BACKGROUND: Mammary-type myofibroblastomas have been reported at extramammary sites, especially along the mammary midline, but not previously in the vulva. CASE: A 56-year-old woman presented with complaints of a left vulvar mass, pelvic organ prolapse and urinary incontinence. Examination revealed a 3-cm,firm vulvar mass, located in close proximity to the Bartholin's gland. CONCLUSION: Although myofibroblastomas have been reported at extramammary sites, this is this first reported case in the vulva. These masses are densely adherent to surrounding tissue, which can lead to a difficult dissection. Therefore they should be removed in the operating room with appropriate equipment and sedation.