Rebecca Hatcher Buckley
Professor Emeritus of Pediatrics
The overall emphasis of Dr. Buckley's research is in human T,B and NK cell development and in aberrations in their development and regulation. The work involves three particular areas of investigation: 1) the cellular and molecular bases of genetically-determined human immunodeficiency diseases, 2) the use of bone marrow stem cells to cure genetically-determined immunodeficiency diseases, and 3) the use of human SCID bone marrow stem cell chimeras to study human thymic education, T and B cell ontogeny, tolerance induction and MHC restriction mechanisms. Methodology includes monoclonal antibody (mAb) analyses of lymphocyte phenotypes, a variety of T cell and natural killer (NK) cell functional assays, studies of thymic output by T cell receptor recombination excision circle measurement, studies of T cell diversity by spectratyping, studies of T cell longevity by telomere analysis and assessment of B cell differentiation and function. A unique resource available for her studies is the largest population of patients with genetically-determined immunodeficiency diseases in the U.S., which includes the largest population in the world of longterm SCID chimeras treated at a single center, some of whom have been studied and followed for more than 37 years. The administration of rigorously T cell depleted haploidentical bone marrow stem cells to SCID recipients without pre-transplant conditioning or post-transplant use of immunosuppressive drugs to prevent GVHD provides an unmanipulated system for studying human thymic education, T and B cell ontogeny, MHC restriction mechanisms and tolerance induction. Studies to identify mutations in patients with primary immunodeficiency are continuing, particularly in those with SCID.
Current Appointments & Affiliations
- Professor Emeritus of Pediatrics, Pediatrics, Allergy and Immunology, Pediatrics 2022
- Member of the Duke Cancer Institute, Duke Cancer Institute, Institutes and Centers 1965
Contact Information
- 426 Jones Building, Durham, NC 27710
- Box 2898 Med Ctr, Durham, NC 27710
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buckl003@mc.duke.edu
(919) 684-3204
- Background
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Education, Training, & Certifications
- M.D., University of North Carolina - Chapel Hill 1958
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Previous Appointments & Affiliations
- Professor of Immunology in the Department of Immunology, Immunology, Basic Science Departments 1994 - 2022
- Professor of Pediatrics, Pediatrics, Allergy and Immunology, Pediatrics 1976 - 2022
- James Buren Sidbury Distinguished Professor of Pediatrics, in the School of Medicine, Pediatrics, Allergy and Immunology, Pediatrics 1979 - 2022
- Chief, Allergy / Immunology, Pediatrics, Allergy and Immunology, Pediatrics 1974 - 2003
- Professor of Immunology in the Department of Microbiology and Immunology, Molecular Genetics and Microbiology, Basic Science Departments 1991 - 1992
- Professor of Immunology in the Department of Microbiology and Immunology, Pediatrics, Clinical Science Departments 1972 - 1991
- Associate Professor of Pediatrics with tenure in the Department of Pediatrics, Pediatrics, Clinical Science Departments 1972 - 1976
- Assistant Professor of Pediatrics, Pediatrics, Clinical Science Departments 1968 - 1972
- Assistant Professor of Immunology in the Department of Microbiology and Immunology, Pediatrics, Clinical Science Departments 1969 - 1972
- Associate in the Department of Microbiology and Immunology, Pediatrics, Clinical Science Departments 1968 - 1969
- Recognition
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In the News
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MAR 15, 2021 Medical Center Archives -
OCT 20, 2015 WRAL -
OCT 20, 2015 WRAL -
MAY 28, 2015 WRAL -
MAY 28, 2015 WRAL
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Awards & Honors
- Honorary Degree of Doctor of Sciences. University of North Carolina. May 12, 2019
- 2019 Distinguished Fellow by the American Association of immunologists’ . American Association of Immunologists. May 9, 2019
- John Howland Award. American Pediatric Society. 2014
- Member. National Academy of Science. 2011
- Abbott Laboratories Award in Clinical and Diagnostic Immunology. American Society for Microbiology. 2006
- Member. Institute of Medicine of The National Academies. 2003
- Expertise
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Subject Headings
- Acute Disease
- Adenosine Deaminase
- Agammaglobulinemia
- Age Factors
- Aged
- Allergens
- Allergy and Immunology
- Amino Acid Sequence
- Antibodies
- Antibodies, Anti-Idiotypic
- Antibodies, Viral
- Antibody Formation
- Antibody Specificity
- Antibody-Producing Cells
- Antigen-Antibody Reactions
- Antigen-Presenting Cells
- Antigens, CD34
- Antigens, CD40
- Antigens, CD45
- Antigens, Surface
- Apoptosis
- Asthma
- Ataxia Telangiectasia
- Australia
- B-Lymphocytes
- Blood
- Blood Protein Disorders
- Bone Marrow Cells
- Bone Marrow Transplantation
- Brain
- CD40 Ligand
- CD8-Positive T-Lymphocytes
- Candida albicans
- Candidiasis
- Cause of Death
- Cell Division
- Cell Line
- Cell Line, Transformed
- Cell Membrane
- Cerebrospinal Fluid
- Child, Preschool
- Chimera
- Chimerism
- Chromatography, Ion Exchange
- Chromosome Deletion
- Chromosomes, Human, Pair 14
- Chromosomes, Human, Pair 4
- Chronic Disease
- Clinical Trial
- Cohort Studies
- Colon
- Common Variable Immunodeficiency
- Consanguinity
- Cytokines
- DNA
- DNA Mutational Analysis
- DNA Primers
- DNA Transposable Elements
- Databases, Factual
- Dendritic Cells
- Deoxyadenosines
- DiGeorge Syndrome
- Disease Susceptibility
- Double-Blind Method
- Duodenum
- Echovirus 9
- Echovirus Infections
- Enterovirus B, Human
- Esophagitis
- Exons
- Fatal Outcome
- Female
- Flow Cytometry
- Follow-Up Studies
- Frameshift Mutation
- Gastroesophageal Reflux
- Gene Deletion
- Gene Frequency
- Gene therapy
- Genes, Dominant
- Genes, Recessive
- Genetic Carrier Screening
- Genetic Diseases, X-Linked
- Genetic Markers
- Genetic Predisposition to Disease
- Genetic Therapy
- Genotype
- Giardiasis
- Goats
- Graft Survival
- Graft vs Host Disease
- Granulocytes
- Granulomatous Disease, Chronic
- Growth
- HLA Antigens
- Haplotypes
- Hematopoietic Stem Cell Transplantation
- Hematopoietic Stem Cells
- Herpesvirus 4, Human
- Homozygote
- Humans
- Hypersensitivity
- Hypersensitivity, Immediate
- IgA Deficiency
- Immune Adherence Reaction
- Immune Sera
- Immune System
- Immune System Diseases
- Immunity, Maternally-Acquired
- Immunization, Passive
- Immunocompromised Host
- Immunodiffusion
- Immunoenzyme Techniques
- Immunoglobulin A
- Immunoglobulin Class Switching
- Immunoglobulin D
- Immunoglobulin E
- Immunoglobulin G
- Immunoglobulin Isotypes
- Immunoglobulin M
- Immunoglobulin mu-Chains
- Immunoglobulins
- Immunoglobulins, Intravenous
- Immunologic Deficiency Syndromes
- Immunologic Memory
- Immunologic Techniques
- Immunophenotyping
- Immunotherapy
- Incidence
- Infant
- Infant, Newborn
- Infection
- Infection Control
- Injections, Intravenous
- Interleukin-13
- Interleukin-2
- Interleukin-4
- Intestine, Small
- Janus Kinase 3
- Kidney Neoplasms
- Killer Cells, Natural
- Lectins
- Leiomyomatosis
- Leukocytes
- Leukocytes, Mononuclear
- Liver Function Tests
- Loss of Heterozygosity
- Lymph Nodes
- Lymphangiectasis, Intestinal
- Lymphatic Diseases
- Lymphocyte Activation
- Lymphocyte Count
- Lymphocytes
- Lymphopenia
- Lymphoproliferative Disorders
- Major Histocompatibility Complex
- Male
- Maltose
- Medical Records
- Membrane Glycoproteins
- Mice
- Microfluidic Analytical Techniques
- Middle Aged
- Mitogens
- Molecular Sequence Data
- Monocytes
- Multicenter Studies as Topic
- Mutagenesis, Site-Directed
- Mutation
- Myelodysplastic Syndromes
- Neonatal Screening
- Neutrophils
- Nucleoside Deaminases
- Pediatrics
- Pedigree
- Phagocytes
- Phenotype
- Phytohemagglutinins
- Pneumonia, Aspiration
- Point Mutation
- Polymerase Chain Reaction
- Polymorphism, Single Nucleotide
- Polymorphism, Single-Stranded Conformational
- Practice Guidelines as Topic
- Precursor Cell Lymphoblastic Leukemia-Lymphoma
- Prevalence
- Prospective Studies
- Protein-Tyrosine Kinases
- RNA
- RNA Splicing
- RNA, Messenger
- Rabbits
- Radioimmunoassay
- Receptors, Antigen, B-Cell
- Receptors, Antigen, T-Cell
- Receptors, Cytokine
- Receptors, Interleukin
- Receptors, Interleukin-2
- Receptors, Interleukin-7
- Registries
- Retreatment
- Retrospective Studies
- Rhinitis, Allergic, Seasonal
- Rosette Formation
- S-Adenosylhomocysteine
- STAT6 Transcription Factor
- Sequence Analysis, DNA
- Serotherapy
- Severe Combined Immunodeficiency
- Sheep
- Siblings
- Signal Transduction
- Skin Tests
- Survival Analysis
- Survival Rate
- T-Lymphocytes
- Thymus Gland
- Tomography, X-Ray Computed
- Trans-Activators
- Transduction, Genetic
- Transplantation Chimera
- Transplantation Conditioning
- Transplantation Immunology
- Uniparental Disomy
- United States
- Unrelated Donors
- Up-Regulation
- Virus Diseases
- Volunteers
- Vomiting
- Wiskott-Aldrich Syndrome
- X Chromosome
- Young Adult
- Research
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Selected Grants
- Safety and Efficacy of Hizentra in Pediatric BMT awarded by Carolinas HealthCare System 2017 - 2018
- Training Program in Inflammatory and Immunological Diseases awarded by National Institutes of Health 1980 - 2017
- Identifying the Causes of Primary immunodeficiency through Next Generation Sequencing awarded by Baxter Healthcare Corporation 2014 - 2015
- Prospective Study of SCID Infants who receive Hematopoietic Cell Therapy awarded by University of California - San Francisco 2009 - 2014
- Identification of Disease-Causing Mutations in SCID Using Exome-Wide Sequencing awarded by National Institutes of Health 2009 - 2012
- Mechanisms of Allogeneic Stem Cell Education in SCID awarded by National Institutes of Health 1999 - 2012
- Development And Persistence Of Immunity In SCID Chimeras awarded by National Institutes of Health 1998 - 2010
- Mentored Clinical Research Scholar Program awarded by National Institutes of Health 2002 - 2006
- Research Training in Allergy and Clinical Immunology awarded by National Institutes of Health 1998 - 2000
- Mechanisms And Therapy Of Primary Immunodeficiency awarded by National Institutes of Health 1996 - 1999
- Mechanisms And Therapy Of Primary Immunodeficiency awarded by National Institutes of Health 1995 - 1999
- Mechanisms and therapy of primary immunodeficiency awarded by National Institutes of Health 1995 - 1999
- Research Training In Allergy And Clinical Immunology awarded by National Institutes of Health 1907 - 1999
- Center For Developmental Immunology And Host Defense awarded by National Institutes of Health 1996 - 1998
- Regulation Of Ige Synthesis By Cytokines awarded by National Institutes of Health 1997 - 1998
- Regulation Of Human Ige Synthesis By Cytokines awarded by National Institutes of Health 1996 - 1998
- The Regulation Of Human Ige Syntehsis By Cytokines awarded by National Institutes of Health 1993 - 1998
- Center For Developmental Immunology And Host Defense awarded by National Institutes of Health 1992 - 1997
- Haploidentical Stem Cell Education In The Human Thymus awarded by National Institutes of Health 1996 - 1997
- The Regulation Of Human 1ge Synthesis By Cytokines awarded by National Institutes of Health 1989 - 1994
- The Regulation Of Human Ige Syntheses By Cytokines awarded by National Institutes of Health 1991 - 1992
- The Regulation Of Human Ige Synthesis By Cytokines awarded by National Institutes of Health 1990 - 1992
- Immunoregulation In Eczema And Other Atopic Diseases awarded by National Institutes of Health 1986 - 1991
- Immunoregulation In Eczema And Other Atopic Disorders awarded by National Institutes of Health 1987 - 1989
- Allergy And Clinical Immunology awarded by National Institutes of Health 1986 - 1987
- Allergy And Clinial Immunology awarded by National Institutes of Health 1986 - 1987
- Lymphocyte Responses In Immaturity And Immunodeficiency awarded by National Institutes of Health 1986 - 1987
- In Vitro Studies Of Human Ige Synthesis awarded by National Institutes of Health 1985 - 1986
- Immunoregulation In Ec\Ema And Other Atopic Diseases awarded by National Institutes of Health 1985 - 1986
- Publications & Artistic Works
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Selected Publications
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Academic Articles
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Labrosse, Roxane, Ines Boufaied, Benoîte Bourdin, Saideep Gona, Haley E. Randolph, Brent R. Logan, Sara Bourbonnais, et al. “Aberrant T-cell exhaustion in severe combined immunodeficiency survivors with poor T-cell reconstitution after transplantation.” J Allergy Clin Immunol 151, no. 1 (January 2023): 260–71. https://doi.org/10.1016/j.jaci.2022.08.004.Full Text Link to Item
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Dvorak, Christopher C., Elie Haddad, Jennifer Heimall, Elizabeth Dunn, Morton J. Cowan, Sung-Yun Pai, Neena Kapoor, et al. “The diagnosis of severe combined immunodeficiency: Implementation of the PIDTC 2022 Definitions.” J Allergy Clin Immunol, November 28, 2022. https://doi.org/10.1016/j.jaci.2022.10.021.Full Text Link to Item
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Dvorak, Christopher C., Elie Haddad, Jennifer Heimall, Elizabeth Dunn, Rebecca H. Buckley, Donald B. Kohn, Morton J. Cowan, et al. “The diagnosis of severe combined immunodeficiency (SCID): The Primary Immune Deficiency Treatment Consortium (PIDTC) 2022 Definitions.” J Allergy Clin Immunol, November 28, 2022. https://doi.org/10.1016/j.jaci.2022.10.022.Full Text Link to Item
