Scholars@Duke

• Background
• 

  Education, Training, & Certifications

  • Ph.D., University of Florida 2007
• 

  Previous Appointments & Affiliations

  • Associate Professor of Surgery, Head and Neck Surgery & Communication Sciences, Clinical Science Departments 2013 - 2018
  • Assistant Professor of Surgery, Head and Neck Surgery & Communication Sciences, Clinical Science Departments 2008 - 2013
  • Instructor, Temporary in the Department of Surgery, Head and Neck Surgery & Communication Sciences, Clinical Science Departments 2007 - 2008
• Recognition
• 

  In the News

  • DEC 21, 2015

    WRAL

    Duke develops therapy treatment to help treat rare genetic disorder
• Research
• 

  Selected Grants

  • Understanding language production after right hemisphere stroke using lesion symptom mapping. awarded by National Institutes of Health 2022 - 2027
  • Otolaryngology Surgeon- Scientist career Path (OSSP) program awarded by National Institutes of Health 2022 - 2027
  • Expanding the Observer-Reported Communication Ability (ORCA) Measure: Measuring the communication ability of individuals with rare, neurodevelopmental disorders awarded by Food and Drug Administration 2021 - 2026
  • Understanding cognitive and neurological pathologies in infantile Pompe disease CNS awarded by Genzyme Corporation 2022 - 2024
  • High-Intensity Respiratory Muscle Training awarded by Genzyme Corporation 2022 - 2024
  • iPRO (Inspiratory Pulmonary Rehabilitation for Children with Obesity and Asthma) awarded by American Lung Association 2022 - 2024
  • Developing a management approach for patients with the "late-onset" Pompe disease GAA variant identified by newborn screening awarded by Amicus Therapeutics Corporation 2018 - 2022
  • Understanding cognitive and neurological pathologies in infantile Pompe disease CNS awarded by Genzyme Corporation 2019 - 2021
  • Determining the diagnostic utility of the identification of tongue involvement in late-onset Pompe disease (LOPD) awarded by Genzyme Corporation 2016 - 2021
  • Respiratory Muscle Training in Individuals With Pompe Disease awarded by National Institutes of Health 2016 - 2019
  • Understanding cognitive and neurological pathologies in infantile Pompe disease awarded by Genzyme Corporation 2016 - 2018
• 

  External Relationships

  • Amicus Therapeutics
  • Aspire Products LLC
  • Northern Speech Services
  • Pattern Health
  • Sanofi Genzyme
• Publications & Artistic Works
• 

