Wilms Tumor After Orthotopic Liver Transplant in a Patient With Alagille Syndrome.
Published
Journal Article
We present a case of Wilms Tumor in a patient with Alagille syndrome 10 months after liver transplant. We explore a suggested genetic connection between these 2 diseases. In children with Wilms Tumor, we propose a pathoembryologic explanation for not just the tumor, but also for the cause of associated benign ureteral and renal parenchymal aberrancies that are commonly seen in the Alagille population. We also discuss the diagnostic and therapeutic challenges that can arise in a liver transplant patient with Alagille syndrome who subsequently develops a renal mass.
Full Text
Duke Authors
- Carlos, Evan
- Madden, John Francis
- Rice, Henry Elliot
- Routh, Jonathan Charles
- Vikraman Sushama, Deepak
Cited Authors
- Carlos, EC; Ajay, D; Muniz-Alers, S; Wechsler, DS; Sushama, DV; Rice, HE; Madden, J; Routh, JC
Published Date
- November 2018
Published In
Volume / Issue
- 121 /
Start / End Page
- 171 - 174
PubMed ID
- 29879405
Pubmed Central ID
- 29879405
Electronic International Standard Serial Number (EISSN)
- 1527-9995
Digital Object Identifier (DOI)
- 10.1016/j.urology.2018.05.020
Language
- eng
Conference Location
- United States