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Cuvelier, Geoffrey D. E., Brent R. Logan, Susan E. Prockop, Rebecca H. Buckley, Caroline Y. Kuo, Linda M. Griffith, Xuerong Liu, et al. “Outcomes following treatment for ADA-deficient severe combined immunodeficiency: a report from the PIDTC.” Blood 140, no. 7 (August 18, 2022): 685–705. https://doi.org/10.1182/blood.2022016196.Full Text Link to Item
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Chandrakasan, Shanmuganathan, Sharat Chandra, Chengyu Prince, Lisa J. Kobrynski, Laura Lucas, Kiran Patel, Jolan Walter, et al. “HSCT using carrier donors for CD40L deficiency results in excellent immune function and higher CD40L expression in cTfh.” Blood Adv 6, no. 12 (June 28, 2022): 3751–55. https://doi.org/10.1182/bloodadvances.2021006905.Full Text Link to Item
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Durkee-Shock, Jessica, Anqing Zhang, Hua Liang, Hannah Wright, Julieann Magnusson, Elizabeth Garabedian, Rebecca A. Marsh, Kathleen E. Sullivan, Michael D. Keller, and Michael D. USIDNET Consortium. “Morbidity, Mortality, and Therapeutics in Combined Immunodeficiency: Data From the USIDNET Registry.” J Allergy Clin Immunol Pract 10, no. 5 (May 2022): 1334-1341.e6. https://doi.org/10.1016/j.jaip.2022.01.042.Full Text Link to Item
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Hardin, Olga, Yuliya Lokhnygina, and Rebecca H. Buckley. “Long-Term Clinical Outcomes of Severe Combined Immunodeficiency Patients Given Nonablative Marrow Transplants.” J Allergy Clin Immunol Pract 10, no. 4 (April 2022): 1077–83. https://doi.org/10.1016/j.jaip.2021.11.032.Full Text Link to Item
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Kohn, Donald B., Claire Booth, Kit L. Shaw, Jinhua Xu-Bayford, Elizabeth Garabedian, Valentina Trevisan, Denise A. Carbonaro-Sarracino, et al. “Autologous Ex Vivo Lentiviral Gene Therapy for Adenosine Deaminase Deficiency.” N Engl J Med 384, no. 21 (May 27, 2021): 2002–13. https://doi.org/10.1056/NEJMoa2027675.Full Text Link to Item
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Dorsey, Morna, Nicola A. M. Wright, Natalia S. Chaimowitz, Blachy J. Dávila Saldaña, Holly Miller, Michael D. Keller, Monica S. Thakar, et al. “Correction to: Infections in Infants with SCID: Isolation, Infection Screening and Prophylaxis in PIDTC Centers.” J Clin Immunol 41, no. 2 (February 2021): 498–500. https://doi.org/10.1007/s10875-020-00917-0.Full Text Link to Item
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Dorsey, Morna J., Nicola A. M. Wright, Natalia S. Chaimowitz, Blachy J. Dávila Saldaña, Holly Miller, Michael D. Keller, Monica S. Thakar, et al. “Infections in Infants with SCID: Isolation, Infection Screening, and Prophylaxis in PIDTC Centers.” J Clin Immunol 41, no. 1 (January 2021): 38–50. https://doi.org/10.1007/s10875-020-00865-9.Full Text Link to Item
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Kuo, Caroline Y., Elizabeth Garabedian, Jennifer Puck, Morton J. Cowan, Kathleen E. Sullivan, Rebecca H. Buckley, Charlotte Cunningham-Rundles, Rebecca Marsh, Fabio Candotti, and Donald B. Kohn. “Adenosine Deaminase (ADA)-Deficient Severe Combined Immune Deficiency (SCID) in the US Immunodeficiency Network (USIDNet) Registry.” J Clin Immunol 40, no. 8 (November 2020): 1124–31. https://doi.org/10.1007/s10875-020-00857-9.Full Text Link to Item
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Buckley, Rebecca H. “Conversations with Founders of the Field of Human Inborn Errors of Immunity.” J Clin Immunol 40, no. 1 (January 2020): 1–8. https://doi.org/10.1007/s10875-019-00736-y.Full Text Link to Item
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Chan, Alice Y., Jennifer W. Leiding, Xuerong Liu, Brent R. Logan, Lauri M. Burroughs, Eric J. Allenspach, Suzanne Skoda-Smith, et al. “Hematopoietic Cell Transplantation in Patients With Primary Immune Regulatory Disorders (PIRD): A Primary Immune Deficiency Treatment Consortium (PIDTC) Survey.” Front Immunol 11 (2020): 239. https://doi.org/10.3389/fimmu.2020.00239.Full Text Link to Item
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O’Shea, John J., John I. Gallin, John P. Atkinson, Thomas Lawley, Dean D. Metcalf, Warren Strober, Rebecca H. Buckley, and Anthony S. Fauci. “Michael M. Frank: February 28, 1937–August 1, 2019.” Journal of Allergy and Clinical Immunology 144, no. 6 (December 2019): 1507–8. https://doi.org/10.1016/j.jaci.2019.10.011.Full Text
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Baloh, Carolyn, Anupama Reddy, Michele Henson, Katherine Prince, Rebecca Buckley, and Patricia Lugar. “30-Year Review of Pediatric- and Adult-Onset CVID: Clinical Correlates and Prognostic Indicators.” J Clin Immunol 39, no. 7 (October 2019): 678–87. https://doi.org/10.1007/s10875-019-00674-9.Full Text Link to Item
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Buckley, Rebecca H. “SCID: A Pediatric Emergency.” N C Med J 80, no. 1 (2019): 55–56. https://doi.org/10.18043/ncm.80.1.55.Full Text Link to Item
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Dvorak, Christopher C., Elie Haddad, Rebecca H. Buckley, Morton J. Cowan, Brent Logan, Linda M. Griffith, Donald B. Kohn, et al. “The genetic landscape of severe combined immunodeficiency in the United States and Canada in the current era (2010-2018).” J Allergy Clin Immunol 143, no. 1 (January 2019): 405–7. https://doi.org/10.1016/j.jaci.2018.08.027.Full Text Link to Item
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Belderbos, Mirjam E., Andrew R. Gennery, Christopher C. Dvorak, Henric-Jan Blok, Dirk-Jan Eikema, Juliana M. F. Silva, Paul Veys, et al. “Outcome of domino hematopoietic stem cell transplantation in human subjects: An international case series.” J Allergy Clin Immunol 142, no. 5 (November 2018): 1628-1631.e4. https://doi.org/10.1016/j.jaci.2018.06.030.Full Text Link to Item
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Haddad, Elie, Brent R. Logan, Linda M. Griffith, Rebecca H. Buckley, Roberta E. Parrott, Susan E. Prockop, Trudy N. Small, et al. “SCID genotype and 6-month posttransplant CD4 count predict survival and immune recovery.” Blood 132, no. 17 (October 25, 2018): 1737–49. https://doi.org/10.1182/blood-2018-03-840702.Full Text Link to Item
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Miggelbrink, Alexandra M., Brent R. Logan, Rebecca H. Buckley, Roberta E. Parrott, Christopher C. Dvorak, Neena Kapoor, Hisham Abdel-Azim, et al. “B-cell differentiation and IL-21 response in IL2RG/JAK3 SCID patients after hematopoietic stem cell transplantation.” Blood 131, no. 26 (June 28, 2018): 2967–77. https://doi.org/10.1182/blood-2017-10-809822.Full Text Link to Item
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Giannelou, Angeliki, Hongying Wang, Qing Zhou, Yong Hwan Park, Mones S. Abu-Asab, Kris Ylaya, Deborah L. Stone, et al. “Aberrant tRNA processing causes an autoinflammatory syndrome responsive to TNF inhibitors.” Ann Rheum Dis 77, no. 4 (April 2018): 612–19. https://doi.org/10.1136/annrheumdis-2017-212401.Full Text Link to Item
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Mayor, Paul C., Kevin H. Eng, Kelly L. Singel, Scott I. Abrams, Kunle Odunsi, Kirsten B. Moysich, Ramsay Fuleihan, et al. “Cancer in primary immunodeficiency diseases: Cancer incidence in the United States Immune Deficiency Network Registry.” J Allergy Clin Immunol 141, no. 3 (March 2018): 1028–35. https://doi.org/10.1016/j.jaci.2017.05.024.Full Text Link to Item
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Farmer, J. R., M. S. Ong, S. Barmettler, L. M. Yonker, R. Fuleihan, K. E. Sullivan, C. Cunningham-Rundles, et al. “Common variable immunodeficiency non-infectious disease endotypes redefined using unbiased network clustering in large electronic datasets.” Frontiers in Immunology 8, no. JAN (January 9, 2018). https://doi.org/10.3389/fimmu.2017.01740.Full Text
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Slack, James, Michael H. Albert, Dmitry Balashov, Bernd H. Belohradsky, Alice Bertaina, Jack Bleesing, Claire Booth, et al. “Outcome of hematopoietic cell transplantation for DNA double-strand break repair disorders.” J Allergy Clin Immunol 141, no. 1 (January 2018): 322-328.e10. https://doi.org/10.1016/j.jaci.2017.02.036.Full Text Open Access Copy Link to Item
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Gernez, Yael, Alexandra F. Freeman, Steven M. Holland, Elizabeth Garabedian, Niraj C. Patel, Jennifer M. Puck, Kathleen E. Sullivan, et al. “Autosomal Dominant Hyper-IgE Syndrome in the USIDNET Registry.” J Allergy Clin Immunol Pract 6, no. 3 (2018): 996–1001. https://doi.org/10.1016/j.jaip.2017.06.041.Full Text Link to Item
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Heimall, Jennifer, Brent R. Logan, Morton J. Cowan, Luigi D. Notarangelo, Linda M. Griffith, Jennifer M. Puck, Donald B. Kohn, et al. “Immune reconstitution and survival of 100 SCID patients post-hematopoietic cell transplant: a PIDTC natural history study.” Blood 130, no. 25 (December 21, 2017): 2718–27. https://doi.org/10.1182/blood-2017-05-781849.Full Text Open Access Copy Link to Item
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Heimall, Jennifer, Rebecca H. Buckley, Jennifer Puck, Thomas A. Fleisher, Andrew R. Gennery, Elie Haddad, Benedicte Neven, et al. “Recommendations for Screening and Management of Late Effects in Patients with Severe Combined Immunodeficiency after Allogenic Hematopoietic Cell Transplantation: A Consensus Statement from the Second Pediatric Blood and Marrow Transplant Consortium International Conference on Late Effects after Pediatric HCT.” Biol Blood Marrow Transplant 23, no. 8 (August 2017): 1229–40. https://doi.org/10.1016/j.bbmt.2017.04.026.Full Text Link to Item
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Heimall, Jennifer, Jennifer Puck, Rebecca Buckley, Thomas A. Fleisher, Andrew R. Gennery, Benedicte Neven, Mary Slatter, et al. “Current Knowledge and Priorities for Future Research in Late Effects after Hematopoietic Stem Cell Transplantation (HCT) for Severe Combined Immunodeficiency Patients: A Consensus Statement from the Second Pediatric Blood and Marrow Transplant Consortium International Conference on Late Effects after Pediatric HCT.” Biol Blood Marrow Transplant 23, no. 3 (March 2017): 379–87. https://doi.org/10.1016/j.bbmt.2016.12.619.Full Text Link to Item
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Buckley, Rebecca H. “Screening for primary immunodeficiency diseases and follow-up testing.” Mlo Med Lab Obs 48, no. 11 (November 2016): 28.Link to Item
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Wu, Eveline Y., Lauren Ehrlich, Brian Handly, Donald P. Frush, and Rebecca H. Buckley. “Clinical and imaging considerations in primary immunodeficiency disorders: an update.” Pediatr Radiol 46, no. 12 (November 2016): 1630–44. https://doi.org/10.1007/s00247-016-3684-x.Full Text Link to Item
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Sayour, Elias J., Talal Mousallem, David Van Mater, Endi Wang, Paul Martin, Rebecca H. Buckley, and Raymond C. Barfield. “Bone marrow transplantation for CVID-like humoral immune deficiency associated with red cell aplasia.” Pediatr Blood Cancer 63, no. 10 (October 2016): 1856–59. https://doi.org/10.1002/pbc.26092.Full Text Link to Item
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Buckley, Rebecca H. “50 Years Ago in TheJournal ofPediatrics: Nutritional and Antigenic Effects of 2 Bovine Milk Preparations in Infants.” J Pediatr 175 (August 2016): 67. https://doi.org/10.1016/j.jpeds.2016.01.059.Full Text Link to Item
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Buckley, Rebecca H. “Progress toward less toxic conditioning.” Blood 128, no. 3 (July 21, 2016): 322–23. https://doi.org/10.1182/blood-2016-06-719922.Full Text Open Access Copy Link to Item
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Petrovski, Slavé, Roberta E. Parrott, Joseph L. Roberts, Hongxiang Huang, Jialong Yang, Balachandra Gorentla, Talal Mousallem, et al. “Dominant Splice Site Mutations in PIK3R1 Cause Hyper IgM Syndrome, Lymphadenopathy and Short Stature.” J Clin Immunol 36, no. 5 (July 2016): 462–71. https://doi.org/10.1007/s10875-016-0281-6.Full Text Open Access Copy Link to Item
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Al-Herz, Waleed, Luigi D. Notarangelo, Ali Sadek, Rebecca Buckley, and Rebecca USIDNET Consortium. “Combined immunodeficiency in the United States and Kuwait: Comparison of patients' characteristics and molecular diagnosis.” Clin Immunol 161, no. 2 (December 2015): 170–73. https://doi.org/10.1016/j.clim.2015.07.013.Full Text Link to Item
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Allewelt, Heather, Paul L. Martin, Paul Szabolcs, Nelson Chao, Rebecca Buckley, and Suhag Parikh. “Hematopoietic Stem Cell Transplantation for CD40 Ligand Deficiency: Single Institution Experience.” Pediatr Blood Cancer 62, no. 12 (December 2015): 2216–22. https://doi.org/10.1002/pbc.25711.Full Text Link to Item
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Mousallem, Talal, Thomas J. Urban, K Melodi McSweeney, Sarah E. Kleinstein, Mingfu Zhu, Mehdi Adeli, Roberta E. Parrott, et al. “Clinical application of whole-genome sequencing in patients with primary immunodeficiency.” J Allergy Clin Immunol 136, no. 2 (August 2015): 476-9.e6. https://doi.org/10.1016/j.jaci.2015.02.040.Full Text Link to Item
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Dobbs, Kerry, Cecilia Domínguez Conde, Shen-Ying Zhang, Silvia Parolini, Magali Audry, Janet Chou, Emma Haapaniemi, et al. “Inherited DOCK2 Deficiency in Patients with Early-Onset Invasive Infections.” N Engl J Med 372, no. 25 (June 18, 2015): 2409–22. https://doi.org/10.1056/NEJMoa1413462.Full Text Link to Item
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Buckley, R. H., and K. Dobbs. “Human DOCK2 mutations underlie an autosomal recessive pleiotropic immunodeficiency with early-onset invasive infections.” The New England Journal of Medicine 372, no. 25 (June 17, 2015): 2409–22.Open Access Copy
