Double aortic arch with aortic atresia and left-sided type B interruption.

Journal Article (Journal Article)

Aortic valve atresia with interruption of the aortic arch is an extremely rare anomaly; only eleven cases of this anomaly have been reported to date. In the absence of additional sources of blood flow to the ascending aorta, aortic valve atresia with interruption of the aortic arch is fatal. We present, to the best of our knowledge, the first case of a live birth with aortic valve atresia and interrupted left aortic arch (type B) without evidence of an aorticopulmonary communication or ductal supply to the native ascending aorta. Instead, blood flow to the native aortic root was derived from a persistent right embryonic dorsal aorta.

Full Text

Duke Authors

Cited Authors

  • Baker-Smith, CM; Milazzo, AS; Frush, DP; Jaggers, J; Kirby, ML; Kanter, RJ; Barker, PC

Published Date

  • May 2010

Published In

Volume / Issue

  • 5 / 3

Start / End Page

  • 316 - 320

PubMed ID

  • 20576054

Electronic International Standard Serial Number (EISSN)

  • 1747-0803

Digital Object Identifier (DOI)

  • 10.1111/j.1747-0803.2009.00341.x


  • eng

Conference Location

  • United States