Polysplenia with pulmonary arteriovenous malformations.

Journal Article (Journal Article)

A patient with polysplenia syndrome, dextrocardia, left atrial isomerism, normal great vessel relationships, and no intracardiac shunts developed progressive cyanosis and clubbing. Pulmonary arteriovenous malformations (PAVMs) were diagnosed by angiography and confirmed by lung biopsy. Superior mesenteric arteriogram revealed hypoplasia of the intrahepatic portal vein branches and a portosystemic shunt. The possible etiologies of PAVMs are discussed.

Full Text

Duke Authors

Cited Authors

  • Papagiannis, J; Kanter, RJ; Effman, EL; Pratt, PC; Marcille, R; Browning, IB; Armstrong, BE

Published Date

  • March 1, 1993

Published In

Volume / Issue

  • 14 / 2

Start / End Page

  • 127 - 129

PubMed ID

  • 8469631

International Standard Serial Number (ISSN)

  • 0172-0643

Digital Object Identifier (DOI)

  • 10.1007/BF00796995


  • eng

Conference Location

  • United States