Sudden cardiac death in young children with neurofibromatosis type 1.

Journal Article (Journal Article)

Patients with neurofibromatosis type 1 (NF1) can manifest a characteristic vasculopathy that in adults is rarely associated with fatal coronary artery occlusion. We describe the clinical and pathological findings from 2 unrelated young children with NF1, a similar vasculopathy affecting their coronary arteries, and sudden cardiac death.

Full Text

Duke Authors

Cited Authors

  • Kanter, RJ; Graham, M; Fairbrother, D; Smith, SV

Published Date

  • November 2006

Published In

Volume / Issue

  • 149 / 5

Start / End Page

  • 718 - 720

PubMed ID

  • 17095352

International Standard Serial Number (ISSN)

  • 0022-3476

Digital Object Identifier (DOI)

  • 10.1016/j.jpeds.2006.07.046


  • eng

Conference Location

  • United States