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Fibrosing mediastinitis.

Publication ,  Journal Article
Rossi, SE; McAdams, HP; Rosado-de-Christenson, ML; Franks, TJ; Galvin, JR
Published in: Radiographics
2001

Fibrosing mediastinitis is a rare benign disorder caused by proliferation of acellular collagen and fibrous tissue within the mediastinum. Although many cases are idiopathic, many (and perhaps most) cases in the United States are thought to be caused by an abnormal immunologic response to Histoplasma capsulatum infection. Affected patients are typically young and present with signs and symptoms of obstruction or compression of the superior vena cava, pulmonary veins or arteries, central airways, or esophagus. There may be two types of fibrosing mediastinitis: focal and diffuse. The focal type usually manifests on computed tomographic (CT) or magnetic resonance (MR) images as a localized, calcified mass in the paratracheal or subcarinal regions of the mediastinum or in the pulmonary hila. The diffuse type manifests on CT or MR images as a diffusely infiltrating, often noncalcified mass that affects multiple mediastinal compartments. CT and MR imaging play a vital role in the diagnosis and management of fibrosing mediastinitis.

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Published In

Radiographics

DOI

ISSN

0271-5333

Publication Date

2001

Volume

21

Issue

3

Start / End Page

737 / 757

Location

United States

Related Subject Headings

  • Tomography, X-Ray Computed
  • Prognosis
  • Nuclear Medicine & Medical Imaging
  • Mediastinitis
  • Magnetic Resonance Imaging
  • Humans
  • Fibrosis
  • 3202 Clinical sciences
  • 1103 Clinical Sciences
 

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Rossi, S. E., McAdams, H. P., Rosado-de-Christenson, M. L., Franks, T. J., & Galvin, J. R. (2001). Fibrosing mediastinitis. Radiographics, 21(3), 737–757. https://doi.org/10.1148/radiographics.21.3.g01ma17737
Rossi, S. E., H. P. McAdams, M. L. Rosado-de-Christenson, T. J. Franks, and J. R. Galvin. “Fibrosing mediastinitis.Radiographics 21, no. 3 (2001): 737–57. https://doi.org/10.1148/radiographics.21.3.g01ma17737.
Rossi SE, McAdams HP, Rosado-de-Christenson ML, Franks TJ, Galvin JR. Fibrosing mediastinitis. Radiographics. 2001;21(3):737–57.
Rossi, S. E., et al. “Fibrosing mediastinitis.Radiographics, vol. 21, no. 3, 2001, pp. 737–57. Pubmed, doi:10.1148/radiographics.21.3.g01ma17737.
Rossi SE, McAdams HP, Rosado-de-Christenson ML, Franks TJ, Galvin JR. Fibrosing mediastinitis. Radiographics. 2001;21(3):737–757.
Journal cover image

Published In

Radiographics

DOI

ISSN

0271-5333

Publication Date

2001

Volume

21

Issue

3

Start / End Page

737 / 757

Location

United States

Related Subject Headings

  • Tomography, X-Ray Computed
  • Prognosis
  • Nuclear Medicine & Medical Imaging
  • Mediastinitis
  • Magnetic Resonance Imaging
  • Humans
  • Fibrosis
  • 3202 Clinical sciences
  • 1103 Clinical Sciences