Congenital generalized fibromatosis with visceral involvement. A case report.

Journal Article (Journal Article)

A case of congenital generalized fibromatosis in a black male infant with involvement of lungs, subcutaneous tissue, pancreas, adrenal, lymph nodes, and bone is described. Fifteen prior cases with pulmonary involvement are reviewed, emphasizing the poor prognosis associated with pulmonary lesions. This case demonstrated, in addition to previously described histologic features, broad bands of fibroblastic proliferation in the interlobular septa producing retraction of the visceral pleura. Possible etiologic factors are discussed, with suggestions for additional studies in future cases.

Full Text

Duke Authors

Cited Authors

  • Roggli, VL; Kim, HS; Hawkins, E

Published Date

  • March 1, 1980

Published In

Volume / Issue

  • 45 / 5

Start / End Page

  • 954 - 960

PubMed ID

  • 7260846

International Standard Serial Number (ISSN)

  • 0008-543X

Digital Object Identifier (DOI)

  • 10.1002/1097-0142(19800301)45:5<954::aid-cncr2820450520>;2-q


  • eng

Conference Location

  • United States