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Polysplenia with pulmonary arteriovenous malformations.

Publication ,  Journal Article
Papagiannis, J; Kanter, RJ; Effman, EL; Pratt, PC; Marcille, R; Browning, IB; Armstrong, BE
Published in: Pediatr Cardiol
March 1993
Published version (DOI) Link to item

A patient with polysplenia syndrome, dextrocardia, left atrial isomerism, normal great vessel relationships, and no intracardiac shunts developed progressive cyanosis and clubbing. Pulmonary arteriovenous malformations (PAVMs) were diagnosed by angiography and confirmed by lung biopsy. Superior mesenteric arteriogram revealed hypoplasia of the intrahepatic portal vein branches and a portosystemic shunt. The possible etiologies of PAVMs are discussed.

Duke Scholars

Ronald Jay Kanter
Author Ronald Jay Kanter Pediatrics, Cardiology

Published In

Pediatr Cardiol

DOI

10.1007/BF00796995

ISSN

0172-0643

Publication Date

March 1993

Volume

14

Issue

2

Start / End Page

127 / 129

Location

United States

Related Subject Headings

  • Syndrome
  • Spleen
  • Pulmonary Artery
  • Lung
  • Liver
  • Humans
  • Heart Defects, Congenital
  • Female
  • Child, Preschool
  • Cardiovascular System & Hematology
 

Citation

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Papagiannis, J., Kanter, R. J., Effman, E. L., Pratt, P. C., Marcille, R., Browning, I. B., & Armstrong, B. E. (1993). Polysplenia with pulmonary arteriovenous malformations. Pediatr Cardiol, 14(2), 127–129. https://doi.org/10.1007/BF00796995
Papagiannis, J., R. J. Kanter, E. L. Effman, P. C. Pratt, R. Marcille, I. B. Browning, and B. E. Armstrong. “Polysplenia with pulmonary arteriovenous malformations.” Pediatr Cardiol 14, no. 2 (March 1993): 127–29. https://doi.org/10.1007/BF00796995.
Papagiannis J, Kanter RJ, Effman EL, Pratt PC, Marcille R, Browning IB, et al. Polysplenia with pulmonary arteriovenous malformations. Pediatr Cardiol. 1993 Mar;14(2):127–9.
Papagiannis, J., et al. “Polysplenia with pulmonary arteriovenous malformations.” Pediatr Cardiol, vol. 14, no. 2, Mar. 1993, pp. 127–29. Pubmed, doi:10.1007/BF00796995.
Papagiannis J, Kanter RJ, Effman EL, Pratt PC, Marcille R, Browning IB, Armstrong BE. Polysplenia with pulmonary arteriovenous malformations. Pediatr Cardiol. 1993 Mar;14(2):127–129.
Journal cover image

Published In

Pediatr Cardiol

DOI

10.1007/BF00796995

ISSN

0172-0643

Publication Date

March 1993

Volume

14

Issue

2

Start / End Page

127 / 129

Location

United States

Related Subject Headings

  • Syndrome
  • Spleen
  • Pulmonary Artery
  • Lung
  • Liver
  • Humans
  • Heart Defects, Congenital
  • Female
  • Child, Preschool
  • Cardiovascular System & Hematology