The Thibierge-Weissenbach syndrome: A rare clinical presentation of generalized soft tissue calcifications associated with scleroderma

Journal Article (Journal Article)

Thibierge-Weissenbach syndrome is a rare entity of generalized soft tissue calcinosis of the hand associated with scleroderma. Patients present with tumorous deformities of the hand and phalanges which are easily misdiagnosed as rheumatoid arthritis. The diagnosis is confirmed by conventional X-rays. Treatment options are limited to local excision of painful or ulcerated nodules. Multiple operations are frequently required due to the high incidence of local recurrence. Two clinical cases and a review of the etiopathogenesis of the Thibierge-Weissenbach syndrome are presented.

Full Text

Duke Authors

Cited Authors

  • Erdmann, D; Busching, K; Sauerbier, M; Germann, G

Published Date

  • October 1, 1999

Published In

Volume / Issue

  • 22 / 7

Start / End Page

  • 326 - 328

International Standard Serial Number (ISSN)

  • 0930-343X

Digital Object Identifier (DOI)

  • 10.1007/s002380050273

Citation Source

  • Scopus