Endolymphatic sac tumors: report of 2 cases and review of the world's literature
Endolymphatic sac tumors are rare, low-grade, locally invasive tumors of the temporal bone that extend into the posterior fossa. An extensive review of the literature reveals only 69 reported cases of endolymphatic sac tumors. We present 2 pathologically proven cases, a 45-year-old male and a 13year-old female (the youngest patient yet reported). Clinical presentation, radiographie studies, and pathological findings, were reviewed and compared with the literature. Findings in these 2 patients are in accordance with those in the literature reporting local recurrence but long-term survival. Key diagnostic features include anatomic location and the characteristic high-signal intensity of the tumor on non-contrasted Tlweighted images. Early recognition and surgical treatment are important factors affecting outcome.
Ferreira, MT; Gonzalez, FL; Zabramski, JM; Deshmukh, P; Preul, MC; Spetzler, RF
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