Successful bilateral lung transplantation for lymphangiomatosis.

Journal Article (Journal Article)

Lymphangiomatosis is a rare disease of lymphatic proliferation for which no adequate treatment is known. We report the first successful case of bilateral lung transplantation for the treatment of end-stage pulmonary lymphangiomatosis. A successful outcome was achieved with continued survival beyond 4 years posttransplant and stable lung function. The primary obstacles to significant gains in pulmonary function were thoracic, skeletal and abdominal lymphangiomatosis, which led to pulmonary restriction. Our report demonstrates that pulmonary lymphangiomatosis should be included among those diseases for which lung transplantation is considered potentially beneficial treatment but also emphasizes the importance of screening patients carefully for chest wall and abdominal lymphangiomas that may impede recovery.

Full Text

Duke Authors

Cited Authors

  • Kinnier, CV; Eu, JPC; Davis, RD; Howell, DN; Sheets, J; Palmer, SM

Published Date

  • September 2008

Published In

Volume / Issue

  • 8 / 9

Start / End Page

  • 1946 - 1950

PubMed ID

  • 18671675

Pubmed Central ID

  • PMC3732029

Electronic International Standard Serial Number (EISSN)

  • 1600-6143

Digital Object Identifier (DOI)

  • 10.1111/j.1600-6143.2008.02340.x


  • eng

Conference Location

  • United States