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Chronic ear surgery in patients with syndromes and multiple congenital malformations.

Publication ,  Journal Article
O'Malley, MR; Kaylie, DM; Van Himbergen, DJ; Bennett, ML; Jackson, CG
Published in: Laryngoscope
November 2007

OBJECTIVES/HYPOTHESIS: The propensity for the development of chronic ear disease in patients with certain congenital syndromes is well described. Little is known about the efficacy of surgery in the management of such patients. This paper will review an institutional experience with the surgical management of chronic ear disease in patients with congenital syndromes or multiple major malformations associated with high rates of ear disease. STUDY DESIGN: Retrospective chart review. METHODS: Charts were reviewed to identify patients diagnosed with either a congenital syndrome or multiple major malformations with a known association with the development of chronic ear disease who underwent ear surgery for chronic ear disease (excluding tympanostomy tube placement). Syndromes encountered, surgeries performed, operative outcomes, complications, and the efficacy of ossicular chain reconstruction is reported. RESULTS: Forty-three patients with 14 different syndromes or malformations were identified. These patients underwent 66 surgical procedures on 56 ears. Seventy-nine percent of patients had undergone an ear procedure prior to presentation. Disease eradication was achieved in 64% of ears with a single procedure, and 89% of ears were controlled with two surgeries or less. Thirty-two percent of surgeries involved a canal wall down procedure, a rate similar to that seen for all patients in our practice over the past decade. When used, ossicular chain reconstruction significantly reduced the air-bone gap, resulting in hearing improvement. Results for patients with Down syndrome, Turner syndrome, and conotruncal cardiac abnormalities are discussed. Only minor complications were encountered. CONCLUSIONS: Syndromic patients and those with a major congenital malformation may present with significant chronic ear disease. Appropriate surgical management can yield successful eradication of disease with low complication rates.

Duke Scholars

Published In

Laryngoscope

DOI

ISSN

0023-852X

Publication Date

November 2007

Volume

117

Issue

11

Start / End Page

1993 / 1998

Location

United States

Related Subject Headings

  • Treatment Outcome
  • Syndrome
  • Retrospective Studies
  • Postoperative Complications
  • Otorhinolaryngology
  • Otologic Surgical Procedures
  • Middle Aged
  • Male
  • Humans
  • Female
 

Citation

APA
Chicago
ICMJE
MLA
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O’Malley, M. R., Kaylie, D. M., Van Himbergen, D. J., Bennett, M. L., & Jackson, C. G. (2007). Chronic ear surgery in patients with syndromes and multiple congenital malformations. Laryngoscope, 117(11), 1993–1998. https://doi.org/10.1097/MLG.0b013e318135449e
O’Malley, Matthew R., David M. Kaylie, Daniel J. Van Himbergen, Marc L. Bennett, and C Gary Jackson. “Chronic ear surgery in patients with syndromes and multiple congenital malformations.Laryngoscope 117, no. 11 (November 2007): 1993–98. https://doi.org/10.1097/MLG.0b013e318135449e.
O’Malley MR, Kaylie DM, Van Himbergen DJ, Bennett ML, Jackson CG. Chronic ear surgery in patients with syndromes and multiple congenital malformations. Laryngoscope. 2007 Nov;117(11):1993–8.
O’Malley, Matthew R., et al. “Chronic ear surgery in patients with syndromes and multiple congenital malformations.Laryngoscope, vol. 117, no. 11, Nov. 2007, pp. 1993–98. Pubmed, doi:10.1097/MLG.0b013e318135449e.
O’Malley MR, Kaylie DM, Van Himbergen DJ, Bennett ML, Jackson CG. Chronic ear surgery in patients with syndromes and multiple congenital malformations. Laryngoscope. 2007 Nov;117(11):1993–1998.
Journal cover image

Published In

Laryngoscope

DOI

ISSN

0023-852X

Publication Date

November 2007

Volume

117

Issue

11

Start / End Page

1993 / 1998

Location

United States

Related Subject Headings

  • Treatment Outcome
  • Syndrome
  • Retrospective Studies
  • Postoperative Complications
  • Otorhinolaryngology
  • Otologic Surgical Procedures
  • Middle Aged
  • Male
  • Humans
  • Female