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Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population.

Publication ,  Journal Article
Marcus, JR; Few, JW; Senger, C; Reynolds, M
Published in: J Pediatr Surg
December 1998

Dermatofibrosarcoma protuberans (DFSP) is a low-intermediate-grade cutaneous sarcoma that has a marked propensity for local recurrence after excision. The Bednar variant of this tumor is even less common and is distinguished histologically by the dispersal of melanin containing cells in an otherwise typical DFSP. Both are considered to be tumors of the third and forth decades of life, but both DFSP and the Bednar variant have been described in children. Until this report of a congenital Bednar tumor, only the DFSP has also been described in the neonate. The histopathology and surgical management of DFSP and Bednar tumors are outlined with emphasis on reported experience in the pediatric population. The surgical management of these lesions in children is based on numerous series in adults and the limited pediatric experience. The recommended treatment is wide excision with 3-cm margins of visibly uninvolved tissue and inclusion of superficial fascia.

Duke Scholars

Published In

J Pediatr Surg

DOI

ISSN

0022-3468

Publication Date

December 1998

Volume

33

Issue

12

Start / End Page

1811 / 1814

Location

United States

Related Subject Headings

  • Skin Neoplasms
  • Pediatrics
  • Infant
  • Humans
  • Female
  • Dermatofibrosarcoma
  • 1114 Paediatrics and Reproductive Medicine
 

Citation

APA
Chicago
ICMJE
MLA
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Marcus, J. R., Few, J. W., Senger, C., & Reynolds, M. (1998). Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population. J Pediatr Surg, 33(12), 1811–1814. https://doi.org/10.1016/s0022-3468(98)90292-5
Marcus, J. R., J. W. Few, C. Senger, and M. Reynolds. “Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population.J Pediatr Surg 33, no. 12 (December 1998): 1811–14. https://doi.org/10.1016/s0022-3468(98)90292-5.
Marcus JR, Few JW, Senger C, Reynolds M. Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population. J Pediatr Surg. 1998 Dec;33(12):1811–4.
Marcus, J. R., et al. “Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population.J Pediatr Surg, vol. 33, no. 12, Dec. 1998, pp. 1811–14. Pubmed, doi:10.1016/s0022-3468(98)90292-5.
Marcus JR, Few JW, Senger C, Reynolds M. Dermatofibrosarcoma protuberans and the Bednar tumor: treatment in the pediatric population. J Pediatr Surg. 1998 Dec;33(12):1811–1814.
Journal cover image

Published In

J Pediatr Surg

DOI

ISSN

0022-3468

Publication Date

December 1998

Volume

33

Issue

12

Start / End Page

1811 / 1814

Location

United States

Related Subject Headings

  • Skin Neoplasms
  • Pediatrics
  • Infant
  • Humans
  • Female
  • Dermatofibrosarcoma
  • 1114 Paediatrics and Reproductive Medicine