Corrected transposition with severe intracardiac deformities with Wolff-Parkinson-White syndrome in a child. Electrophysiologic investigation and surgical correction.


Journal Article

This is a report of a 10-year-old child who underwent surgery for complex congenital heart disease consisting of corrected transposition of the great vessels, ventricular septal defect, patent ductus arterisus, severe left-sided atrioventricular (AV) valve insuffieicney (Ebstein's deformity) and Wolff-Parkinson-White syndrome. The site of his accessory AV connection was localized preoperatively at a left anterolateral site by isopotential body surface maps and by intracardiac electrophysiologic studies. He successfully underwent surgery for closure of the ventricular septal defect, ligation of the patent ductus arteriosus, replacement of the left-sided AV valve, and interruption of the accessory AV pathway. Unavoidable complete AV block acquired at surgery required subsequent permanent pacemaker therapy.

Full Text

Cited Authors

  • Benson, DW; Gallagher, JJ; Oldham, HN; Sealy, WC; Sterba, R; Spach, MS

Published Date

  • June 1980

Published In

Volume / Issue

  • 61 / 6

Start / End Page

  • 1256 - 1261

PubMed ID

  • 7371140

Pubmed Central ID

  • 7371140

International Standard Serial Number (ISSN)

  • 0009-7322

Digital Object Identifier (DOI)

  • 10.1161/01.cir.61.6.1256


  • eng

Conference Location

  • United States