Hypoplastic left heart syndrome, interrupted inferior vena cava, biliary atresia.


Journal Article

A neonate was diagnosed with hypoplastic left heart syndrome, heterotaxy syndrome, and interrupted inferior vena cava soon after birth. At 6 days old she underwent the Norwood procedure using Sano modification. Postoperatively she had persistent direct hyperbilirubinemia and was diagnosed with biliary atresia for which she underwent a Kasai procedure at 29 days old. At 10 months she underwent the Kawashima procedure. She is now 20 months old and has been thriving without any jaundice. This case report illustrates that even in the presence of major multiple congenital anomalies, staged reconstruction for hypoplastic left heart syndrome can be successfully performed.

Full Text

Cited Authors

  • Imamura, M; Dyamenahalli, U; Sachdeva, R; Kokoska, ER; Jaquiss, RDB

Published Date

  • November 2007

Published In

Volume / Issue

  • 84 / 5

Start / End Page

  • 1746 - 1748

PubMed ID

  • 17954104

Pubmed Central ID

  • 17954104

Electronic International Standard Serial Number (EISSN)

  • 1552-6259

International Standard Serial Number (ISSN)

  • 0003-4975

Digital Object Identifier (DOI)

  • 10.1016/j.athoracsur.2007.05.068


  • eng