Airway Management in a Patient with Wolf-Hirschhorn Syndrome.


Journal Article

We present a case of a 3-month-old female with Wolf-Hirschhorn syndrome (WHS) undergoing general anesthesia for laparoscopic gastrostomy tube placement with a focus on airway management. WHS is a rare 4p microdeletion syndrome resulting in multiple congenital abnormalities, including craniofacial deformities. Microcephaly, micrognathia, and glossoptosis are common features in WHS patients and risk factors for a pediatric airway that is potentially difficult to intubate. We discuss anesthesia strategies for airway preparation and management in a WHS patient requiring general anesthesia with endotracheal intubation.

Full Text

Duke Authors

Cited Authors

  • Gamble, JF; Kurian, DJ; Udani, AG; Greene, NH

Published Date

  • 2016

Published In

Volume / Issue

  • 2016 /

Start / End Page

  • 7070125 -

PubMed ID

  • 27752382

Pubmed Central ID

  • 27752382

International Standard Serial Number (ISSN)

  • 2090-6803

Digital Object Identifier (DOI)

  • 10.1155/2016/7070125


  • eng

Conference Location

  • United States