  Selected Publications

  • Academic Articles

    • Jones, Harrison N., David A. Leiman, Kathryn N. Porter Starr, Rebecca North, Carl F. Pieper, Raele D. Robison, and Seth M. Cohen. “Dysphagia in Older Adults is Associated With Food Insecurity and Being Homebound.” J Appl Gerontol, May 30, 2023, 7334648231177568. https://doi.org/10.1177/07334648231177568.
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    • Zigler, Christina K., Li Lin, Molly McFatrich, Nicole Lucas, Kelly L. Gordon, Harrison N. Jones, Allyson Berent, Jennifer Panagoulias, Paula Evans, and Bryce B. Reeve. “Validation of the Observer-Reported Communication Ability (ORCA) Measure for Individuals With Angelman Syndrome.” Am J Intellect Dev Disabil 128, no. 3 (May 1, 2023): 204–18. https://doi.org/10.1352/1944-7558-128.3.204.
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    • Zigler, Christina K., Nicole Lucas, Molly McFatrich, Kelly L. Gordon, Harrison N. Jones, Allyson Berent, Jennifer Panagoulias, Paula Evans, and Bryce B. Reeve. “Exploring Communication Ability in Individuals With Angelman Syndrome: Findings From Qualitative Interviews With Caregivers.” Am J Intellect Dev Disabil 128, no. 3 (May 1, 2023): 185–203. https://doi.org/10.1352/1944-7558-128.3.185.
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    • Canick, Julia, James C. Campbell, Seth M. Cohen, Harrison N. Jones, David A. Leiman, Sudha Raman, and Kathryn N. Porter Starr. “Preoperative dysphagia risk in community-dwelling adults aged ≥50 years: Prevalence and risk factors.” Nutr Clin Pract 38, no. 1 (February 2023): 157–66. https://doi.org/10.1002/ncp.10889.
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    • Huggins, Erin, Maggie Holland, Laura E. Case, Janet Blount, Andrew P. Landstrom, Harrison N. Jones, and Priya S. Kishnani. “Early clinical phenotype of late onset Pompe disease: Lessons learned from newborn screening.” Mol Genet Metab 135, no. 3 (March 2022): 179–85. https://doi.org/10.1016/j.ymgme.2022.01.003.
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    • Bhammar, Dharini M., Harrison N. Jones, and Jason E. Lang. “Inspiratory Muscle Rehabilitation Training in Pediatrics: What Is the Evidence?” Can Respir J 2022 (2022): 5680311. https://doi.org/10.1155/2022/5680311.
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    • Wenninger, Stephan, and Harrison N. Jones. “Hypoventilation syndrome in neuromuscular disorders.” Curr Opin Neurol 34, no. 5 (October 1, 2021): 686–96. https://doi.org/10.1097/WCO.0000000000000973.
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    • Crisp, Kelly D., Amy T. Neel, Sathya Amarasekara, Jill Marcus, Gretchen Nichting, Aditi Korlimarla, Priya S. Kishnani, and Harrison N. Jones. “Assessment of Dysphonia in Children with Pompe Disease Using Auditory-Perceptual and Acoustic/Physiologic Methods.” J Clin Med 10, no. 16 (August 16, 2021). https://doi.org/10.3390/jcm10163617.
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    • Jones, Harrison N., Lisa D. Hobson-Webb, Maragatha Kuchibhatla, Kelly D. Crisp, Ashley Whyte-Rayson, Milisa T. Batten, Paul J. Zwelling, and Priya S. Kishnani. “Tongue weakness and atrophy differentiates late-onset Pompe disease from other forms of acquired/hereditary myopathy.” Molecular Genetics and Metabolism 133, no. 3 (July 2021): 261–68. https://doi.org/10.1016/j.ymgme.2021.05.005.
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    • Cohen, Seth M., Kathryn N. Porter Starr, Thomas Risoli, Hui-Jie Lee, Stephanie Misono, Harrison Jones, and Sudha Raman. “Association between Dysphagia and Surgical Outcomes across the Continuum of Frailty.” J Nutr Gerontol Geriatr 40, no. 2–3 (2021): 59–79. https://doi.org/10.1080/21551197.2021.1929644.
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    • Jones, Harrison N., Maragatha Kuchibhatla, Kelly D. Crisp, Lisa D. Hobson-Webb, Laura Case, Milisa T. Batten, Jill A. Marcus, Richard M. Kravitz, and Priya S. Kishnani. “Respiratory muscle training in late-onset Pompe disease: Results of a sham-controlled clinical trial.” Neuromuscul Disord 30, no. 11 (November 2020): 904–14. https://doi.org/10.1016/j.nmd.2020.09.023.