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Szabolcs, Paul, Rebecca H. Buckley, Robert Duane Davis, Jerelyn Moffet, Judith Voynow, Jeyaraj Antony, Xiaohua Chen, Gregory D. Sempowski, and David W. Zaas. “Tolerance and immunity after sequential lung and bone marrow transplantation from an unrelated cadaveric donor.” J Allergy Clin Immunol 135, no. 2 (February 2015): 567–70. https://doi.org/10.1016/j.jaci.2014.07.058.Full Text Link to Item
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McWilliams, Laurie M., Mary Dell Railey, and Rebecca H. Buckley. “Positive Family History, Infection, Low Absolute Lymphocyte Count (ALC), and Absent Thymic Shadow: Diagnostic Clues for All Molecular Forms of Severe Combined Immunodeficiency (SCID).” J Allergy Clin Immunol Pract 3, no. 4 (2015): 585–91. https://doi.org/10.1016/j.jaip.2015.01.026.Full Text Link to Item
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Smith, Lauren L., Benjamin L. Wright, and Rebecca H. Buckley. “Successful treatment of disseminated BCG in a patient with severe combined immunodeficiency.” J Allergy Clin Immunol Pract 3, no. 3 (2015): 438–40. https://doi.org/10.1016/j.jaip.2014.12.004.Full Text Link to Item
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Buckley, Rebecca H. “American Pediatric Society's 2014 John Howland Award acceptance lecture: saving lives through early diagnosis.” Pediatr Res 76, no. 5 (November 2014): 491–94. https://doi.org/10.1038/pr.2014.123.Full Text Link to Item
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Dvorak, Christopher C., Amel Hassan, Mary A. Slatter, Manfred Hönig, Arjan C. Lankester, Rebecca H. Buckley, Michael A. Pulsipher, et al. “Comparison of outcomes of hematopoietic stem cell transplantation without chemotherapy conditioning by using matched sibling and unrelated donors for treatment of severe combined immunodeficiency.” J Allergy Clin Immunol 134, no. 4 (October 2014): 935-943.e15. https://doi.org/10.1016/j.jaci.2014.06.021.Full Text Link to Item
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Mousallem, Talal, Jialong Yang, Thomas J. Urban, Hongxia Wang, Mehdi Adeli, Roberta E. Parrott, Joseph L. Roberts, David B. Goldstein, Rebecca H. Buckley, and Xiao-Ping Zhong. “A nonsense mutation in IKBKB causes combined immunodeficiency.” Blood 124, no. 13 (September 25, 2014): 2046–50. https://doi.org/10.1182/blood-2014-04-571265.Full Text Link to Item
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Pai, Sung-Yun, Brent R. Logan, Linda M. Griffith, Rebecca H. Buckley, Roberta E. Parrott, Christopher C. Dvorak, Neena Kapoor, et al. “Transplantation outcomes for severe combined immunodeficiency, 2000-2009.” N Engl J Med 371, no. 5 (July 31, 2014): 434–46. https://doi.org/10.1056/NEJMoa1401177.Full Text Link to Item
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Wilson, Michael R., Samia N. Naccache, Erik Samayoa, Mark Biagtan, Hiba Bashir, Guixia Yu, Shahriar M. Salamat, et al. “Actionable diagnosis of neuroleptospirosis by next-generation sequencing.” N Engl J Med 370, no. 25 (June 19, 2014): 2408–17. https://doi.org/10.1056/NEJMoa1401268.Full Text Link to Item
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Medical Advisory Committee of the Immune Deficiency Foundation, Jerry, William T. Shearer, Thomas A. Fleisher, Rebecca H. Buckley, Zuhair Ballas, Mark Ballow, R Michael Blaese, et al. “Recommendations for live viral and bacterial vaccines in immunodeficient patients and their close contacts.” J Allergy Clin Immunol 133, no. 4 (April 2014): 961–66. https://doi.org/10.1016/j.jaci.2013.11.043.Full Text Link to Item
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Shearer, William T., Elizabeth Dunn, Luigi D. Notarangelo, Christopher C. Dvorak, Jennifer M. Puck, Brent R. Logan, Linda M. Griffith, et al. “Establishing diagnostic criteria for severe combined immunodeficiency disease (SCID), leaky SCID, and Omenn syndrome: the Primary Immune Deficiency Treatment Consortium experience.” J Allergy Clin Immunol 133, no. 4 (April 2014): 1092–98. https://doi.org/10.1016/j.jaci.2013.09.044.Full Text Link to Item
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Griffith, Linda M., Morton J. Cowan, Luigi D. Notarangelo, Donald B. Kohn, Jennifer M. Puck, Sung-Yun Pai, Barbara Ballard, et al. “Primary Immune Deficiency Treatment Consortium (PIDTC) report.” J Allergy Clin Immunol 133, no. 2 (February 2014): 335–47. https://doi.org/10.1016/j.jaci.2013.07.052.Full Text Link to Item
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Smith, Lauren L., Rebecca Buckley, and Patricia Lugar. “Diagnostic Immunization with Bacteriophage ΦX 174 in Patients with Common Variable Immunodeficiency/Hypogammaglobulinemia.” Front Immunol 5 (2014): 410. https://doi.org/10.3389/fimmu.2014.00410.Full Text Link to Item
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Dvorak, Christopher C., Morton J. Cowan, Brent R. Logan, Luigi D. Notarangelo, Linda M. Griffith, Jennifer M. Puck, Donald B. Kohn, et al. “The natural history of children with severe combined immunodeficiency: baseline features of the first fifty patients of the primary immune deficiency treatment consortium prospective study 6901.” J Clin Immunol 33, no. 7 (October 2013): 1156–64. https://doi.org/10.1007/s10875-013-9917-y.Full Text Link to Item
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Teigland, C. L., R. E. Parrott, and R. H. Buckley. “Long-term outcome of non-ablative booster BMT in patients with SCID.” Bone Marrow Transplant 48, no. 8 (August 2013): 1050–55. https://doi.org/10.1038/bmt.2013.6.Full Text Open Access Copy Link to Item
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Haddad, Elie, Sandrine Leroy, and Rebecca H. Buckley. “B-cell reconstitution for SCID: should a conditioning regimen be used in SCID treatment?” J Allergy Clin Immunol 131, no. 4 (April 2013): 994–1000. https://doi.org/10.1016/j.jaci.2013.01.047.Full Text Link to Item
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Markert, M Louise, Stephanie E. Gupton, Elizabeth A. McCarthy, Blythe H. Devlin, Chia-san Hsieh, Jie Li, Troy R. Torgerson, Hans D. Ochs, and Rebecca H. Buckley. “RESPONSE TO BACTERIOPHAGE Phi chi 174 IN CHILDREN WITH PARTIAL DIGEORGE ANOMALY AND IN CHILDREN WITH COMPLETE DIGEORGE ANOMALY AFTER CULTURED POSTNATAL ALLOGENEIC THYMUS TRANSPLANTATION.” Journal of Clinical Immunology 33, no. 3 (April 1, 2013): 679–80.Link to Item
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Teigland, C. L., R. E. Parrott, and R. H. Buckley. “Long-term outcome of non-ablative booster BMT in patients with SCID.” Bone Marrow Transplantation 48, no. 8 (2013): 1050–55. https://doi.org/10.1038/bmt.2013.6.Full Text
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Buckley, Rebecca H., Chan M. Win, Barry K. Moser, Roberta E. Parrott, Elisa Sajaroff, and Marcella Sarzotti-Kelsoe. “Post-transplantation B cell function in different molecular types of SCID.” J Clin Immunol 33, no. 1 (January 2013): 96–110. https://doi.org/10.1007/s10875-012-9797-6.Full Text Open Access Copy Link to Item
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Heimall, Jennifer, Michael Keller, Rushani Saltzman, Nancy Bunin, Donna McDonald-McGinn, Elaine Zakai, Jean-Pierre de Villartay, et al. “Diagnosis of 22q11.2 deletion syndrome and artemis deficiency in two children with T-B-NK+ immunodeficiency.” J Clin Immunol 32, no. 5 (October 2012): 1141–44. https://doi.org/10.1007/s10875-012-9741-9.Full Text Link to Item
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Roberts, Joseph L., Rebecca H. Buckley, Biao Luo, Jianming Pei, Alla Lapidus, Suraj Peri, Qiong Wei, et al. “CD45-deficient severe combined immunodeficiency caused by uniparental disomy.” Proc Natl Acad Sci U S A 109, no. 26 (June 26, 2012): 10456–61. https://doi.org/10.1073/pnas.1202249109.Full Text Link to Item
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Palendira, Umaimainthan, Carol Low, Andrew I. Bell, Cindy S. Ma, Rachel J. M. Abbott, Tri Giang Phan, D Sean Riminton, et al. “Expansion of somatically reverted memory CD8+ T cells in patients with X-linked lymphoproliferative disease caused by selective pressure from Epstein-Barr virus.” J Exp Med 209, no. 5 (May 7, 2012): 913–24. https://doi.org/10.1084/jem.20112391.Full Text Link to Item
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Buckley, Rebecca H. “The long quest for neonatal screening for severe combined immunodeficiency.” J Allergy Clin Immunol 129, no. 3 (March 2012): 597–604. https://doi.org/10.1016/j.jaci.2011.12.964.Full Text Link to Item
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Buckley, R. H., C. M. Win, B. K. Moser, R. E. Parrott, E. Sajaroff, and M. Sarzotti-Kelsoe. “Post-Transplantation B Cell Function in Different Molecular Types of SCID.” Journal of Clinical Immunology, 2012, 1–15.
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Sokolic, Robert, Irina Maric, Chimene Kesserwan, Elizabeth Garabedian, I Celine Hanson, Margaret Dodds, Rebecca Buckley, et al. “Myeloid dysplasia and bone marrow hypocellularity in adenosine deaminase-deficient severe combined immune deficiency.” Blood 118, no. 10 (September 8, 2011): 2688–94. https://doi.org/10.1182/blood-2011-01-329359.Full Text Link to Item
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Buckley, Rebecca H. “Transplantation of hematopoietic stem cells in human severe combined immunodeficiency: longterm outcomes.” Immunol Res 49, no. 1–3 (April 2011): 25–43. https://doi.org/10.1007/s12026-010-8191-9.Full Text Link to Item
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Sarzotti-Kelsoe, Marcella, Xiaoju G. Daniell, John F. Whitesides, and Rebecca H. Buckley. “The long and the short of telomeres in bone marrow recipient SCID patients.” Immunol Res 49, no. 1–3 (April 2011): 44–48. https://doi.org/10.1007/s12026-010-8192-8.Full Text Link to Item
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Adeli, Mehdi M., and Rebecca H. Buckley. “Why newborn screening for severe combined immunodeficiency is essential: a case report.” Pediatrics 126, no. 2 (August 2010): e465–69. https://doi.org/10.1542/peds.2009-3659.Full Text Link to Item
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Buckley, Rebecca H. “B-cell function in severe combined immunodeficiency after stem cell or gene therapy: a review.” J Allergy Clin Immunol 125, no. 4 (April 2010): 790–97. https://doi.org/10.1016/j.jaci.2010.02.012.Full Text Link to Item
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Millington, David S., Ramakrishna Sista, Allen Eckhardt, Jeremy Rouse, Deeksha Bali, Ronald Goldberg, Michael Cotten, Rebecca Buckley, and Vamsee Pamula. “Digital microfluidics: a future technology in the newborn screening laboratory?” Semin Perinatol 34, no. 2 (April 2010): 163–69. https://doi.org/10.1053/j.semperi.2009.12.008.Full Text Link to Item
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Chinen, Javier, and Rebecca H. Buckley. “Transplantation immunology: solid organ and bone marrow.” J Allergy Clin Immunol 125, no. 2 Suppl 2 (February 2010): S324–35. https://doi.org/10.1016/j.jaci.2009.11.014.Full Text Link to Item
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Griffith, Linda M., Morton J. Cowan, Luigi D. Notarangelo, Jennifer M. Puck, Rebecca H. Buckley, Fabio Candotti, Mary Ellen Conley, et al. “Improving cellular therapy for primary immune deficiency diseases: recognition, diagnosis, and management.” J Allergy Clin Immunol 124, no. 6 (December 2009): 1152-60.e12. https://doi.org/10.1016/j.jaci.2009.10.022.Full Text Link to Item
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Railey, Mary Dell, Yuliya Lokhnygina, and Rebecca H. Buckley. “Long-term clinical outcome of patients with severe combined immunodeficiency who received related donor bone marrow transplants without pretransplant chemotherapy or post-transplant GVHD prophylaxis.” J Pediatr 155, no. 6 (December 2009): 834-840.e1. https://doi.org/10.1016/j.jpeds.2009.07.049.Full Text Link to Item
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Sarzotti-Kelsoe, Marcella, Chan M. Win, Roberta E. Parrott, Myriah Cooney, Barry K. Moser, Joseph L. Roberts, Gregory D. Sempowski, and Rebecca H. Buckley. “Thymic output, T-cell diversity, and T-cell function in long-term human SCID chimeras.” Blood 114, no. 7 (August 13, 2009): 1445–53. https://doi.org/10.1182/blood-2009-01-199323.Full Text Link to Item
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Buckley, R. H., and J. B. Sidbury. “On Assessing Immunocompetence.” Journal of Allergy and Clinical Immunology 123, no. 2 SUPPL. (February 1, 2009). https://doi.org/10.1016/j.jaci.2008.11.028.Full Text
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Aiuti, Alessandro, Federica Cattaneo, Stefania Galimberti, Ulrike Benninghoff, Barbara Cassani, Luciano Callegaro, Samantha Scaramuzza, et al. “Gene therapy for immunodeficiency due to adenosine deaminase deficiency.” N Engl J Med 360, no. 5 (January 29, 2009): 447–58. https://doi.org/10.1056/NEJMoa0805817.Full Text Link to Item
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Griffith, Linda M., Morton J. Cowan, Donald B. Kohn, Luigi D. Notarangelo, Jennifer M. Puck, Kirk R. Schultz, Rebecca H. Buckley, et al. “Allogeneic hematopoietic cell transplantation for primary immune deficiency diseases: current status and critical needs.” J Allergy Clin Immunol 122, no. 6 (December 2008): 1087–96. https://doi.org/10.1016/j.jaci.2008.09.045.Full Text Link to Item
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Adeli, M., and R. H. Buckley. “Why newborn screening for severe combined immunodeficiency is essential: a case report.” Clinical and Experimental Immunology 154 (November 1, 2008): 59–59.Link to Item
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Boyle, J. M., and R. H. Buckley. “Population prevalence of diagnosed primary immunodeficiency diseases in the United States.” Pharmaceuticals Policy and Law 10 (January 1, 2008): 99–108.
