Hepatic failure in adult Niemann-Pick disease.

Journal Article (Journal Article)

The case of a 29-year-old man with Niemann-Pick disease and hepatic failure is presented. Massive hepatomegaly with hepatic calcification were noted in association with a course of persistent hepatitis B serum antigenemia with rapid hepatic decompensation, ascites, encephalopathy and renal failure. The possible relationship of the clinical course to the underlying disease process is discussed, and a review of Niemann-Pick disease is presented.

Full Text

Duke Authors

Cited Authors

  • Wilson, JA; Raufman, JP

Published Date

  • September 1986

Published In

Volume / Issue

  • 292 / 3

Start / End Page

  • 168 - 172

PubMed ID

  • 3752163

International Standard Serial Number (ISSN)

  • 0002-9629

Digital Object Identifier (DOI)

  • 10.1097/00000441-198609000-00010


  • eng

Conference Location

  • United States