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    • Korlimarla, Aditi, Gail A. Spiridigliozzi, Kelly Crisp, Mrudu Herbert, Steven Chen, Michael Malinzak, Mihaela Stefanescu, et al. “Novel approaches to quantify CNS involvement in children with Pompe disease.” Neurology 95, no. 6 (August 11, 2020): e718–32. https://doi.org/10.1212/WNL.0000000000009979.
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    • Jones, Harrison N., Samuela Fernandes, William B. Hannah, Sujay Kansagra, Eileen M. Raynor, and Priya S. Kishnani. “Adenotonsillectomy should be avoided whenever possible in infantile-onset Pompe disease.” Mol Genet Metab Rep 23 (June 2020): 100574. https://doi.org/10.1016/j.ymgmr.2020.100574.
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    • Khan, Aleena A., Laura E. Case, Mrudu Herbert, Stephanie DeArmey, Harrison Jones, Kelly Crisp, Kanecia Zimmerman, Mai K. ElMallah, Sarah P. Young, and Priya S. Kishnani. “Higher dosing of alglucosidase alfa improves outcomes in children with Pompe disease: a clinical study and review of the literature.” Genet Med 22, no. 5 (May 2020): 898–907. https://doi.org/10.1038/s41436-019-0738-0.
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    • Crisp, Kelly D., Laura E. Case, Richard M. Kravitz, Priya S. Kishnani, and Harrison N. Jones. “Training, detraining, and retraining: Two 12-week respiratory muscle training regimens in a child with infantile-onset Pompe disease.” J Pediatr Rehabil Med 13, no. 1 (2020): 71–80. https://doi.org/10.3233/PRM-190601.
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    • Crowson, Matthew G., Betty C. Tong, Hui-Jie Lee, Yao Song, Stephanie Misono, Harrison N. Jones, and Seth Cohen. “Vocal Fold Paralysis/Paresis as a Marker for Poor Swallowing Outcomes After Thoracic Surgery Procedures.” Dysphagia 34, no. 6 (December 2019): 904–15. https://doi.org/10.1007/s00455-019-09987-8.
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    • Jones, Harrison N., Maragatha Kuchibhatla, Kelly D. Crisp, Lisa D. Hobson Webb, Laura Case, Milisa T. Batten, Jill A. Marcus, Richard M. Kravitz, and Priya S. Kishnani. “[Not Available].” Mol Genet Metab 127, no. 4 (August 2019): 346–54. https://doi.org/10.1016/j.ymgme.2019.05.001.
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    • Jones, Harrison N., Kelly D. Crisp, Maragatha Kuchibhatla, Leslie Mahler, Thomas Risoli, Carlee W. Jones, and Priya Kishnani. “Auditory-Perceptual Speech Features in Children With Down Syndrome.” Am J Intellect Dev Disabil 124, no. 4 (July 2019): 324–38. https://doi.org/10.1352/1944-7558-124.4.324.
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    • Crowson, Matthew G., Betty C. Tong, Hui-Jie Lee, Yao Song, David H. Harpole, Harrison N. Jones, and Seth Cohen. “Prevalence and resource utilization for vocal fold paralysis/paresis after esophagectomy.” Laryngoscope 128, no. 12 (December 2018): 2815–22. https://doi.org/10.1002/lary.27252.
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    • Keeling, Lori A., Gail A. Spiridigliozzi, Sarah J. Hart, Jane A. Baker, Harrison N. Jones, and Priya S. Kishnani. “Challenges in measuring the effects of pharmacological interventions on cognitive and adaptive functioning in individuals with Down syndrome: A systematic review.” Am J Med Genet A 173, no. 11 (November 2017): 3058–66. https://doi.org/10.1002/ajmg.a.38416.
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    • Chan, Justin, Ankit K. Desai, Zoheb B. Kazi, Kaitlyn Corey, Stephanie Austin, Lisa D. Hobson-Webb, Laura E. Case, Harrison N. Jones, and Priya S. Kishnani. “The emerging phenotype of late-onset Pompe disease: A systematic literature review.” Mol Genet Metab 120, no. 3 (March 2017): 163–72. https://doi.org/10.1016/j.ymgme.2016.12.004.
