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Congenital generalized fibromatosis with visceral involvement. A case report.

Publication ,  Journal Article
Roggli, VL; Kim, HS; Hawkins, E
Published in: Cancer
March 1, 1980

A case of congenital generalized fibromatosis in a black male infant with involvement of lungs, subcutaneous tissue, pancreas, adrenal, lymph nodes, and bone is described. Fifteen prior cases with pulmonary involvement are reviewed, emphasizing the poor prognosis associated with pulmonary lesions. This case demonstrated, in addition to previously described histologic features, broad bands of fibroblastic proliferation in the interlobular septa producing retraction of the visceral pleura. Possible etiologic factors are discussed, with suggestions for additional studies in future cases.

Duke Scholars

Published In

Cancer

DOI

ISSN

0008-543X

Publication Date

March 1, 1980

Volume

45

Issue

5

Start / End Page

954 / 960

Location

United States

Related Subject Headings

  • Oncology & Carcinogenesis
  • Neoplasms, Multiple Primary
  • Myocardium
  • Male
  • Lung
  • Infant
  • Humans
  • Fibroma
  • 1117 Public Health and Health Services
  • 1112 Oncology and Carcinogenesis
 

Citation

APA
Chicago
ICMJE
MLA
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Roggli, V. L., Kim, H. S., & Hawkins, E. (1980). Congenital generalized fibromatosis with visceral involvement. A case report. Cancer, 45(5), 954–960. https://doi.org/10.1002/1097-0142(19800301)45:5<954::aid-cncr2820450520>3.0.co;2-q
Roggli, V. L., H. S. Kim, and E. Hawkins. “Congenital generalized fibromatosis with visceral involvement. A case report.Cancer 45, no. 5 (March 1, 1980): 954–60. https://doi.org/10.1002/1097-0142(19800301)45:5<954::aid-cncr2820450520>3.0.co;2-q.
Roggli VL, Kim HS, Hawkins E. Congenital generalized fibromatosis with visceral involvement. A case report. Cancer. 1980 Mar 1;45(5):954–60.
Roggli, V. L., et al. “Congenital generalized fibromatosis with visceral involvement. A case report.Cancer, vol. 45, no. 5, Mar. 1980, pp. 954–60. Pubmed, doi:10.1002/1097-0142(19800301)45:5<954::aid-cncr2820450520>3.0.co;2-q.
Roggli VL, Kim HS, Hawkins E. Congenital generalized fibromatosis with visceral involvement. A case report. Cancer. 1980 Mar 1;45(5):954–960.
Journal cover image

Published In

Cancer

DOI

ISSN

0008-543X

Publication Date

March 1, 1980

Volume

45

Issue

5

Start / End Page

954 / 960

Location

United States

Related Subject Headings

  • Oncology & Carcinogenesis
  • Neoplasms, Multiple Primary
  • Myocardium
  • Male
  • Lung
  • Infant
  • Humans
  • Fibroma
  • 1117 Public Health and Health Services
  • 1112 Oncology and Carcinogenesis