Endolymphatic sac tumors: report of 2 cases and review of the world's literature


Journal Article

Endolymphatic sac tumors are rare, low-grade, locally invasive tumors of the temporal bone that extend into the posterior fossa. An extensive review of the literature reveals only 69 reported cases of endolymphatic sac tumors. We present 2 pathologically proven cases, a 45-year-old male and a 13year-old female (the youngest patient yet reported). Clinical presentation, radiographie studies, and pathological findings, were reviewed and compared with the literature. Findings in these 2 patients are in accordance with those in the literature reporting local recurrence but long-term survival. Key diagnostic features include anatomic location and the characteristic high-signal intensity of the tumor on non-contrasted Tlweighted images. Early recognition and surgical treatment are important factors affecting outcome.

Duke Authors

Cited Authors

  • Ferreira, MT; Gonzalez, FL; Zabramski, JM; Deshmukh, P; Preul, MC; Spetzler, RF

Published Date

  • January 1, 2001

Published In

Volume / Issue

  • 11 / SUPPL. 1

Start / End Page

  • 13 -

International Standard Serial Number (ISSN)

  • 1531-5010

Citation Source

  • Scopus