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    • Boentert, Matthias, Hélène Prigent, Katalin Várdi, Harrison N. Jones, Uwe Mellies, Anita K. Simonds, Stephan Wenninger, Emilia Barrot Cortés, and Marco Confalonieri. “Practical Recommendations for Diagnosis and Management of Respiratory Muscle Weakness in Late-Onset Pompe Disease.” Int J Mol Sci 17, no. 10 (October 17, 2016). https://doi.org/10.3390/ijms17101735.
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    • Jones, Harrison N., Kelly D. Crisp, Randall R. Robey, Laura E. Case, Richard M. Kravitz, and Priya S. Kishnani. “Respiratory muscle training (RMT) in late-onset Pompe disease (LOPD): Effects of training and detraining.” Mol Genet Metab 117, no. 2 (February 2016): 120–28. https://doi.org/10.1016/j.ymgme.2015.09.003.
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    • Horvath, Jeffrey J., Stephanie L. Austin, Laura E. Case, Karla B. Greene, Harrison N. Jones, Brian J. Soher, Priya S. Kishnani, and Mustafa R. Bashir. “Correlation between quantitative whole-body muscle magnetic resonance imaging and clinical muscle weakness in Pompe disease.” Muscle Nerve 51, no. 5 (May 2015): 722–30. https://doi.org/10.1002/mus.24437.
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    • Jones, Harrison N., Kelly D. Crisp, Priyanka Asrani, Richard Sloane, and Priya S. Kishnani. “Quantitative assessment of lingual strength in late-onset Pompe disease.” Muscle Nerve 51, no. 5 (May 2015): 731–35. https://doi.org/10.1002/mus.24523.
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    • Jones, Harrison N., Kelly D. Crisp, Tronda Moss, Katherine Strollo, Randy Robey, Jeffrey Sank, Michelle Canfield, et al. “Effects of respiratory muscle training (RMT) in children with infantile-onset Pompe disease and respiratory muscle weakness.” J Pediatr Rehabil Med 7, no. 3 (2014): 255–65. https://doi.org/10.3233/PRM-140294.
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    • Hobson-Webb, Lisa D., Harrison N. Jones, and Priya S. Kishnani. “Oropharyngeal dysphagia may occur in late-onset Pompe disease, implicating bulbar muscle involvement.” Neuromuscul Disord 23, no. 4 (April 2013): 319–23. https://doi.org/10.1016/j.nmd.2012.12.003.
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    • Horvath, Jeffrey J., Stephanie L. Austin, Harrison N. Jones, Elizabeth J. Drake, Laura E. Case, Brian J. Soher, Mustafa R. Bashir, and Priya S. Kishnani. “Bulbar muscle weakness and fatty lingual infiltration in glycogen storage disorder type IIIa.” Mol Genet Metab 107, no. 3 (November 2012): 496–500. https://doi.org/10.1016/j.ymgme.2012.09.025.
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    • Prater, Sean N., Suhrad G. Banugaria, Stephanie M. DeArmey, Eleanor G. Botha, Erin M. Stege, Laura E. Case, Harrison N. Jones, et al. “The emerging phenotype of long-term survivors with infantile Pompe disease.” Genet Med 14, no. 9 (September 2012): 800–810. https://doi.org/10.1038/gim.2012.44.
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    • Jacks, A., K. L. Haley, B. L. Scott, and H. Jones. “Auditory-perceptual analysis of dysarthria in bilateral striatopallidodentate calcinosis (fahr's disease).” Journal of Medical Speech Language Pathology 20, no. 1 (March 1, 2012): 29–34.
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    • Spiridigliozzi, Gail A., James H. Heller, Laura E. Case, Harrison N. Jones, and Priya S. Kishnani. “Early cognitive development in children with infantile Pompe disease.” Mol Genet Metab 105, no. 3 (March 2012): 428–32. https://doi.org/10.1016/j.ymgme.2011.10.012.
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    • Mahler, Leslie A., and Harrison N. Jones. “Intensive treatment of dysarthria in two adults with Down syndrome.” Dev Neurorehabil 15, no. 1 (2012): 44–53. https://doi.org/10.3109/17518423.2011.632784.
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    • Murdoch, B., T. Whitehill, M. De Letter, and H. Jones. “Communication impairments in parkinson's disease.” Parkinson’S Disease, December 1, 2011. https://doi.org/10.4061/2011/234657.
