Fibrosing alveolitis in patients with neurofibromatosis.
Publication
, Journal Article
Webb, WR; Goodman, PC
Published in: Radiology
February 1977
Fibrosing alveolitis, or interstitial pulmonary fibrosis, is a common manifestation of neurofibromatosis, and was observed in 7 of 70 patients with the disease. Though neurofibromatosis is congenital, fibrosing alveolitis does not appear until adulthood, and occurs in 20% of patients with the disease who are over 30 years old. Characteristic radiographic findings include linear, interstitial density, and large upper lobe bullae; this combination limits the differential diagnosis. Pathological examination demonstrates alveolar wall thickening progressing to fibrosis and lung destruction. Pulmonary function tests can show obstructive or restrictive lung disease.
Duke Scholars
Published In
Radiology
DOI
ISSN
0033-8419
Publication Date
February 1977
Volume
122
Issue
2
Start / End Page
289 / 293
Location
United States
Related Subject Headings
- Radiography
- Pulmonary Fibrosis
- Pulmonary Alveoli
- Nuclear Medicine & Medical Imaging
- Neurofibromatosis 1
- Middle Aged
- Male
- Infant
- Humans
- Female
Citation
APA
Chicago
ICMJE
MLA
NLM
Webb, W. R., & Goodman, P. C. (1977). Fibrosing alveolitis in patients with neurofibromatosis. Radiology, 122(2), 289–293. https://doi.org/10.1148/122.2.289
Webb, W. R., and P. C. Goodman. “Fibrosing alveolitis in patients with neurofibromatosis.” Radiology 122, no. 2 (February 1977): 289–93. https://doi.org/10.1148/122.2.289.
Webb WR, Goodman PC. Fibrosing alveolitis in patients with neurofibromatosis. Radiology. 1977 Feb;122(2):289–93.
Webb, W. R., and P. C. Goodman. “Fibrosing alveolitis in patients with neurofibromatosis.” Radiology, vol. 122, no. 2, Feb. 1977, pp. 289–93. Pubmed, doi:10.1148/122.2.289.
Webb WR, Goodman PC. Fibrosing alveolitis in patients with neurofibromatosis. Radiology. 1977 Feb;122(2):289–293.
Published In
Radiology
DOI
ISSN
0033-8419
Publication Date
February 1977
Volume
122
Issue
2
Start / End Page
289 / 293
Location
United States
Related Subject Headings
- Radiography
- Pulmonary Fibrosis
- Pulmonary Alveoli
- Nuclear Medicine & Medical Imaging
- Neurofibromatosis 1
- Middle Aged
- Male
- Infant
- Humans
- Female