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Epidural spinal involvement of Erdheim-Chester disease causing myelopathy.

Publication ,  Journal Article
Hwang, BY; Liu, A; Kern, J; Goodwin, CR; Wolinsky, JP; Desai, A
Published in: J Clin Neurosci
September 2015

We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.

Duke Scholars

Published In

J Clin Neurosci

DOI

EISSN

1532-2653

Publication Date

September 2015

Volume

22

Issue

9

Start / End Page

1532 / 1536

Location

Scotland

Related Subject Headings

  • Spinal Cord Diseases
  • Neurology & Neurosurgery
  • Humans
  • Female
  • Erdheim-Chester Disease
  • Epidural Space
  • Adult
  • 5202 Biological psychology
  • 3209 Neurosciences
  • 3202 Clinical sciences
 

Citation

APA
Chicago
ICMJE
MLA
NLM
Hwang, B. Y., Liu, A., Kern, J., Goodwin, C. R., Wolinsky, J. P., & Desai, A. (2015). Epidural spinal involvement of Erdheim-Chester disease causing myelopathy. J Clin Neurosci, 22(9), 1532–1536. https://doi.org/10.1016/j.jocn.2015.04.004
Hwang, Brian Y., Ann Liu, Jason Kern, C Rory Goodwin, Jean Paul Wolinsky, and Atman Desai. “Epidural spinal involvement of Erdheim-Chester disease causing myelopathy.J Clin Neurosci 22, no. 9 (September 2015): 1532–36. https://doi.org/10.1016/j.jocn.2015.04.004.
Hwang BY, Liu A, Kern J, Goodwin CR, Wolinsky JP, Desai A. Epidural spinal involvement of Erdheim-Chester disease causing myelopathy. J Clin Neurosci. 2015 Sep;22(9):1532–6.
Hwang, Brian Y., et al. “Epidural spinal involvement of Erdheim-Chester disease causing myelopathy.J Clin Neurosci, vol. 22, no. 9, Sept. 2015, pp. 1532–36. Pubmed, doi:10.1016/j.jocn.2015.04.004.
Hwang BY, Liu A, Kern J, Goodwin CR, Wolinsky JP, Desai A. Epidural spinal involvement of Erdheim-Chester disease causing myelopathy. J Clin Neurosci. 2015 Sep;22(9):1532–1536.
Journal cover image

Published In

J Clin Neurosci

DOI

EISSN

1532-2653

Publication Date

September 2015

Volume

22

Issue

9

Start / End Page

1532 / 1536

Location

Scotland

Related Subject Headings

  • Spinal Cord Diseases
  • Neurology & Neurosurgery
  • Humans
  • Female
  • Erdheim-Chester Disease
  • Epidural Space
  • Adult
  • 5202 Biological psychology
  • 3209 Neurosciences
  • 3202 Clinical sciences