Motor variant of chronic inflammatory demyelinating polyneuropathy in a child.
Journal Article (Journal Article)
Only 2 cases of pure motor chronic demyelinating inflammatory polyneuropathy in the pediatric age group have been reported in the literature. We report on a motor variant of chronic demyelinating inflammatory polyneuropathy with anti-ganglioside antibodies, diagnosed in a 5-year-old girl who presented with progressive motor weakness over a period of 12 months with no sensory involvement. She initially responded partially to intravenous immunoglobulin therapy (1 gm/kg/month for 6 months), and then demonstrated sustained but incomplete improvement on chronic prednisone therapy (1-2 mg/kg/day), on which she has continued since 1 year and 4 months after her initial presentation 3 years ago.
Full Text
Duke Authors
Cited Authors
- Sinno, DD; Darras, BT; Yamout, BI; Rebeiz, JG; Mikati, MA
Published Date
- June 2008
Published In
Volume / Issue
- 38 / 6
Start / End Page
- 426 - 429
PubMed ID
- 18486826
International Standard Serial Number (ISSN)
- 0887-8994
Digital Object Identifier (DOI)
- 10.1016/j.pediatrneurol.2008.02.008
Language
- eng
Conference Location
- United States