Gynecologic and surgical complications in type IV Ehlers-Danlos syndrome.

Published

Journal Article

BACKGROUND: Although type IV Ehlers-Danlos syndrome is a rare condition, it is critical that physicians be aware of this disease because it presents unique management challenges. CASE: We present a young woman who was admitted with a pelvic abscess after having a miscarriage and an appendiceal perforation. She had an exploratory laparotomy secondary to a persistent pelvic abscess and endured multiple postoperative complications. Based on her family history and physical characteristics, type IV Ehlers-Danlos syndrome was diagnosed. CONCLUSION: The decision to proceed with surgery should be weighed against tissue fragility in patients with type IV Ehlers-Danlos syndrome. A conservative, multidisciplinary team approach addresses whether to proceed with surgery and minimize postoperative complications if surgery is performed.

Full Text

Duke Authors

Cited Authors

  • Wheeler, SM; Russo, M; Wilson-Murphy, M; Shen, W

Published Date

  • February 2014

Published In

Volume / Issue

  • 123 / 2 Pt 2 Suppl 2

Start / End Page

  • 431 - 433

PubMed ID

  • 24413228

Pubmed Central ID

  • 24413228

Electronic International Standard Serial Number (EISSN)

  • 1873-233X

Digital Object Identifier (DOI)

  • 10.1097/AOG.0000000000000001

Language

  • eng

Conference Location

  • United States