Diabetes mellitus and profound insulin resistance in Johanson-Blizzard syndrome.


Journal Article

Pancreatic exocrine insufficiency in Johanson-Blizzard syndrome (JBS) is well described but only two previous patient reports document pancreatic endocrine insufficiency manifested as diabetes mellitus, and each patient required only a modest dose of insulin to control hyperglycemia. We report a patient with JBS and new-onset diabetes mellitus with profound insulin resistance, with no clinical or laboratory evidence of pancreatic exocrine insufficiency.

Full Text

Duke Authors

Cited Authors

  • Steinbach, WJ; Hintz, RL

Published Date

  • November 2000

Published In

Volume / Issue

  • 13 / 9

Start / End Page

  • 1633 - 1636

PubMed ID

  • 11154160

Pubmed Central ID

  • 11154160

International Standard Serial Number (ISSN)

  • 0334-018X

Digital Object Identifier (DOI)

  • 10.1515/jpem.2000.13.9.1633


  • eng

Conference Location

  • Germany