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Keller, M. D., D. F. Chen, S. A. Condron, N. Liu, N. L. Reinsmoen, and R. H. Buckley. “The Effect of Natural Killer Cell Killer Ig-Like Receptor Alloreactivity on the Outcome of Bone Marrow Stem Cell Transplantation for Severe Combined Immunodeficiency (SCID).” Journal of Clinical Immunology 27, no. 6 (November 12, 2007): 659–659. https://doi.org/10.1007/s10875-007-9116-9.Full Text
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Boyle, J. M., and R. H. Buckley. “Population prevalence of diagnosed primary immunodeficiency diseases in the United States.” J Clin Immunol 27, no. 5 (September 2007): 497–502. https://doi.org/10.1007/s10875-007-9103-1.Full Text Link to Item
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Palmer, Kricia, Todd D. Green, Joseph L. Roberts, Elisa Sajaroff, Myriah Cooney, Roberta Parrott, Dong-Feng Chen, Nancy L. Reinsmoen, and Rebecca H. Buckley. “Unusual clinical and immunologic manifestations of transplacentally acquired maternal T cells in severe combined immunodeficiency.” J Allergy Clin Immunol 120, no. 2 (August 2007): 423–28. https://doi.org/10.1016/j.jaci.2007.02.047.Full Text Link to Item
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Booth, Claire, Mike Hershfield, Luigi Notarangelo, Rebecca Buckley, Manfred Hoenig, Nizar Mahlaoui, Marina Cavazzana-Calvo, Alessandro Aiuti, and H Bobby Gaspar. “Management options for adenosine deaminase deficiency; proceedings of the EBMT satellite workshop (Hamburg, March 2006).” Clin Immunol 123, no. 2 (May 2007): 139–47. https://doi.org/10.1016/j.clim.2006.12.009.Full Text Link to Item
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Roberts, Joseph L., Jens Peter H. Lauritsen, Myriah Cooney, Roberta E. Parrott, Elisa O. Sajaroff, Chan M. Win, Michael D. Keller, et al. “T-B+NK+ severe combined immunodeficiency caused by complete deficiency of the CD3zeta subunit of the T-cell antigen receptor complex.” Blood 109, no. 8 (April 15, 2007): 3198–3206. https://doi.org/10.1182/blood-2006-08-043166.Full Text Link to Item
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Atluri, Srilatha, Kathleen Neville, Mary Davis, Kent A. Robertson, Francis E. Marshalleck, Dennis P. O’Malley, Rebecca H. Buckley, and Robert P. Nelson. “Epstein-Barr-associated leiomyomatosis and T-cell chimerism after haploidentical bone marrow transplantation for severe combined immunodeficiency disease.” J Pediatr Hematol Oncol 29, no. 3 (March 2007): 166–72. https://doi.org/10.1097/MPH.0b013e31803b95b3.Full Text Link to Item
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Keller, M. D., D. F. Chen, S. A. Condron, N. Liu, N. L. Reinsmoen, and R. H. Buckley. “The effect of natural killer cell killer Ig-like receptor alloreactivity on the outcome of bone marrow stem cell transplantation for severe combined immunodeficiency (SCID).” J Clin Immunol 27, no. 1 (January 2007): 109–16. https://doi.org/10.1007/s10875-006-9058-7.Full Text Link to Item
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Buckley, Rebecca H. “Primary immunodeficiency or not? Making the correct diagnosis.” J Allergy Clin Immunol 117, no. 4 (April 2006): 756–58. https://doi.org/10.1016/j.jaci.2006.01.008.Full Text Link to Item
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Orange, Jordan S., Elham M. Hossny, Catherine R. Weiler, Mark Ballow, Melvin Berger, Francisco A. Bonilla, Rebecca Buckley, et al. “Use of intravenous immunoglobulin in human disease: a review of evidence by members of the Primary Immunodeficiency Committee of the American Academy of Allergy, Asthma and Immunology.” J Allergy Clin Immunol 117, no. 4 Suppl (April 2006): S525–53. https://doi.org/10.1016/j.jaci.2006.01.015.Full Text Link to Item
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Buckley, Rebecca H. “Variable phenotypic expression of mutations in genes of the immune system.” J Clin Invest 115, no. 11 (November 2005): 2974–76. https://doi.org/10.1172/JCI26956.Full Text Link to Item
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Buckley, Rebecca H. “The multiple causes of human SCID.” J Clin Invest 114, no. 10 (November 2004): 1409–11. https://doi.org/10.1172/JCI23571.Full Text Link to Item
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Rosenzweig, Sergio D., Susan E. Dorman, Gulbu Uzel, Stephen Shaw, Amy Scurlock, Margaret R. Brown, Rebecca H. Buckley, and Steven M. Holland. “A novel mutation in IFN-gamma receptor 2 with dominant negative activity: biological consequences of homozygous and heterozygous states.” J Immunol 173, no. 6 (September 15, 2004): 4000–4008. https://doi.org/10.4049/jimmunol.173.6.4000.Full Text Link to Item
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O’Shea, John J., Matthew Husa, Denise Li, Sigrun R. Hofmann, Wendy Watford, Joseph L. Roberts, Rebecca H. Buckley, Paul Changelian, and Fabio Candotti. “Jak3 and the pathogenesis of severe combined immunodeficiency.” Mol Immunol 41, no. 6–7 (July 2004): 727–37. https://doi.org/10.1016/j.molimm.2004.04.014.Full Text Link to Item
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Buckley, Rebecca H. “A historical review of bone marrow transplantation for immunodeficiencies.” J Allergy Clin Immunol 113, no. 4 (April 2004): 793–800. https://doi.org/10.1016/j.jaci.2004.01.764.Full Text Link to Item
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Markert, M Louise, Marilyn J. Alexieff, Jie Li, Marcella Sarzotti, Daniel A. Ozaki, Blythe H. Devlin, Gregory D. Sempowski, et al. “Complete DiGeorge syndrome: development of rash, lymphadenopathy, and oligoclonal T cells in 5 cases.” J Allergy Clin Immunol 113, no. 4 (April 2004): 734–41. https://doi.org/10.1016/j.jaci.2004.01.766.Full Text Link to Item
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Roberts, Joseph L., Andrea Lengi, Stephanie M. Brown, Min Chen, Yong-Jie Zhou, John J. O’Shea, and Rebecca H. Buckley. “Janus kinase 3 (JAK3) deficiency: clinical, immunologic, and molecular analyses of 10 patients and outcomes of stem cell transplantation.” Blood 103, no. 6 (March 15, 2004): 2009–18. https://doi.org/10.1182/blood-2003-06-2104.Full Text Link to Item
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Buckley, Rebecca H. “Molecular defects in human severe combined immunodeficiency and approaches to immune reconstitution.” Annu Rev Immunol 22 (2004): 625–55. https://doi.org/10.1146/annurev.immunol.22.012703.104614.Full Text Link to Item
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Buckley, Rebecca H. “Pulmonary complications of primary immunodeficiencies.” Paediatr Respir Rev 5 Suppl A (2004): S225–33. https://doi.org/10.1016/s1526-0542(04)90043-7.Full Text Link to Item
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Hale, Laura P., Rebecca H. Buckley, Jennifer M. Puck, and Dhavalkumar D. Patel. “Abnormal development of thymic dendritic and epithelial cells in human X-linked severe combined immunodeficiency.” Clin Immunol 110, no. 1 (January 2004): 63–70. https://doi.org/10.1016/j.clim.2003.09.002.Full Text Link to Item
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Kalman, Lisa, Mary Lou Lindegren, Lisa Kobrynski, Robert Vogt, Harry Hannon, Joelyn Tonkin Howard, and Rebecca Buckley. “Mutations in genes required for T-cell development: IL7R, CD45, IL2RG, JAK3, RAG1, RAG2, ARTEMIS, and ADA and severe combined immunodeficiency: HuGE review.” Genet Med 6, no. 1 (2004): 16–26. https://doi.org/10.1097/01.GIM.0000105752.80592.A3.Full Text Link to Item
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Roifman, Chaim M., Harry Schroeder, Melvin Berger, Ricardo Sorensen, Mark Ballow, Rebecca H. Buckley, Anita Gewurz, Phillip Korenblat, Gordon Sussman, and Georg Lemm. “Comparison of the efficacy of IGIV-C, 10% (caprylate/chromatography) and IGIV-SD, 10% as replacement therapy in primary immune deficiency. A randomized double-blind trial.” Int Immunopharmacol 3, no. 9 (September 2003): 1325–33. https://doi.org/10.1016/s1567-5769(03)00134-6.Full Text Link to Item
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Ballow, M., M. Berger, F. A. Bonilla, R. H. Buckley, C. H. Cunningham-Rundles, P. Fireman, M. Kaliner, et al. “Pharmacokinetics and tolerability of a new intravenous immunoglobulin preparation, IGIV-C, 10% (Gamunex, 10%).” Vox Sang 84, no. 3 (April 2003): 202–10. https://doi.org/10.1046/j.1423-0410.2003.00286.x.Full Text Link to Item
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Sarzotti, Marcella, Dhavalkumar D. Patel, Xiaojing Li, Daniel A. Ozaki, Shui Cao, Scott Langdon, Roberta E. Parrott, Katherine Coyne, and Rebecca H. Buckley. “T cell repertoire development in humans with SCID after nonablative allogeneic marrow transplantation.” J Immunol 170, no. 5 (March 1, 2003): 2711–18. https://doi.org/10.4049/jimmunol.170.5.2711.Full Text Link to Item
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Buckley, Rebecca H. “Treatment options for genetically determined immunodeficiency.” Lancet 361, no. 9357 (February 15, 2003): 541–42. https://doi.org/10.1016/S0140-6736(03)12562-7.Full Text Link to Item
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Buckley, Rebecca H. “27. Transplantation immunology: organ and bone marrow.” J Allergy Clin Immunol 111, no. 2 Suppl (February 2003): S733–44. https://doi.org/10.1067/mai.2003.142.Full Text Link to Item
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Buckley, Rebecca H. “Gene therapy for SCID--a complication after remarkable progress.” Lancet 360, no. 9341 (October 19, 2002): 1185–86. https://doi.org/10.1016/S0140-6736(02)11290-6.Full Text Link to Item
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Buckley, Rebecca H. “Immunoglobulin G subclass deficiency: fact or fancy?” Curr Allergy Asthma Rep 2, no. 5 (September 2002): 356–60. https://doi.org/10.1007/s11882-002-0067-1.Full Text Link to Item
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Buckley, Rebecca H. “Primary immunodeficiency diseases: dissectors of the immune system.” Immunol Rev 185 (July 2002): 206–19. https://doi.org/10.1034/j.1600-065x.2002.18517.x.Full Text Link to Item
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Buckley, Rebecca H. “Primary cellular immunodeficiencies.” J Allergy Clin Immunol 109, no. 5 (May 2002): 747–57. https://doi.org/10.1067/mai.2002.123617.Full Text Link to Item
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Puck, J. M., B. N. Hay, A. P. Hsu, R. Fischer, E. Tsai, G. Uzel, R. H. Buckley, and H. L. Malech. “Patients with atypical X-linked severe combined immunodeficiency (XSCID) may benefit from hematopoietic stem cell gene therapy.” Blood Cells Molecules and Diseases 28, no. 3 (May 1, 2002): 343–343.Link to Item
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Sarzotti, M., D. D. Patel, X. Li, S. Cao, D. Ozaki, S. Langdon, R. E. Parrott, K. Coyne, and R. H. Buckley. “T cell repertoire diversity after hematopoietic stem cell transplantation in SCID patients.” Faseb Journal 16, no. 5 (March 22, 2002): A1030–A1030.Link to Item
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Myers, Laurie A., Dhavalkumar D. Patel, Jennifer M. Puck, and Rebecca H. Buckley. “Hematopoietic stem cell transplantation for severe combined immunodeficiency in the neonatal period leads to superior thymic output and improved survival.” Blood 99, no. 3 (February 1, 2002): 872–78. https://doi.org/10.1182/blood.v99.3.872.Full Text Link to Item
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Buckley, Rebecca H. “American Pediatric Society Presidential Address 2000: reflections on the 20th and 21st centuries.” Pediatr Res 51, no. 1 (January 2002): 119–23. https://doi.org/10.1203/00006450-200201000-00021.Full Text Link to Item
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Mustillo, Peter John, Katharine E. Coyne, Joseph Roberts, Kim Nichols, and Rebecca H. Buckley. “Prevalence of X-linked lymphoproliferative (XLP) disease mutation among male patients with CVID.” Journal of Allergy and Clinical Immunology 109, no. 1 (January 2002): S276–S276. https://doi.org/10.1016/s0091-6749(02)81977-7.Full Text
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Piltch, R. G., R. Parrott, and Rebecca H. Buckley. “Natural killer (NK) cell ontogeny in severe combined immunodeficiency (SCID) after bone marrow transplantation (BMT).” Journal of Allergy and Clinical Immunology 109, no. 1 (January 2002): S277–S277. https://doi.org/10.1016/s0091-6749(02)81980-7.Full Text
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Shaw, Stephen Gerard, Rebecca H. Buckley, and Joseph Roberts. “Distinctive clinical and laboratory features of autosomal-recessive hyper IgM syndrome.” Journal of Allergy and Clinical Immunology 109, no. 1 (January 2002): S254–S254. https://doi.org/10.1016/s0091-6749(02)81911-x.Full Text
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Zhou, Y. J., M. Chen, N. A. Cusack, L. H. Kimmel, K. S. Magnuson, J. G. Boyd, W. Lin, et al. “Unexpected effects of FERM domain mutations on catalytic activity of Jak3: structural implication for Janus kinases.” Mol Cell 8, no. 5 (November 2001): 959–69. https://doi.org/10.1016/s1097-2765(01)00398-7.Full Text Link to Item
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Morra, M., O. Silander, S. Calpe, M. Choi, H. Oettgen, L. Myers, A. Etzioni, R. Buckley, and C. Terhorst. “Alterations of the X-linked lymphoproliferative disease gene SH2D1A in common variable immunodeficiency syndrome.” Blood 98, no. 5 (September 1, 2001): 1321–25. https://doi.org/10.1182/blood.v98.5.1321.Full Text Link to Item
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Yin, E. Z., D. P. Frush, L. F. Donnelly, and R. H. Buckley. “Primary immunodeficiency disorders in pediatric patients: clinical features and imaging findings.” Ajr Am J Roentgenol 176, no. 6 (June 2001): 1541–52. https://doi.org/10.2214/ajr.176.6.1761541.Full Text Link to Item
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Ballow, M., M. Berger, F. A. Bonilla, R. H. Buckley, C. Cunningham-Rundles, P. Fireman, M. Kaliner, et al. “Pharmacokinetics of a novel, intravenous immunoglobulin preparation.” Journal of Allergy and Clinical Immunology 107, no. 2 (February 1, 2001): S208–S208.Link to Item
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Buckley, R. H. “The hyper-IgE syndrome.” Clin Rev Allergy Immunol 20, no. 1 (February 2001): 139–54. https://doi.org/10.1385/CRIAI:20:1:139.Full Text Link to Item
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Buckley, R. H., and R. E. Parrott. “CD27+memory B cells in human severe combined immunodeficiency (SCID).” Journal of Allergy and Clinical Immunology 107, no. 2 (February 1, 2001): S137–S137.Link to Item
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Koleilat, M. A., R. H. Buckley, and M. Loubser. “Adenosine deaminase (ADA) deficiency, multiple phenotypes.” Journal of Allergy and Clinical Immunology 107, no. 2 (February 1, 2001): S202–S202.Link to Item
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Shaw, S. G., A. Ahmed, W. R. Treem, and R. H. Buckley. “Intestinal lymphangiectasia masquerading as severe combined immunodeficiency (SCID).” Journal of Allergy and Clinical Immunology 107, no. 2 (February 1, 2001): S201–S201.Link to Item
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Antaya, R. J., E. S. Gardner, M. S. Bettencourt, M. Daines, Y. Denise, S. Uthaisangsook, R. H. Buckley, and N. S. Prose. “Cutaneous complications of BCG vaccination in infants with immune disorders: two cases and a review of the literature.” Pediatr Dermatol 18, no. 3 (2001): 205–9. https://doi.org/10.1046/j.1525-1470.2001.018003205.x.Full Text Link to Item
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Minegishi, Y., A. Lavoie, C. Cunningham-Rundles, P. M. Bédard, J. Hébert, L. Côté, K. Dan, et al. “Mutations in activation-induced cytidine deaminase in patients with hyper IgM syndrome.” Clin Immunol 97, no. 3 (December 2000): 203–10. https://doi.org/10.1006/clim.2000.4956.Full Text Link to Item
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Buckley, R. H. “Primary immunodeficiency diseases due to defects in lymphocytes.” N Engl J Med 343, no. 18 (November 2, 2000): 1313–24. https://doi.org/10.1056/NEJM200011023431806.Full Text Link to Item
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Hsu, A. P., E. J. Tsai, S. M. Anderson, R. E. Fischer, H. Malech, R. H. Buckley, and J. M. Puck. “Unusual X-linked SCID phenotype due to mutation of the poly-A addition signal of IL2RG.” American Journal of Human Genetics 67, no. 4 (October 1, 2000): 50–50.Link to Item
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Buckley, R. H. “Gene therapy for human SCID: dreams become reality.” Nat Med 6, no. 6 (June 2000): 623–24. https://doi.org/10.1038/76185.Full Text Link to Item
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Patel, D. D., M. E. Gooding, R. E. Parrott, K. M. Curtis, B. F. Haynes, and R. H. Buckley. “Thymic function after hematopoietic stem-cell transplantation for the treatment of severe combined immunodeficiency.” N Engl J Med 342, no. 18 (May 4, 2000): 1325–32. https://doi.org/10.1056/NEJM200005043421804.Full Text Link to Item
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U.S. National Institutes of Health. Recombinant DNA Advisory Committee, Thomas A. “Prenatal gene tranfer: scientific, medical, and ethical issues: a report of the Recombinant DNA Advisory Committee.” Hum Gene Ther 11, no. 8 (May 1, 2000): 1211–29. https://doi.org/10.1089/10430340050015257.Full Text Link to Item
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Winkelstein, J. A., M. C. Marino, R. B. Johnston, J. Boyle, J. Curnutte, J. I. Gallin, H. L. Malech, et al. “Chronic granulomatous disease. Report on a national registry of 368 patients.” Medicine (Baltimore) 79, no. 3 (May 2000): 155–69. https://doi.org/10.1097/00005792-200005000-00003.Full Text Link to Item
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Shaw, S. G., S. E. Dorman, G. Uzel, S. M. Holland, and R. H. Buckley. “Correction of complete IFNGR2 deficiency with transplantation of bone marrow from a parent.” Faseb Journal 14, no. 6 (April 20, 2000): A933–A933.Link to Item
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Buckley, R. H. “Advances in the understanding and treatment of human severe combined immunodeficiency.” Immunol Res 22, no. 2–3 (2000): 237–51. https://doi.org/10.1385/IR:22:2-3:237.Full Text Link to Item
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Lowe, D., E. Livingston, D. Penning, and R. H. Buckley. “Successful and rapid immune reconstitution using a pregnant donor for T-Cell depleted haploidentical bone marrow transplantation for a patient with severe combined immunodeficiency.” Journal of Allergy and Clinical Immunology 105, no. 1 (2000): S266–S266. https://doi.org/10.1016/s0091-6749(00)91215-6.Full Text
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PATEL, D. “784 Thymic output after non-ablative allogeneic hematopoietic stem cell transplantation in infants with severe combined immunodeficiency (SCID).” Journal of Allergy and Clinical Immunology 105, no. 1 (January 2000): S264–65. https://doi.org/10.1016/s0091-6749(00)91212-0.Full Text
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SHAW, S. “788 Haploidentical T cell-depleted bone marrow transplantation into a premature infant with X-linked severe combined immunodeficiency (X-SCID).” Journal of Allergy and Clinical Immunology 105, no. 1 (January 2000): S266–S266. https://doi.org/10.1016/s0091-6749(00)91216-8.Full Text
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Markert, M. L., A. Boeck, L. P. Hale, A. L. Kloster, T. M. McLaughlin, M. N. Batchvarova, D. C. Douek, et al. “Transplantation of thymus tissue in complete DiGeorge syndrome.” N Engl J Med 341, no. 16 (October 14, 1999): 1180–89. https://doi.org/10.1056/NEJM199910143411603.Full Text Link to Item
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Buckley, R. H. “Cellular therapy for severe combined immunodeficiency: Transplant options and impact of donor type and graft manipulation on long-term graft function and completeness of immune reconstitution.” Cancer Research Therapy and Control 9, no. 1–2 (September 7, 1999): 73–79.
