Prognosis of pulmonary arterial hypertension: ACCP evidence-based clinical practice guidelines.

Journal Article (Journal Article;Review)

Although idiopathic pulmonary arterial hypertension is perceived as a progressive disease with a uniformly poor outcome, the natural history of disease is heterogeneous, with some patients dying within months of diagnosis and others living for decades. The course of the disease has also been altered by advances in medical therapies. The outcome of patients with other types of pulmonary arterial hypertension (PAH) has been less well characterized. Assessment of prognosis of such patients is important, as it influences both medical therapy and referral for transplantation. This chapter will provide evidence based recommendations to assess the prognosis of patients with PAH.

Full Text

Duke Authors

Cited Authors

  • McLaughlin, VV; Presberg, KW; Doyle, RL; Abman, SH; McCrory, DC; Fortin, T; Ahearn, G; American College of Chest Physicians,

Published Date

  • July 1, 2004

Published In

Volume / Issue

  • 126 / 1 Suppl

Start / End Page

  • 78S - 92S

PubMed ID

  • 15249497

International Standard Serial Number (ISSN)

  • 0012-3692

Digital Object Identifier (DOI)

  • 10.1378/chest.126.1_suppl.78S


  • eng

Conference Location

  • United States