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Keratosis follicularis spinulosa decalvans in a family.

Publication ,  Journal Article
Bellet, JS; Kaplan, AL; Selim, MA; Olsen, EA
Published in: J Am Acad Dermatol
March 2008

Keratosis follicularis spinulosa decalvans (KFSD) is a rare condition characterized by diffuse keratosis pilaris with a scarring alopecia of the scalp and associated photophobia, facial erythema, and palmoplantar keratoderma. Although initially described as a sex-linked disorder, several different inheritance patterns have been observed. We describe a patient whose father and sister were also affected with this condition, consistent with an autosomal dominant genetic transmission. Multiple topical and systemic treatments have been unsuccessful in this patient, attesting to the treatment refractoriness typically seen in KFSD.

Duke Scholars

Published In

J Am Acad Dermatol

DOI

EISSN

1097-6787

Publication Date

March 2008

Volume

58

Issue

3

Start / End Page

499 / 502

Location

United States

Related Subject Headings

  • Photophobia
  • Middle Aged
  • Male
  • Humans
  • Genes, Dominant
  • Female
  • Face
  • Eyebrows
  • Erythema
  • Dermatology & Venereal Diseases
 

Citation

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ICMJE
MLA
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Bellet, J. S., Kaplan, A. L., Selim, M. A., & Olsen, E. A. (2008). Keratosis follicularis spinulosa decalvans in a family. J Am Acad Dermatol, 58(3), 499–502. https://doi.org/10.1016/j.jaad.2007.03.028
Bellet, Jane S., Andrew L. Kaplan, M Angelica Selim, and Elise A. Olsen. “Keratosis follicularis spinulosa decalvans in a family.J Am Acad Dermatol 58, no. 3 (March 2008): 499–502. https://doi.org/10.1016/j.jaad.2007.03.028.
Bellet JS, Kaplan AL, Selim MA, Olsen EA. Keratosis follicularis spinulosa decalvans in a family. J Am Acad Dermatol. 2008 Mar;58(3):499–502.
Bellet, Jane S., et al. “Keratosis follicularis spinulosa decalvans in a family.J Am Acad Dermatol, vol. 58, no. 3, Mar. 2008, pp. 499–502. Pubmed, doi:10.1016/j.jaad.2007.03.028.
Bellet JS, Kaplan AL, Selim MA, Olsen EA. Keratosis follicularis spinulosa decalvans in a family. J Am Acad Dermatol. 2008 Mar;58(3):499–502.
Journal cover image

Published In

J Am Acad Dermatol

DOI

EISSN

1097-6787

Publication Date

March 2008

Volume

58

Issue

3

Start / End Page

499 / 502

Location

United States

Related Subject Headings

  • Photophobia
  • Middle Aged
  • Male
  • Humans
  • Genes, Dominant
  • Female
  • Face
  • Eyebrows
  • Erythema
  • Dermatology & Venereal Diseases