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Grimbacher, B., A. A. Schäffer, S. M. Holland, J. Davis, J. I. Gallin, H. L. Malech, T. P. Atkinson, et al. “Genetic linkage of hyper-IgE syndrome to chromosome 4.” Am J Hum Genet 65, no. 3 (September 1999): 735–44. https://doi.org/10.1086/302547.Full Text Link to Item
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Flake, A. W., and E. D. Zanjani. “Treatment of severe combined immunodeficiency.” N Engl J Med 341, no. 4 (July 22, 1999): 291–92. https://doi.org/10.1056/NEJM199907223410416.Full Text Link to Item
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Daines, M. O., J. L. Roberts, and R. H. Buckley. “Deficiency of nuclear factor of activated T cells 1(NFAT1) in combined immunodeficiencies.” Faseb Journal 13, no. 4 (March 12, 1999): A642–A642.Link to Item
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Buckley, R. H., S. E. Schiff, R. I. Schiff, L. Markert, L. W. Williams, J. L. Roberts, L. A. Myers, and F. E. Ward. “Hematopoietic stem-cell transplantation for the treatment of severe combined immunodeficiency.” N Engl J Med 340, no. 7 (February 18, 1999): 508–16. https://doi.org/10.1056/NEJM199902183400703.Full Text Link to Item
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Daines, M. O., J. L. Roberts, and R. H. Buckley. “Deficiency of nuclear factor of activated T cells 1 (NFAT1) in combined immunodeficiencies.” Journal of Allergy and Clinical Immunology 103, no. 1 (January 1, 1999): S118–S118.Link to Item
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Riester, D. E., L. A. Myers, and R. H. Buckley. “Successful HLA-identical bone marrow transplantation in combined immunodeficiency without pre-transplant chemoablation or GVHD prophylaxis.” Journal of Allergy and Clinical Immunology 103, no. 1 (January 1, 1999): S118–S118.Link to Item
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Uthaisangsook, S., and R. H. Buckley. “Clinical and immunologic spectrum of the hyper IgM syndrome.” Journal of Allergy and Clinical Immunology 103, no. 1 (January 1, 1999): S148–49.Link to Item
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Buckley, R. H., N. Dinno, and P. Weber. “Angelman syndrome: are the estimates too low?” Am J Med Genet 80, no. 4 (December 4, 1998): 385–90. https://doi.org/10.1002/(sici)1096-8628(19981204)80:4<385::aid-ajmg15>3.0.co;2-9.Full Text Link to Item
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Puel, A., S. F. Ziegler, R. H. Buckley, and W. J. Leonard. “Defective IL7R expression in T(-)B(+)NK(+) severe combined immunodeficiency.” Nat Genet 20, no. 4 (December 1998): 394–97. https://doi.org/10.1038/3877.Full Text Link to Item
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Howrey, R. P., P. L. Martin, G. Ciocci, T. A. Driscoll, M. Frey, R. H. Buckley, W. H. Hickling, et al. “Unrelated cord blood transplantation for correction of genetic diseases.” Blood 92, no. 10 (November 15, 1998): 291A-291A.Link to Item
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Jabara, H. H., R. H. Buckley, J. L. Roberts, G. Lefranc, J. Loiselet, G. Khalil, and R. S. Geha. “Role of JAK3 in CD40-mediated signaling.” Blood 92, no. 7 (October 1, 1998): 2435–40.Link to Item
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Buckley, C. R. “Agammaglobulinemia, by Col. Ogden C. Bruton, MC, USA, Pediatrics, 1952;9:722-728.” Pediatrics 102, no. 1 Pt 2 (July 1998): 213–15.Link to Item
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Buckley, R. H. “Effect of genetic type of SCID on T, B, and NK cell function following bone marrow stem cell transplantation.” Faseb Journal 12, no. 5 (March 20, 1998).
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Jabara, H. H., R. H. Buckley, J. L. Roberts, G. Lefranc, J. Loiselet, G. Khalil, and R. S. Geha. “Role of JAK3 in CD40 mediated signaling.” Faseb Journal 12, no. 5 (March 20, 1998).
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Laughlin, M. J., D. A. Rizzieri, C. A. Smith, J. O. Moore, S. Lilly, D. McGaughey, P. Martin, et al. “Hematologic engraftment and reconstitution of immune function post unrelated placental cord blood transplant in an adult with acute lymphocytic leukemia.” Leuk Res 22, no. 3 (March 1998): 215–19. https://doi.org/10.1016/s0145-2126(97)00171-9.Full Text Link to Item
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Buckley, R. H., M. Carrington, J. L. Roberts, D. Riester, and F. E. Ward. “Influence of host HLA type on mixed leukocyte (ML) responsiveness of haploidentical donor T cells.” Journal of Allergy and Clinical Immunology 101, no. 1 (January 1, 1998): S100–101.Link to Item
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Daines, M. O., and R. H. Buckley. “T cell activation defect presenting with elevated IgE, eczema and severe food allergies.” Journal of Allergy and Clinical Immunology 101, no. 1 (January 1, 1998): S71–S71.Link to Item
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Markert, M. L., D. S. Hummell, H. M. Rosenblatt, S. E. Schiff, T. O. Harville, L. W. Williams, R. I. Schiff, and R. H. Buckley. “Complete DiGeorge syndrome: persistence of profound immunodeficiency.” J Pediatr 132, no. 1 (January 1998): 15–21. https://doi.org/10.1016/s0022-3476(98)70478-0.Full Text Link to Item
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Arrendondo-Vega, F. X., I. Santisteban, L. D. Notarangelo, J. El Dahr, R. Buckley, C. Roifman, M. E. Conley, and M. S. Hershfield. “Seven novel mutations in the adenosine deaminase (ADA) gene in patients with severe and delayed onset combined immunodeficiency: G74C, V129M, G140E, R149W, Q199P, 462delG, and E337del. Mutations in brief no. 142. Online.” Hum Mutat 11, no. 6 (1998): 482. https://doi.org/10.1002/(SICI)1098-1004(1998)11:6<482::AID-HUMU15>3.0.CO;2-E.Full Text Link to Item
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Laughlin, M. J., K. McKinnon, J. Demarest, R. Buckley, K. Weinhold, R. Kaufman, C. M. Koropchak, et al. “Immune recovery post unrelated allogeneic umbilical cord blood (UCB) transplantation in adult recipients.” Blood 90, no. 10 (November 15, 1997): 1868–1868.Link to Item
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Parker, W., P. B. Yu, Z. E. Holzknecht, K. Lundberg, R. H. Buckley, and J. L. Platt. “Specificity and function of "natural" antibodies in immunodeficient subjects: clues to B cell lineage and development.” J Clin Immunol 17, no. 4 (July 1997): 311–21. https://doi.org/10.1023/a:1027378716015.Full Text Link to Item
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Puck, J. M., A. E. Pepper, P. S. Henthorn, F. Candotti, J. Isakov, T. Whitwam, M. E. Conley, et al. “Mutation analysis of IL2RG in human X-linked severe combined immunodeficiency.” Blood 89, no. 6 (March 15, 1997): 1968–77.Link to Item
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Boeck, A., R. H. Buckley, and R. I. Schiff. “Gastroesophageal reflux and severe combined immunodeficiency.” J Allergy Clin Immunol 99, no. 3 (March 1997): 420–24. https://doi.org/10.1016/s0091-6749(97)70062-9.Full Text Link to Item
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Buckley, R. H., R. I. Schiff, S. E. Schiff, M. L. Markert, L. W. Williams, T. O. Harville, J. L. Roberts, and J. M. Puck. “Human severe combined immunodeficiency: genetic, phenotypic, and functional diversity in one hundred eight infants.” J Pediatr 130, no. 3 (March 1997): 378–87. https://doi.org/10.1016/s0022-3476(97)70199-9.Full Text Link to Item
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Davis, C. M., T. M. McLaughlin, T. J. Watson, R. H. Buckley, S. E. Schiff, L. P. Hale, B. F. Haynes, and M. L. Markert. “Normalization of the peripheral blood T cell receptor V beta repertoire after cultured postnatal human thymic transplantation in DiGeorge syndrome.” J Clin Immunol 17, no. 2 (March 1997): 167–75. https://doi.org/10.1023/a:1027382600143.Full Text Link to Item
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Markert, M. L., D. D. Kostyu, F. E. Ward, T. M. McLaughlin, T. J. Watson, R. H. Buckley, S. E. Schiff, et al. “Successful formation of a chimeric human thymus allograft following transplantation of cultured postnatal human thymus.” J Immunol 158, no. 2 (January 15, 1997): 998–1005.Link to Item
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Buckley, R. H. “Responsiveness of SCID lymphocytes to anti-CD3, PMA and Ionomycin before and after bone marrow transplantation.” Journal of Allergy and Clinical Immunology 99, no. 1 (January 1, 1997): 412–412.Link to Item
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Markert, M. L., T. J. Watson, T. M. McLaughlin, D. S. Hummel, H. M. Rosenblatt, S. E. Schiff, T. O. Harville, L. Williams, R. I. Schiff, and R. H. Buckley. “Complete DiGeorge syndrome: Persistence of profound immunodeficiency.” Journal of Allergy and Clinical Immunology 99, no. 1 (January 1, 1997): 1599–1599.Link to Item
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Myers, L. A., D. E. Riester, R. I. Schiff, S. E. Schiff, L. W. Williams, J. L. Roberts, J. M. Puck, and R. H. Buckley. “Bone marrow transplantation for SCID in the neonatal period.” Journal of Allergy and Clinical Immunology 99, no. 1 (January 1, 1997): 411–411.Link to Item
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Yel, L., H. Trubel, R. H. Buckley, L. M. Pachman, and M. E. Conley. “Clinical features in patients with mutations in the immunoglobulin mu heavy chain gene.” Journal of Allergy and Clinical Immunology 99, no. 1 (January 1, 1997): 1927–1927.Link to Item
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Buckley, R., M. W. Cobb, S. Ghurani, N. F. Brock, and R. R. Harford. “Mycobacterium fortuitum infection occurring after a punch biopsy procedure.” Pediatr Dermatol 14, no. 4 (1997): 290–92. https://doi.org/10.1111/j.1525-1470.1997.tb00960.x.Full Text Link to Item
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SHEARER, WILLIAM T., REBECCA H. BUCKLEY, RENATA J. M. ENGLER, ALBERT F. FINN, THOMAS A. FLEISHER, THEODORE M. FREEMAN, HENRY G. HERROD, et al. “Practice Parameters for the Diagnosis and Management of Immunodeficiency.” Pediatric Asthma, Allergy &Amp; Immunology 11, no. 1 (January 1997): 45–64. https://doi.org/10.1089/pai.1997.11.45.Full Text
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Schiff, R. I., L. W. Williams, R. P. Nelson, R. H. Buckley, W. Burks, and R. A. Good. “Multicenter crossover comparison of the safety and efficacy of Intraglobin-F with Gamimune-N, Sandoglobulin, and Gammagard in patients with primary immunodeficiency diseases.” J Clin Immunol 17, no. 1 (January 1997): 21–28. https://doi.org/10.1023/a:1027380210989.Full Text Link to Item
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Yel, L., Y. Minegishi, E. Coustan-Smith, R. H. Buckley, H. Trübel, L. M. Pachman, G. R. Kitchingman, D. Campana, J. Rohrer, and M. E. Conley. “Mutations in the mu heavy-chain gene in patients with agammaglobulinemia.” N Engl J Med 335, no. 20 (November 14, 1996): 1486–93. https://doi.org/10.1056/NEJM199611143352003.Full Text Link to Item
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Washington, K., T. T. Stenzel, R. H. Buckley, and M. R. Gottfried. “Gastrointestinal pathology in patients with common variable immunodeficiency and X-linked agammaglobulinemia.” Am J Surg Pathol 20, no. 10 (October 1996): 1240–52. https://doi.org/10.1097/00000478-199610000-00010.Full Text Link to Item
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Markert, M. L., C. M. Davis, F. E. Ward, D. D. Kostyu, R. H. Buckley, S. E. Schiff, T. J. Watson, et al. “Thymic transplantation for digeorge syndrome.” Faseb Journal 10, no. 6 (April 30, 1996): 373–373.Link to Item
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Roberts, J. L., I. I. OShea, J. M. Puck, and R. H. Buckley. “Human autosomal recessive SCID due to Jak3 deficiency.” Faseb Journal 10, no. 6 (April 30, 1996): 370–370.Link to Item
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Buckley, R. H., R. E. Schiff, S. E. Schiff, M. L. Markert, L. W. Williams, T. O. Harville, J. L. Roberts, and J. Puck. “Human severe combined immunodeficiency (SCID): Genetic, phenotypic and functional diversity in 95 infants.” Pediatric Research 39, no. 4 (April 1, 1996): 41–41.Link to Item
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Broome, C. B., M. L. Graham, F. T. Saulsbury, M. S. Hershfield, and R. H. Buckley. “Correction of purine nucleoside phosphorylase deficiency by transplantation of allogeneic bone marrow from a sibling.” J Pediatr 128, no. 3 (March 1996): 373–76. https://doi.org/10.1016/s0022-3476(96)70285-8.Full Text Link to Item
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Shearer, W. T., R. H. Buckley, R. J. Engler, A. F. Finn, T. A. Fleisher, T. M. Freeman, H. G. Herrod, et al. “Practice parameters for the diagnosis and management of immunodeficiency. The Clinical and Laboratory Immunology Committee of the American Academy of Allergy, Asthma, and Immunology (CLIC-AAAAI).” Ann Allergy Asthma Immunol 76, no. 3 (March 1996): 282–94. https://doi.org/10.1016/s1081-1206(10)63442-4.Full Text Link to Item
