Reversible pulmonary hypertension in POEMS syndrome--another etiology of triggered pulmonary vasculopathy?

Published

Journal Article (Review)

Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes (POEMS) syndrome, a plasma cell dyscrasia associated with pulmonary hypertension, has been treated in the past with anticytokine strategies with a poor outcome. A patient is described who had POEMS syndrome with precapillary pulmonary hypertension and Raynaud's phenomenon, and who responded well to a short course of corticosteroids and long term nifedipine. POEMS syndrome, like anorexigens, cocaine, portal hypertension and human immunodeficiency virus infection, may be another trigger for the pulmonary vascular occlusive process found in primary pulmonary hypertension.

Full Text

Duke Authors

Cited Authors

  • Paciocco, G; Bossone, E; Erba, H; Rubenfire, M

Published Date

  • August 2000

Published In

Volume / Issue

  • 16 / 8

Start / End Page

  • 1007 - 1012

PubMed ID

  • 10978936

Pubmed Central ID

  • 10978936

International Standard Serial Number (ISSN)

  • 0828-282X

Language

  • eng

Conference Location

  • England