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Inflammatory Pseudotumor of the Temporal Bone Leading to Atypical Superior Semicircular Canal Dehiscence Syndrome: A Novel Case Report.

Publication ,  Journal Article
Smith, BD; Cunningham, CD
Published in: Otol Neurotol
September 1, 2021

OBJECTIVE: Inflammatory pseudotumor of the temporal bone is a benign idiopathic inflammatory process that is rarely encountered in clinical practice. We describe a novel case of a patient who developed superior semicircular canal dehiscence syndrome in the setting of active inflammatory pseudotumor of the temporal bone. PATIENT: One female patient found to have inflammatory pseudotumor of the temporal bone. After treatment with mastoidectomy and steroids, she subsequently developed superior semicircular canal dehiscence syndrome. INTERVENTIONS: The patient initially underwent myringotomy and pressure equalization tube placement for a unilateral effusion. Imaging with computed tomography and magnetic resonance imaging revealed a lytic mastoid mass. A complete mastoidectomy was diagnostic for inflammatory pseudotumor and the patient was treated with adjuvant long-term corticosteroids. After this procedure, she was discovered to have new development of symptomatic superior semicircular canal dehiscence syndrome. She eventually underwent a trans-mastoid repair of her superior semicircular canal dehiscence. MAIN OUTCOME MEASURES: The patient's clinical course is described with emphasis on the development of superior semicircular canal dehiscence syndrome in the setting of active inflammatory pseudotumor of the temporal bone. RESULTS: The patient's radiographic and clinical history were found to be consistent with inflammatory pseudotumor of the temporal bone. She underwent a therapeutic mastoidectomy with long-term post-operative corticosteroids. During her post-operative course, she developed symptoms of vertigo, hearing loss, and autophony. She was subsequently diagnosed with superior semicircular canal dehiscence and treated with a trans-mastoid repair of the dehiscence. Her symptoms satisfactorily resolved after this surgery. CONCLUSIONS: Inflammatory pseudotumor of the temporal bone is a rare benign inflammatory process. We present what is to our knowledge the first description of superior semicircular canal dehiscence syndrome developing in the setting of inflammatory pseudotumor.

Duke Scholars

Published In

Otol Neurotol

DOI

EISSN

1537-4505

Publication Date

September 1, 2021

Volume

42

Issue

8

Start / End Page

e1062 / e1066

Location

United States

Related Subject Headings

  • Vertigo
  • Temporal Bone
  • Semicircular Canals
  • Semicircular Canal Dehiscence
  • Otorhinolaryngology
  • Humans
  • Granuloma, Plasma Cell
  • Female
  • 4201 Allied health and rehabilitation science
  • 3202 Clinical sciences
 

Citation

APA
Chicago
ICMJE
MLA
NLM
Smith, B. D., & Cunningham, C. D. (2021). Inflammatory Pseudotumor of the Temporal Bone Leading to Atypical Superior Semicircular Canal Dehiscence Syndrome: A Novel Case Report. Otol Neurotol, 42(8), e1062–e1066. https://doi.org/10.1097/MAO.0000000000003218
Smith, Blaine D., and Calhoun D. Cunningham. “Inflammatory Pseudotumor of the Temporal Bone Leading to Atypical Superior Semicircular Canal Dehiscence Syndrome: A Novel Case Report.Otol Neurotol 42, no. 8 (September 1, 2021): e1062–66. https://doi.org/10.1097/MAO.0000000000003218.
Smith, Blaine D., and Calhoun D. Cunningham. “Inflammatory Pseudotumor of the Temporal Bone Leading to Atypical Superior Semicircular Canal Dehiscence Syndrome: A Novel Case Report.Otol Neurotol, vol. 42, no. 8, Sept. 2021, pp. e1062–66. Pubmed, doi:10.1097/MAO.0000000000003218.

Published In

Otol Neurotol

DOI

EISSN

1537-4505

Publication Date

September 1, 2021

Volume

42

Issue

8

Start / End Page

e1062 / e1066

Location

United States

Related Subject Headings

  • Vertigo
  • Temporal Bone
  • Semicircular Canals
  • Semicircular Canal Dehiscence
  • Otorhinolaryngology
  • Humans
  • Granuloma, Plasma Cell
  • Female
  • 4201 Allied health and rehabilitation science
  • 3202 Clinical sciences