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Russell, S. M., N. Tayebi, H. Nakajima, M. C. Riedy, J. L. Roberts, M. J. Aman, T. S. Migone, et al. “Mutation of Jak3 in a patient with SCID: essential role of Jak3 in lymphoid development.” Science 270, no. 5237 (November 3, 1995): 797–800. https://doi.org/10.1126/science.270.5237.797.Full Text Link to Item
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MARKERT, M. L., T. J. WATSON, T. M. MCLAUGHLIN, C. A. MCGUIRE, F. E. WARD, D. KOSTYU, L. P. HALE, et al. “DEVELOPMENT OF T-CELL FUNCTION AFTER POSTNATAL THYMIC TRANSPLANTATION FOR DIGEORGE-SYNDROME.” American Journal of Human Genetics 57, no. 4 (October 1, 1995): 64–64.Link to Item
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PEPPER, A. E., R. H. BUCKLEY, T. N. SMALL, and J. M. PUCK. “2 MUTATIONAL HOTSPOTS IN THE INTERLEUKIN-2 RECEPTOR-GAMMA CHAIN GENE CAUSING HUMAN X-LINKED SEVERE COMBINED IMMUNODEFICIENCY.” American Journal of Human Genetics 57, no. 3 (September 1, 1995): 564–71.Link to Item
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Pepper, A. E., R. H. Buckley, T. N. Small, and J. M. Puck. “Two mutational hotspots in the interleukin-2 receptor gamma chain gene causing human X-linked severe combined immunodeficiency.” Am J Hum Genet 57, no. 3 (September 1995): 564–71.Link to Item
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BUCKLEY, R. H., R. I. SCHIFF, M. L. MARKERT, L. W. WILLIAMS, T. O. HARVILLE, and S. E. SCHIFF. “IMMUNOBIOLOGY OF HUMAN SEVERE COMBINED IMMUNODEFICIENCY.” Faseb Journal 9, no. 4 (March 10, 1995): A780–A780.Link to Item
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MARKERT, M. L., F. E. WARD, D. KOSTYU, R. H. BUCKLEY, S. E. SCHIFF, J. J. H. BLEESING, C. B. BROOME, et al. “DEVELOPMENT OF T-CELL FUNCTION AFTER POSTNATAL THYMIC TRANSPLANTATION FOR DIGEORGE-SYNDROME.” Faseb Journal 9, no. 4 (March 10, 1995): A780–A780.Link to Item
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BROOME, C. B., M. L. GRAHAM, F. T. SAULSBURY, M. S. HERSHFIELD, and R. H. BUCKLEY. “SUCCESSFUL BONE-MARROW TRANSPLANTATION (BMT) FOR PURINE NUCLEOSIDE PHOSPHORYLASE (PNP) DEFICIENCY.” Journal of Allergy and Clinical Immunology 95, no. 1 (January 1, 1995): 142–142.Link to Item
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BUCKLEY, R. H. “ATYPICAL X-LINKED AGAMMAGLOBULINEMIA - REPLY.” New England Journal of Medicine 331, no. 14 (October 6, 1994): 950–51.Link to Item
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Kornfeld, S. J., R. A. Good, and G. W. Litman. “Atypical X-linked agammaglobulinemia.” N Engl J Med 331, no. 14 (October 6, 1994): 949–51.Link to Item
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Conley, M. E., M. Larché, V. R. Bonagura, A. R. Lawton, R. H. Buckley, S. M. Fu, E. Coustan-Smith, H. G. Herrod, and D. Campana. “Hyper IgM syndrome associated with defective CD40-mediated B cell activation.” J Clin Invest 94, no. 4 (October 1994): 1404–9. https://doi.org/10.1172/JCI117476.Full Text Link to Item
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Buckley, R. H. “Breakthroughs in the understanding and therapy of primary immunodeficiency.” Pediatr Clin North Am 41, no. 4 (August 1994): 665–90. https://doi.org/10.1016/s0031-3955(16)38803-4.Full Text Link to Item
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Borchardt, R. A., W. T. Lee, A. Kalen, R. H. Buckley, C. Peters, S. Schiff, and R. M. Bell. “Growth-dependent regulation of cellular ceramides in human T-cells.” Biochim Biophys Acta 1212, no. 3 (June 2, 1994): 327–36. https://doi.org/10.1016/0005-2760(94)90207-0.Full Text Link to Item
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Buckley, R. H. “Assessing inheritance of agammaglobulinemia.” N Engl J Med 330, no. 21 (May 26, 1994): 1526–28. https://doi.org/10.1056/NEJM199405263302111.Full Text Link to Item
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HARVILLE, T. O., K. E. NORVELL, and R. H. BUCKLEY. “POLYCLONAL MATERNAL T-LYMPHOCYTES ARE PRESENT IN INFANTS WITH SEVERE COMBINED IMMUNODEFICIENCY (SCID) PRIOR TO BONE-MARROW TRANSPLANTATION (BMT).” Pediatric Research 35, no. 4 (April 1, 1994): A11–A11.Link to Item
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BUCKLEY, R. H., J. KLUGE, and A. LEVINE. “IGE SYNTHESIS BY B-CELLS FROM IMMUNODEFICIENCY PATIENTS.” Faseb Journal 8, no. 5 (March 18, 1994): A752–A752.Link to Item
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Buckley, R. H., S. E. Schiff, R. I. Schiff, J. L. Roberts, M. L. Markert, W. Peters, L. W. Williams, and F. E. Ward. “Haploidentical bone marrow stem cell transplantation in human severe combined immunodeficiency.” Semin Hematol 30, no. 4 Suppl 4 (October 1993): 92–101.Link to Item
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BUCKLEY, R. H., S. E. SCHIFF, R. I. SCHIFF, M. L. MARKERT, L. W. WILLIAMS, and F. E. WARD. “HAPLOIDENTICAL STEM-CELL THERAPY FOR HUMAN SEVERE COMBINED IMMUNODEFICIENCY (SCID) - ANALYSIS AT 10 YEARS.” Clinical Research 41, no. 2 (April 1, 1993): A278–A278.Link to Item
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Buckley, R. H., S. E. Schiff, R. I. Schiff, J. L. Roberts, M. L. Markert, W. Peters, L. W. Williams, et al. “Haploidentical bone marrow stem cell transplantation in human severe combined immunodeficiency.” Seminars in Hematology 30, no. 4 SUPPL. 4 (January 1, 1993): 92–104.
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Buckley, R. H. “Immunodeficiency diseases.” Jama 268, no. 20 (November 25, 1992): 2797–2806.Link to Item
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Ochs, H. D., R. H. Buckley, R. H. Kobayashi, A. L. Kobayashi, R. U. Sorensen, S. D. Douglas, B. L. Hamilton, and M. S. Hershfield. “Antibody responses to bacteriophage phi X174 in patients with adenosine deaminase deficiency.” Blood 80, no. 5 (September 1, 1992): 1163–71.Link to Item
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Claassen, J. L., A. D. Levine, and R. H. Buckley. “Mechanism of pokeweed mitogen inhibition of rhIL-4-induced human IgE synthesis.” Cell Immunol 140, no. 2 (April 1992): 357–69. https://doi.org/10.1016/0008-8749(92)90202-z.Full Text Link to Item
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Eggleston, P. A., D. P. Huston, W. T. Shearer, K. J. Bloch, W. W. Busse, R. R. Rich, V. R. Bonagura, et al. “Workshop C: The growing importance of clinical immunology: Impact on the allergy training program and the practice of allergy.” Journal of Allergy and Clinical Immunology 90, no. 6 I (1992): 999–1001. https://doi.org/10.1016/0091-6749(92)90476-I.Full Text
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Bloch, K. J., R. H. Buckley, and P. F. Kohler. “Diagnostic laboratory immunology: a subspecialty that encompasses clinical as well as laboratory immunology.” J Allergy Clin Immunol 88, no. 6 (December 1991): 961–63. https://doi.org/10.1016/0091-6749(91)90254-l.Full Text Link to Item
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Claasen, J. J., A. D. Levine, S. E. Schiff, and R. H. Buckley. “Mononuclear cells from patients with the hyper-IgE syndrome produce little IgE when they are stimulated with recombinant human interleukin-4.” J Allergy Clin Immunol 88, no. 5 (November 1991): 713–21. https://doi.org/10.1016/0091-6749(91)90177-p.Full Text Link to Item
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Gaines, A. D., S. E. Schiff, and R. H. Buckley. “Donor type natural killer cells after haploidentical T cell-depleted bone marrow stem cell transplantation in a patient with adenosine deaminase-deficient severe combined immunodeficiency.” Clin Immunol Immunopathol 60, no. 2 (August 1991): 299–304. https://doi.org/10.1016/0090-1229(91)90072-i.Full Text Link to Item
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Buckley, R. H., and R. I. Schiff. “The use of intravenous immune globulin in immunodeficiency diseases.” N Engl J Med 325, no. 2 (July 11, 1991): 110–17. https://doi.org/10.1056/NEJM199107113250207.Full Text Link to Item
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Schiff, R. I., D. Sedlak, and R. H. Buckley. “Rapid infusion of Sandoglobulin in patients with primary humoral immunodeficiency.” J Allergy Clin Immunol 88, no. 1 (July 1991): 61–67. https://doi.org/10.1016/0091-6749(91)90301-4.Full Text Link to Item
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Sheerin, K. A., and R. H. Buckley. “Antibody responses to protein, polysaccharide, and phi X174 antigens in the hyperimmunoglobulinemia E (hyper-IgE) syndrome.” J Allergy Clin Immunol 87, no. 4 (April 1991): 803–11. https://doi.org/10.1016/0091-6749(91)90126-9.Full Text Link to Item
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BUCKLEY, R. H., S. E. SCHIFF, and A. R. HAYWARD. “REDUCED FREQUENCY OF CD45RO+ LYMPHOCYTES-T IN BLOOD OF HYPER IGE SYNDROME PATIENTS.” Faseb Journal 5, no. 6 (March 19, 1991): A1636–A1636.Link to Item
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Friedman, N. J., S. E. Shiff, F. E. Ward, R. I. Schiff, and R. H. Buckley. “Graft versus graft and graft versus host reactions after HLA‐identical bone marrow transplantation in a patient with severe combined immunodeficiency with transplacentally acquired lymphoid chimerism.” Pediatric Allergy and Immunology 2, no. 3 (January 1, 1991): 111–16. https://doi.org/10.1111/j.1399-3038.1991.tb00192.x.Full Text
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Gossage, D. L., and R. H. Buckley. “Prevalence of lymphocytopenia in severe combined immunodeficiency.” N Engl J Med 323, no. 20 (November 15, 1990): 1422–23. https://doi.org/10.1056/NEJM199011153232014.Full Text Link to Item
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Conley, M. E., R. H. Buckley, R. Hong, C. Guerra-Hanson, C. M. Roifman, J. A. Brochstein, S. Pahwa, and J. M. Puck. “X-linked severe combined immunodeficiency. Diagnosis in males with sporadic severe combined immunodeficiency and clarification of clinical findings.” J Clin Invest 85, no. 5 (May 1990): 1548–54. https://doi.org/10.1172/JCI114603.Full Text Link to Item
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Puck, J. M., C. M. Krauss, S. M. Puck, R. H. Buckley, and M. E. Conley. “Prenatal test for X-linked severe combined immunodeficiency by analysis of maternal X-chromosome inactivation and linkage analysis.” N Engl J Med 322, no. 15 (April 12, 1990): 1063–66. https://doi.org/10.1056/NEJM199004123221508.Full Text Link to Item
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Claassen, J. L., A. D. Levine, and R. H. Buckley. “Recombinant human IL-4 induces IgE and IgG synthesis by normal and atopic donor mononuclear cells. Similar dose response, time course, requirement for T cells, and effect of pokeweed mitogen.” J Immunol 144, no. 6 (March 15, 1990): 2123–30.Link to Item
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Kent, E. F., J. Crawford, H. J. Cohen, and R. H. Buckley. “Development of multiple monoclonal serum immunoglobulins (multiclonal gammopathy) following both HLA-identical unfractionated and T cell-depleted haploidentical bone marrow transplantation in severe combined immunodeficiency.” J Clin Immunol 10, no. 2 (March 1990): 106–14. https://doi.org/10.1007/BF00918192.Full Text Link to Item
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Claassen, J. L., A. D. Levine, and R. H. Buckley. “A cell culture system that enhances mononuclear cell IgE synthesis induced by recombinant human interleukin-4.” J Immunol Methods 126, no. 2 (February 9, 1990): 213–22. https://doi.org/10.1016/0022-1759(90)90153-m.Full Text Link to Item
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Roberts, J. L., D. J. Volkman, and R. H. Buckley. “Modified MHC restriction of donor-origin T cells in humans with severe combined immunodeficiency transplanted with haploidentical bone marrow stem cells.” J Immunol 143, no. 5 (September 1, 1989): 1575–79.Link to Item
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Gaines, A. D., and R. H. Buckley. “Impaired antibody response to polysaccharides in association with functional asplenia.” J Pediatr 114, no. 1 (January 1989): 89–91. https://doi.org/10.1016/s0022-3476(89)80607-9.Full Text Link to Item
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Welch, M. J., J. P. Kemp, C. W. Bierman, E. A. Bronsky, R. H. Buckley, R. K. Bush, R. J. Dockhorn, et al. “Comparison of Bitolterol Mesylate and Isoproterenol by Metered-Dose Inhaler for Regular, Long-Term Treatment in Asthmatic Children.” Pediatric Asthma, Allergy and Immunology 3, no. 1 (January 1, 1989): 27–36. https://doi.org/10.1089/pai.1989.3.27.Full Text
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Barrett, M. J., R. H. Buckley, S. E. Schiff, P. C. Kidd, and F. E. Ward. “Accelerated development of immunity following transplantation of maternal marrow stem cells into infants with severe combined immunodeficiency and transplacentally acquired lymphoid chimerism.” Clin Exp Immunol 72, no. 1 (April 1988): 118–23.Link to Item
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ROBERTS, J. L., D. J. VOLKMAN, and R. H. BUCKLEY. “MODIFIED T-CELL MHC RESTRICTION FOLLOWING SUCCESSFUL HAPLOIDENTICAL BONE-MARROW STEM-CELL TRANSPLANTATION IN SEVERE COMBINED IMMUNODEFICIENCY DISEASE (SCID).” Faseb Journal 2, no. 4 (March 15, 1988): A448–A448.Link to Item
