Living with Tricuspid Atresia: Case Report with Review of Literature.

Journal Article (Review;Journal Article)

Tricuspid atresia (TA) is a rare congenital heart defect in which the right atrioventricular connection, the tricuspid valve, is absent. As a result, there is no direct communication between the right atrium and right ventricle. Surgical treatment, including the Fontan procedure, is indicated yet palliative, leaving patients with various lifelong complications. A comprehensive literature review revealed a paucity of evidence-based education on the identification, evaluation, management, treatment, and life span implications of TA. We present a case of TA from birth through adulthood, while simultaneously assessing the literature, to report the most current evidence relative to living with TA after surgical palliation. In addition, the embryology, methods of prenatal and postnatal diagnosis, potential complications, management, anticipatory guidance, and educational needs of both parents and patient are discussed.

Full Text

Duke Authors

Cited Authors

  • Frock, BW; Jnah, AJ; Newberry, DM

Published Date

  • July 2017

Published In

Volume / Issue

  • 36 / 4

Start / End Page

  • 218 - 228

PubMed ID

  • 28764825

Electronic International Standard Serial Number (EISSN)

  • 1539-2880

International Standard Serial Number (ISSN)

  • 0730-0832

Digital Object Identifier (DOI)

  • 10.1891/0730-0832.36.4.218


  • eng