1

Start / End Page

100 / 103

Location

United States

Related Subject Headings

  • Young Adult
  • Vascular Resistance
  • Syndrome
  • Mitral Valve Stenosis
  • Male
  • Lung Transplantation
  • Hypertension, Pulmonary
  • Humans
  • Heart Valve Prosthesis Implantation
  • Heart Transplantation