Bilateral renal carcinoma in von Hippel-Lindau Disease.

Published

Journal Article

Von Hippel-Lindau disease, one of the phakomatoses, is believed to be a disorder of mesodermal differentiation. Renal lesions, usually cysts or adenocarcinomas with an occasional hemangioblastoma, occur in approximately two thirds of all patients. The renal neoplasms previously reported have been multiple, bilateral, and usually beyond resection. A thirty-eight-year-old white male with a cerebellar hemangioblastoma and bilateral renal adenocarcinoma underwent suboccipital craniotomy, right heminephrectomy, and left radical nephrectomy. No evidence of recurrent disease can be identified ten months postoperatively. An aggressive approach in this systemic disease appears to be warranted.

Full Text

Duke Authors

Cited Authors

  • Mullin, EM; White, RD; Peterson, LJ; Paulson, DF

Published Date

  • November 1, 1976

Published In

Volume / Issue

  • 8 / 5

Start / End Page

  • 475 - 478

PubMed ID

  • 982734

Pubmed Central ID

  • 982734

International Standard Serial Number (ISSN)

  • 0090-4295

Digital Object Identifier (DOI)

  • 10.1016/0090-4295(76)90279-x

Language

  • eng

Conference Location

  • United States