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Buckley, R. H. “Certification in diagnostic laboratory immunology.” Ann Intern Med 108, no. 3 (March 1988): 458–59. https://doi.org/10.7326/0003-4819-108-3-458.Full Text Link to Item
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Mings, R., A. P. Knutsen, L. W. Williams, R. H. Buckley, and R. W. Warren. “Immune Thrombocytopenia Treated with High-Dose Intravenous Gamma Globulin and Corticosteroids in Two Patients with Wiskott-Aldrich Syndrome.” Pediatric Asthma, Allergy and Immunology 2, no. 3 (January 1, 1988): 191–97. https://doi.org/10.1089/pai.1988.2.191.Full Text
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Buckley, R. H. “Immunodeficiency diseases.” Jama 258, no. 20 (November 27, 1987): 2841–50.Link to Item
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Kaplan, A. P., R. H. Buckley, and K. P. Mathews. “Allergic skin disorders.” Jama 258, no. 20 (November 27, 1987): 2900–2909.Link to Item
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Sampson, H. A., R. H. Buckley, and D. D. Metcalfe. “Food allergy.” Jama 258, no. 20 (November 27, 1987): 2886–90.Link to Item
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Markert, M. L., M. S. Hershfield, R. I. Schiff, and R. H. Buckley. “Adenosine deaminase and purine nucleoside phosphorylase deficiencies: evaluation of therapeutic interventions in eight patients.” J Clin Immunol 7, no. 5 (September 1987): 389–99. https://doi.org/10.1007/BF00917017.Full Text Link to Item
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Claassen, J. L., S. C. Eppes, and R. H. Buckley. “Pulmonary coin lesion caused by Neisseria mucosa in a child with chronic granulomatous disease.” Pediatr Infect Dis J 6, no. 6 (June 1987): 567–69. https://doi.org/10.1097/00006454-198706000-00016.Full Text Link to Item
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Schiff, S. E., J. Kurtzberg, and R. H. Buckley. “Studies of human bone marrow treated with soybean lectin and sheep erythrocytes: stepwise analysis of cell morphology, phenotype and function.” Clin Exp Immunol 68, no. 3 (June 1987): 685–93.Link to Item
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Markert, M. L., M. S. Hershfield, D. A. Wiginton, J. C. States, F. E. Ward, S. H. Bigner, R. H. Buckley, R. E. Kaufman, and J. J. Hutton. “Identification of a deletion in the adenosine deaminase gene in a child with severe combined immunodeficiency.” J Immunol 138, no. 10 (May 15, 1987): 3203–6.Link to Item
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Buckley, R. H. “Advances in the correction of immunodeficiency by bone marrow transplantation.” Pediatr Ann 16, no. 5 (May 1987): 412–21. https://doi.org/10.3928/0090-4481-19870501-09.Full Text Link to Item
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Schiff, S. E., and R. H. Buckley. “Modified responses to recipient and donor B cells by genetically donor T cells from human haploidentical bone marrow chimeras.” J Immunol 138, no. 7 (April 1, 1987): 2088–94.Link to Item
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Hershfield, M. S., R. H. Buckley, M. L. Greenberg, A. L. Melton, R. Schiff, C. Hatem, J. Kurtzberg, M. L. Markert, R. H. Kobayashi, and A. L. Kobayashi. “Treatment of adenosine deaminase deficiency with polyethylene glycol-modified adenosine deaminase.” N Engl J Med 316, no. 10 (March 5, 1987): 589–96. https://doi.org/10.1056/NEJM198703053161005.Full Text Link to Item
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BARRETT, M. J., S. E. SCHIFF, P. C. KIDD, and R. H. BUCKLEY. “DEVELOPMENT OF IMMUNITY IN SEVERE COMBINED IMMUNODEFICIENCY (SCID) WITH TRANSPLACENTALLY ACQUIRED MATERNAL LYMPHOCYTES FOLLOWING TRANSPLANTATION OF T-DEPLETED MATERNAL STEM-CELLS.” Federation Proceedings 46, no. 3 (March 1, 1987): 1022–1022.Link to Item
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BUCKLEY, R. H., and H. D. OCHS. “DEVELOPMENT OF B-CELL FUNCTION IN HUMAN HAPLOIDENTICAL BONE-MARROW CHIMERAS.” Federation Proceedings 46, no. 3 (March 1, 1987): 1021–1021.Link to Item
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Björkander, J., L. Hammarström, C. I. Smith, R. H. Buckley, C. Cunningham-Rundles, and L. A. Hanson. “Immunoglobulin prophylaxis in patients with antibody deficiency syndromes and anti-IgA antibodies.” J Clin Immunol 7, no. 1 (January 1987): 8–15. https://doi.org/10.1007/BF00915419.Full Text Link to Item
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Buckley, R. H. “Certification in Diagnostic Laboratory Immunology.” Pediatric Asthma, Allergy and Immunology 1, no. 4 (January 1, 1987): 189–90. https://doi.org/10.1089/pai.1987.1.189.Full Text
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Leickly, F. E., and R. H. Buckley. “Successful treatment of autoimmune hemolytic anemia in common variable immunodeficiency with high-dose intravenous gamma globulin.” Am J Med 82, no. 1 (January 1987): 159–62. https://doi.org/10.1016/0002-9343(87)90398-6.Full Text Link to Item
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Markert, M. L., and R. H. Buckley. “Natural-killer-cell function and bone marrow transplantation.” N Engl J Med 315, no. 22 (November 27, 1986): 1418–19. https://doi.org/10.1056/NEJM198611273152216.Full Text Link to Item
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Conley, M. E., P. Brown, A. R. Pickard, R. H. Buckley, D. S. Miller, W. H. Raskind, J. W. Singer, and P. J. Fialkow. “Expression of the gene defect in X-linked agammaglobulinemia.” N Engl J Med 315, no. 9 (August 28, 1986): 564–67. https://doi.org/10.1056/NEJM198608283150907.Full Text Link to Item
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BURKS, A. W., H. A. SAMPSON, and R. H. BUCKLEY. “ANAPHYLAXIS AFTER ADMINISTRATION OF GAMMA-GLOBULIN FOR HYPOGAMMAGLOBULINEMIA - REPLY.” New England Journal of Medicine 315, no. 8 (August 21, 1986): 520–520.Link to Item
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“Anaphylaxis after administration of gamma globulin for hypogammaglobulinemia.” N Engl J Med 315, no. 8 (August 21, 1986): 519–20. https://doi.org/10.1056/NEJM198608213150817.Full Text Link to Item
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BUCKLEY, R. H. “SYMPOSIUM CHILDHOOD IMMUNODEFICIENCY DISORDERS - DIAGNOSIS, PREVENTION, AND MANAGEMENT - INTRODUCTION.” Clinical Immunology and Immunopathology 40, no. 1 (July 1, 1986): 40–40.Link to Item
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Buckley, R. H. “Humoral immunodeficiency.” Clin Immunol Immunopathol 40, no. 1 (July 1986): 13–24. https://doi.org/10.1016/0090-1229(86)90065-6.Full Text Link to Item
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Leickley, F. E., and R. Buckley. “Variability in B cell maturation and differentiation in X-linked agammaglobulinemia.” Clin Exp Immunol 65, no. 1 (July 1986): 90–99.Link to Item
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Guill, M. F., R. H. Buckley, W. Rocha, J. P. Kemp, A. T. Segal, L. R. Shirley, D. G. Tinkelman, Z. Shaath-Schwen, K. K. Dietrich, and L. J. Wille. “Multicenter, double-blind, placebo-controlled trial of terfenadine suspension in the treatment of fall-allergic rhinitis in children.” J Allergy Clin Immunol 78, no. 1 Pt 1 (July 1986): 4–9. https://doi.org/10.1016/0091-6749(86)90107-7.Full Text Link to Item
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Helm, R. M., R. H. Buckley, N. F. Adkinson, D. L. Squillace, G. J. Gleich, and J. W. Yunginger. “Variability of IgE protein measurement in cell-culture supernatants: results from a multicenter collaborative study.” J Allergy Clin Immunol 77, no. 6 (June 1986): 880–90. https://doi.org/10.1016/0091-6749(86)90387-8.Full Text Link to Item
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Buckley, R. H., S. E. Schiff, H. A. Sampson, R. I. Schiff, M. L. Markert, A. P. Knutsen, M. S. Hershfield, A. T. Huang, G. H. Mickey, and F. E. Ward. “Development of immunity in human severe primary T cell deficiency following haploidentical bone marrow stem cell transplantation.” J Immunol 136, no. 7 (April 1, 1986): 2398–2407.Link to Item
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CONLEY, M. E., R. H. BUCKLEY, W. H. RASKIND, and P. J. FIALKOW. “EXPRESSION OF GENE DEFECT IN X-LINKED AGAMMAGLOBULINEMIA (XLA) IS INTRINSIC TO THE B-CELL LINEAGE.” Clinical Research 34, no. 2 (April 1, 1986): A668–A668.Link to Item
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CONLEY, M. E., R. H. BUCKLEY, W. H. RASKIND, and P. J. FIALKOW. “EXPRESSION OF GENE DEFECT IN X-LINKED AGAMMAGLOBULINEMIA (XLA) IS INTRINSIC TO THE B-CELL LINEAGE.” Pediatric Research 20, no. 4 (April 1, 1986): A301–A301.Link to Item
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MCKINNEY, R. E., M. L. MARKERT, L. W. WILLIAMS, R. H. BUCKLEY, and C. M. WILFERT. “THE USE OF INTRAVENOUS IMMUNOGLOBULIN (IVIG) PREPARATIONS IN THE TREATMENT OF CHRONIC ENTEROVIRAL INFECTIONS.” Pediatric Research 20, no. 4 (April 1, 1986): A297–A297.Link to Item
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SCHIFF, S. E., H. A. SAMPSON, and R. H. BUCKLEY. “RESPONSES TO RECIPIENT AND DONOR B-CELLS BY GENETICALLY DONOR T-CELLS FROM HUMAN HAPLOIDENTICAL CHIMERAS.” Clinical Research 34, no. 2 (April 1, 1986): A850–A850.Link to Item
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Ammann, A. J., M. Cowan, D. Wara, M. Heyman, M. M. Thaler, R. Buckley, A. Lawton, L. B. Vogler, and R. Hirschhorn. “Alpha-fetoprotein levels in immunodeficiency.” N Engl J Med 314, no. 11 (March 13, 1986): 717–18. https://doi.org/10.1056/NEJM198603133141118.Full Text Link to Item
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Leickly, F. E., and R. H. Buckley. “Development of IgA and IgG2 subclass deficiency after sulfasalazine therapy.” J Pediatr 108, no. 3 (March 1986): 481–82. https://doi.org/10.1016/s0022-3476(86)80907-6.Full Text Link to Item
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Ghory, P., S. Schiff, and R. Buckley. “Appearance of multiple benign paraproteins during early engraftment of soy lectin T cell-depleted haploidentical bone marrow cells in severe combined immunodeficiency.” J Clin Immunol 6, no. 2 (March 1986): 161–69. https://doi.org/10.1007/BF00918749.Full Text Link to Item
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Burks, A. W., H. A. Sampson, and R. H. Buckley. “Anaphylactic reactions after gamma globulin administration in patients with hypogammaglobulinemia. Detection of IgE antibodies to IgA.” N Engl J Med 314, no. 9 (February 27, 1986): 560–64. https://doi.org/10.1056/NEJM198602273140907.Full Text Link to Item
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Buckley, R. H. “Advances in the diagnosis and treatment of primary immunodeficiency diseases.” Arch Intern Med 146, no. 2 (February 1986): 377–84.Link to Item
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BURKS, A. W., H. A. SAMPSON, and R. H. BUCKLEY. “ANAPHYLACTIC REACTIONS FOLLOWING GAMMA-GLOBULIN ADMINISTRATION IN PATIENTS WITH HYPOGAMMAGLOBULINEMIA - DETECTION OF IGE ANTIBODIES TO IGA.” Clinical Research 34, no. 1 (January 1, 1986): A246–A246.Link to Item
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Buckley, R. H. “Introduction.” Clinical Immunology and Immunopathology 40, no. 1 (January 1, 1986): 4. https://doi.org/10.1016/0090-1229(86)90063-2.Full Text Open Access Copy
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Buckley, R. H. “Certification in diagnostic laboratory immunology.” Annals of Internal Medicine 104, no. 3 (January 1, 1986): 435. https://doi.org/10.7326/0003-4819-104-3-435.Full Text
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Siegel, S. C., D. D. Sogn, C. W. Bierman, R. H. Buckley, E. F. Ellis, T. J. Fischer, H. Levinson, R. M. Sly, and W. F. Westlin. “Workshop 7: Special pediatric problems.” The Journal of Allergy and Clinical Immunology 78, no. 3 PART 2 (January 1, 1986): 534–40. https://doi.org/10.1016/0091-6749(86)90101-6.Full Text
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Buckley, Rebecca H., Sherrie E. Schiff, Hugh A. Sampson, Richard I. Schiff, Bonnie E. Ammerman, Ruby R. Johnson, and Frances E. Ward. “960 DEVELOPMENT OF IMMUNITY IN SEVERE PRIMARY T CELL DEFICIENCY FOLLOWING HAPLOIDENTICAL STEM CELL TRANSPLANTATION.” Pediatric Research 19, no. 4 (April 1985): 270A-270A. https://doi.org/10.1203/00006450-198504000-00990.Full Text
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BUCKLEY, R. H. “GAMMA-GLOBULIN REPLACEMENT.” Clinics in Immunology and Allergy 5, no. 1 (January 1, 1985): 141–58.Link to Item
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BUCKLEY, R. H., S. E. SCHIFF, H. A. SAMPSON, R. I. SCHIFF, B. AMMERMAN, R. R. JOHNSON, and F. E. WARD. “DEVELOPMENT OF IMMUNITY IN SEVERE PRIMARY T-CELL DEFICIENCY FOLLOWING HAPLOIDENTICAL STEM-CELL TRANSPLANTATION.” Federation Proceedings 44, no. 6 (January 1, 1985): 1922–1922.Link to Item
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Buckley, R. H. “γ-Globulin replacement.” Clinics in Immunology and Allergy 5, no. 1 (January 1, 1985): 141–58.
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Buckley, R. H., S. E. Schiff, and H. A. Sampson. “Development of immunity in severe primary T cell deficiency following haploidentical stem cell transplantation.” Federation Proceedings 44, no. 6 (January 1, 1985).
