Motor variant of chronic inflammatory demyelinating polyneuropathy in a child.

Journal Article (Journal Article)

Only 2 cases of pure motor chronic demyelinating inflammatory polyneuropathy in the pediatric age group have been reported in the literature. We report on a motor variant of chronic demyelinating inflammatory polyneuropathy with anti-ganglioside antibodies, diagnosed in a 5-year-old girl who presented with progressive motor weakness over a period of 12 months with no sensory involvement. She initially responded partially to intravenous immunoglobulin therapy (1 gm/kg/month for 6 months), and then demonstrated sustained but incomplete improvement on chronic prednisone therapy (1-2 mg/kg/day), on which she has continued since 1 year and 4 months after her initial presentation 3 years ago.

Full Text

Duke Authors

Cited Authors

  • Sinno, DD; Darras, BT; Yamout, BI; Rebeiz, JG; Mikati, MA

Published Date

  • June 2008

Published In

Volume / Issue

  • 38 / 6

Start / End Page

  • 426 - 429

PubMed ID

  • 18486826

International Standard Serial Number (ISSN)

  • 0887-8994

Digital Object Identifier (DOI)

  • 10.1016/j.pediatrneurol.2008.02.008


  • eng

Conference Location

  • United States