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    • Dubrovsky, Alberto, Jose Corderi, Min Lin, Priya S. Kishnani, and Harrison N. Jones. “Expanding the phenotype of late-onset Pompe disease: tongue weakness: a new clinical observation.” Muscle Nerve 44, no. 6 (December 2011): 897–901. https://doi.org/10.1002/mus.22202.
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    • Jones, Harrison N., Tronda Moss, Laurie Edwards, and Priya S. Kishnani. “Increased inspiratory and expiratory muscle strength following respiratory muscle strength training (RMST) in two patients with late-onset Pompe disease.” Mol Genet Metab 104, no. 3 (November 2011): 417–20. https://doi.org/10.1016/j.ymgme.2011.05.006.
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    • Jones, Harrison N., Tyler J. Story, Timothy A. Collins, Daniel Dejoy, and Christopher L. Edwards. “Multidisciplinary assessment and diagnosis of conversion disorder in a patient with foreign accent syndrome.” Behav Neurol 24, no. 3 (2011): 245–55. https://doi.org/10.3233/BEN-2011-0332.
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    • Jones, Harrison N., Carolyn W. Muller, Min Lin, Suhrad G. Banugaria, Laura E. Case, Jennifer S. Li, Gwendolyn O’Grady, James H. Heller, and Priya S. Kishnani. “Oropharyngeal dysphagia in infants and children with infantile Pompe disease.” Dysphagia 25, no. 4 (December 2010): 277–83. https://doi.org/10.1007/s00455-009-9252-x.
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    • Jones, Harrison N., Diane L. Kendall, Michael S. Okun, Samuel S. Wu, Craig Velozo, Hubert H. Fernandez, Kristie A. Spencer, and John C. Rosenbek. “Speech motor program maintenance, but not switching, is enhanced by left-hemispheric deep brain stimulation in Parkinson's disease.” Int J Speech Lang Pathol 12, no. 5 (October 2010): 385–98. https://doi.org/10.3109/17549507.2010.491870.
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    • Jones, H. N., R. Shrivastav, S. S. Wu, E. K. Plowman-Prine, and J. C. Rosenbek. “Fundamental frequency and intensity mean and variability before and after two behavioral treatments for aprosodia.” Journal of Medical Speech Language Pathology 17, no. 1 (March 1, 2009): 45–53.
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    • Muller, C. W., H. N. Jones, G. O’Grady, H. A. Suárez, J. H. Heller, and P. S. Kishnani. “Language and speech function in children with infantile Pompe disease.” Journal of Pediatric Neurology 7, no. 2 (January 1, 2009): 147–56. https://doi.org/10.3233/JPN-2009-0291.
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    • Jones, H. N., N. J. Donovan, C. M. Sapienza, R. Shrivastav, H. H. Fernandez, and J. C. Rosenbek. “Expiratory muscle strength training in the treatment of mixed dysarthria in a patient with Lance-Adams syndrome.” Journal of Medical Speech Language Pathology 14, no. 3 (September 1, 2006): 207–17.

  • Conference Papers

    • Huggins, Erin, Maggie Holland, Laura E. Case, Janet Blount, Andrew P. Landstrom, Harrison N. Jones, and Priya S. Kishnani. “Early clinical phenotype of late-onset Pompe disease: Lessons learned from newborn screening.” In Molecular Genetics and Metabolism, 135:S57–S57. Elsevier BV, 2022. https://doi.org/10.1016/j.ymgme.2021.11.141.
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    • Lucas, Nicole, Molly McFatrich, Christina K. Zigler, Allyson Berent, Paula Evans, Kelly Gordon, Harrison N. Jones, Jennifer Panagoulias, and Bryce B. Reeve. “Designing measures of communication ability in individuals with Angelman syndrome.” In Quality of Life Research, 28:S117–S117. SPRINGER, 2019.
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    • Jones, Harrison N., Kaylea Nicholson, and Kelly D. Crisp. “Respiratory muscle training in late-onset Pompe disease.” In Molecular Genetics and Metabolism, 120:S72–S72. Elsevier BV, 2017. https://doi.org/10.1016/j.ymgme.2016.11.169.
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