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DeVoe, P. W., R. H. Buckley, L. R. Shirley, C. P. Darby, F. E. Ward, G. H. Mickey, N. Raab-Traub, and G. R. Vandenbark. “Successful immune reconstitution in severe combined immunodeficiency despite Epstein-Barr virus and cytomegalovirus infections.” Clin Immunol Immunopathol 34, no. 1 (January 1985): 48–59. https://doi.org/10.1016/0090-1229(85)90006-6.Full Text Link to Item
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LEICKLY, F. E., and R. H. BUCKLEY. “SUCCESSFUL TREATMENT OF AUTOIMMUNE HEMOLYTIC-ANEMIA (AIHA) IN COMMON VARIABLE IMMUNODEFICIENCY (CVID) WITH HIGH-DOSE INTRAVENOUS IMMUNE GLOBULIN (IVIG).” Pediatric Research 19, no. 4 (January 1, 1985): A278–A278.Link to Item
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Thompson, L. F., H. L. Spiegelberg, and R. H. Buckley. “IgE Fc receptor positive T and B lymphocytes in patients with the hyper IgE syndrome.” Clin Exp Immunol 59, no. 1 (January 1985): 77–84.Link to Item
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Spiegelberg, H. L., L. F. Thompson, D. McNeil, and R. H. Buckley. “IgE Fc receptor positive T, B and NK cells in patients with the hyper-IgE syndrome.” Int Arch Allergy Appl Immunol 77, no. 1–2 (1985): 277–79. https://doi.org/10.1159/000233809.Full Text Link to Item
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Smego, R. A., P. W. Devoe, H. A. Sampson, J. R. Perfect, C. M. Wilfert, and R. H. Buckley. “Candida meningitis in two children with severe combined immunodeficiency.” J Pediatr 104, no. 6 (June 1984): 902–4. https://doi.org/10.1016/s0022-3476(84)80493-x.Full Text Link to Item
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Sindel, L. J., R. H. Buckley, S. E. Schiff, F. E. Ward, G. H. Mickey, A. T. Huang, C. Naspitz, and H. Koren. “Severe combined immunodeficiency with natural killer-cell predominance: abrogation of graft-versus-host disease and immunologic reconstitution with HLA-identical bone marrow cells.” J Allergy Clin Immunol 73, no. 6 (June 1984): 829–36. https://doi.org/10.1016/0091-6749(84)90455-x.Full Text Link to Item
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Schiff, R. I., C. Rudd, R. Johnson, and R. H. Buckley. “Use of a new chemically modified intravenous IgG preparation in severe primary humoral immunodeficiency: clinical efficacy and attempts to individualize dosage.” Clin Immunol Immunopathol 31, no. 1 (April 1984): 13–23. https://doi.org/10.1016/0090-1229(84)90185-5.Full Text Link to Item
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BURKS, A. W., and R. H. BUCKLEY. “ANAPHYLACTIC REACTIONS IN COMMON VARIABLE AGAMMAGLOBULINEMIA (CVA-GAMMA) - TREATMENT WITH IGA-DEFICIENT INTRAVENOUS IMMUNE GLOBULIN (IVIG).” Clinical Research 32, no. 5 (January 1, 1984): A891–A891.Link to Item
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Spiegelberg, H. L., L. F. Thompson, and R. H. Buckley. “IgE Fc receptor positive lymphocytes in patients with the hyper-IgE syndrome.” Federation Proceedings 43, no. 7 (January 1, 1984).
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Ayres, S. “Atopic dermatitis--a new therapeutic regimen.” Jama 250, no. 21 (December 2, 1983): 2926–27. https://doi.org/10.1001/jama.1983.03340210024009.Full Text Link to Item
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Buckley, R. H. “Immunodeficiency.” J Allergy Clin Immunol 72, no. 6 (December 1983): 627–41. https://doi.org/10.1016/0091-6749(83)90619-x.Full Text Link to Item
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Buckley, R. H., and D. D. Metcalfe. “In Reply.” Jama: The Journal of the American Medical Association 250, no. 20 (November 25, 1983): 2792. https://doi.org/10.1001/jama.1983.03340200025018.Full Text
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Kohler, P. F., R. H. Buckley, and K. J. Bloch. “Implications of "certification in diagnostic laboratory immunology" for the training and practice in allergy-immunology.” J Allergy Clin Immunol 72, no. 2 (August 1983): 121–22. https://doi.org/10.1016/0091-6749(83)90517-1.Full Text Link to Item
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Haynes, B. F., R. W. Warren, R. H. Buckley, J. E. McClure, A. L. Goldstein, F. W. Henderson, L. L. Hensley, and G. S. Eisenbarth. “Demonstration of abnormalities in expression of thymic epithelial surface antigens in severe cellular immunodeficiency diseases.” J Immunol 130, no. 3 (March 1983): 1182–88.Link to Item
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BUCKLEY, R. H., and D. D. METCALFE. “FOOD ALLERGY - REPLY.” Jama Journal of the American Medical Association 250, no. 20 (January 1, 1983): 2792–2792.Link to Item
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Buckley, R. H., S. Gard, B. F. Haynes, L. J. Sindel, K. Davis, H. A. Sampson, M. E. Ruff, and H. S. Koren. “Severe combined immunodeficiency (SCID) with natural killer (NK) cell predominance.” Birth Defects Orig Artic Ser 19, no. 3 (1983): 101–4.Link to Item
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Buckley, R. H., S. Gard, R. I. Schiff, and H. A. Sampson. “T cells and T-cell subsets in a large population of patients with primary immunodeficiency.” Birth Defects Orig Artic Ser 19, no. 3 (1983): 187–91.Link to Item
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Haynes, B. F., R. W. Warren, R. H. Buckley, J. E. McClure, A. L. Goldstein, F. W. Henderson, L. L. Hensley, and G. S. Eisenbarth. “Demonstration of abnormalities in expression of thymic epithelial surface antigens in severe cellular immunodeficiency diseases.” Birth Defects Orig Artic Ser 19, no. 3 (1983): 255–58.Link to Item
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OCHS, H. D., C. G. LINDGREN, R. H. BUCKLEY, and R. J. WEDGWOOD. “ANTIBODY DEFICIENCY WITH NORMAL IMMUNE GLOBULINS - A DEFECT IN IMMUNE REGULATION.” Clinical Research 31, no. 1 (January 1, 1983): A119–A119.Link to Item
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SINDEL, L. J., and R. H. BUCKLEY. “COMPARISON OF CORD AND ADULT T-CELL SUPPRESSOR FUNCTIONS IN 2 ASSAYS OF B-CELL DIFFERENTIATION.” Federation Proceedings 42, no. 4 (January 1, 1983): 953–953.Link to Item
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Schiff, R. I., C. Rudd, R. Johnson, and R. H. Buckley. “Individualization of gamma globulin dosage in patients with humoral immunodeficiency.” Birth Defects Orig Artic Ser 19, no. 3 (1983): 209–12.Link to Item
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BUCKLEY, R. H. “ATOPIC-DERMATITIS - A NEW THERAPEUTIC REGIMEN - REPLY.” Jama Journal of the American Medical Association 250, no. 21 (1983): 2927–2927. https://doi.org/10.1001/jama.1983.03340210024010.Full Text Link to Item
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BUCKLEY, R. H. “POSSIBLE IMMUNOGLOBULIN DEFICIENCY - REPLY.” Jama Journal of the American Medical Association 250, no. 22 (1983): 3047–48. https://doi.org/10.1001/jama.1983.03340220019018.Full Text Link to Item
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Buckley, R. H., and D. Metcalfe. “Food allergy.” Jama 248, no. 20 (November 26, 1982): 2627–31.Link to Item
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Buckley, R. H., and K. P. Mathews. “Common "allergic' skin diseases.” Jama 248, no. 20 (November 26, 1982): 2611–22.Link to Item
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Cooper, M. D., and R. H. Buckley. “Developmental immunology and the immunodeficiency diseases.” Jama 248, no. 20 (November 26, 1982): 2658–69.Link to Item
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Buckley, R. H., H. A. Sampson, P. M. Fisher, W. G. Becker, and L. R. Shirley. “Abnormalities in the regulation of human IgE synthesis.” Ann Allergy 49, no. 2 (August 1982): 67–72.Link to Item
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LoGalbo, P. R., H. A. Sampson, and R. H. Buckley. “Symptomatic giardiasis in three patients with X-linked agammaglobulinemia.” J Pediatr 101, no. 1 (July 1982): 78–80. https://doi.org/10.1016/s0022-3476(82)80188-1.Full Text Link to Item
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Shirley, L. R., R. H. Buckley, M. J. Borowitz, S. I. Welt, and D. D. Kostyu. “Monoclonal immunoglobulin-secreting lymphoma in a patient with severe combined immunodeficiency disease.” Clin Exp Immunol 48, no. 3 (June 1982): 666–74.Link to Item
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Buckley, R. H. “Long term use of intravenous immune globulin in patients with primary immunodeficiency diseases: inadequacy of current dosage practices and approaches to the problem.” J Clin Immunol 2, no. 2 Suppl (April 1982): 15S-21S. https://doi.org/10.1007/BF00918362.Full Text Link to Item
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HAYNES, B. F., R. W. WARREN, R. H. BUCKLEY, J. E. MCCLURE, A. L. GOLDSTEIN, and G. S. EISENBARTH. “COMPLEX GANGLIOSIDES AS MARKERS OF THYMIC EPITHELIUM - DEMONSTRATION OF DEFECTS IN THYMIC EPITHELIUM STRUCTURE AND GANGLIOSIDE EXPRESSION IN SEVERE COMBINED IMMUNODEFICIENCY DISEASE.” Clinical Research 30, no. 2 (January 1, 1982): A350–A350.Link to Item
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LOGALBO, P. R., and R. H. BUCKLEY. “HUMAN CORD BLOOD (CB) LYMPHOCYTE-T HELPER AND SUPPRESSOR PHENOTYPES, IMMUNOGLOBULIN (IG) PRODUCTION, AND EFFECTS ON NORMAL ADULT IG PRODUCTION.” Federation Proceedings 41, no. 3 (January 1, 1982): 799–799.Link to Item
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Shirley, L. R., H. A. Sampson, and R. H. Buckley. “Effects of hydrocortisone (HC) on IgE synthesis by cultured human mononuclear cells (MNC).” Journal of Allergy and Clinical Immunology 69, no. 1 II (January 1, 1982): 258. https://doi.org/10.1016/s0091-6749(62)80540-5.Full Text
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Ammann, A. J., R. F. Ashman, R. H. Buckley, W. R. Hardie, H. J. Krantmann, J. Nelson, H. Ochs, et al. “Use of intravenous gamma-globulin in antibody immunodeficiency: results of a multicenter controlled trial.” Clin Immunol Immunopathol 22, no. 1 (January 1982): 60–67. https://doi.org/10.1016/0090-1229(82)90022-8.Full Text Link to Item
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Sampson, H. A., and R. H. Buckley. “Human IgE synthesis in vitro: a reassessment.” J Immunol 127, no. 3 (September 1981): 829–34.Link to Item
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Gross, S. J., R. H. Buckley, S. S. Wakil, D. C. McAllister, R. J. David, and R. G. Faix. “Elevated IgA concentration in milk produced by mothers delivered of preterm infants.” J Pediatr 99, no. 3 (September 1981): 389–93. https://doi.org/10.1016/s0022-3476(81)80323-x.Full Text Link to Item
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Cohen, M. S., R. E. Isturiz, H. L. Malech, R. K. Root, C. M. Wilfert, L. Gutman, and R. H. Buckley. “Fungal infection in chronic granulomatous disease. The importance of the phagocyte in defense against fungi.” Am J Med 71, no. 1 (July 1981): 59–66. https://doi.org/10.1016/0002-9343(81)90259-x.Full Text Link to Item
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Buckley, R. H., P. M. Fiser, and W. G. Becker. “In vitro studies of IgE synthesis by human blood mononuclear cells.” Fed Proc 40, no. 8 (June 1981): 2167–70.Link to Item
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Buckley, R. H. “Regulation of IgE synthesis: introduction.” Fed Proc 40, no. 8 (June 1981): 2159–61.Link to Item
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Shirley, L Reed, and Rebecca H. Buckley. “967 EFFECTS HYDROCORTISONE AND THEOPHYLLINE CN MONONUCLEAR CELL SUPERNATANT IgE CONCENTRATIONS.” Pediatric Research 15 (April 1981): 603–603. https://doi.org/10.1203/00006450-198104001-00992.Full Text
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Knutsen, A. P., D. F. Merten, and R. H. Buckley. “Colonic nodular lymphoid hyperplasia in a child with antibody deficiency and near-normal immunoglobulins.” J Pediatr 98, no. 3 (March 1981): 420–23. https://doi.org/10.1016/s0022-3476(81)80709-3.Full Text Link to Item
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OCHS, H. D., R. H. BUCKLEY, B. PIROFSKY, S. H. FISCHER, R. H. ROUSELL, C. J. ANDERSON, and R. J. WEDGWOOD. “INTRAVENOUS IMMUNE GLOBULIN IN 10-PERCENT MALTOSE - EVALUATION OF SAFETY AND PATIENT ACCEPTANCE.” Clinical Research 29, no. 1 (January 1, 1981): A90–A90.Link to Item
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Shirley, L. R., and R. H. Buckley. “Effects of hydrocortisone and theophylline on mononuclear cell supernatant IgE concentrations.” Pediatric Research 15, no. 4 II (January 1, 1981): 967.
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Knutsen, A. P., W. F. Rosse, T. R. Kinney, and R. H. Buckley. “Immunologic studies before and after splenectomy in a patient with the Wiskott-Aldrich syndrome.” J Clin Immunol 1, no. 1 (January 1981): 13–19. https://doi.org/10.1007/BF00915472.Full Text Link to Item
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Buckley, R. H. “Presidential address. Reflections on the 1970s and a look to the future.” J Allergy Clin Immunol 66, no. 6 (December 1980): 432–37. https://doi.org/10.1016/0091-6749(80)90002-0.Full Text Link to Item
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Ochs, H. D., R. H. Buckley, B. Pirofsky, S. H. Fischer, R. H. Rousell, C. J. Anderson, and R. J. Wedgwood. “Safety and patient acceptability of intravenous immune globulin in 10% maltose.” Lancet 2, no. 8205 (November 29, 1980): 1158–59. https://doi.org/10.1016/s0140-6736(80)92594-5.Full Text Link to Item
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Hanker, J. S., R. J. Chandross, N. F. Weatherly, J. Laszlo, J. O. Moore, R. H. Buckley, and A. Ottolenghi. “Medusa cells: the morphology and cytochemistry of common amoeboid variants of eosinophils.” Histochem J 12, no. 6 (November 1980): 701–15. https://doi.org/10.1007/BF01012025.Full Text Link to Item
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Gross, S. J., and R. H. Buckley. “IgA in saliva of breast-fed and bottle-fed infants.” Lancet 2, no. 8193 (September 6, 1980): 543. https://doi.org/10.1016/s0140-6736(80)91876-0.Full Text Link to Item
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Josephs, S. H., S. J. Rothman, and R. H. Buckley. “Phenytoin hypersensitivity.” J Allergy Clin Immunol 66, no. 2 (August 1980): 166–72. https://doi.org/10.1016/0091-6749(80)90065-2.Full Text Link to Item
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Josephs, S. H., and R. H. Buckley. “Serum IgD concentrations in normal infants, children, and adults and in patients with elevated IgE.” J Pediatr 96, no. 3 Pt 1 (March 1980): 417–20. https://doi.org/10.1016/s0022-3476(80)80684-6.Full Text Link to Item
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SAMPSON, H. A., and R. H. BUCKLEY. “REGULATION OF IGE SYNTHESIS INVITRO - EFFECTS OF MITOGENS AND IRRADIATION OF T-CELLS.” Federation Proceedings 39, no. 3 (January 1, 1980): 567–567.Link to Item
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Fiser, P. M., and R. H. Buckley. “Human IgE biosynthesis in vitro: studies with atopic and normal blood mononuclear cells and subpopulations.” J Immunol 123, no. 4 (October 1979): 1788–94.Link to Item
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Merten, D. F., R. H. Buckley, P. C. Pratt, E. L. Effmann, and H. Grossman. “Hyperimmunoglobulinemia E syndrome: radiographic observations.” Radiology 132, no. 1 (July 1979): 71–78. https://doi.org/10.1148/132.1.71.Full Text Link to Item
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Herrod, H. G., and R. H. Buckley. “Use of a human plaque-forming cell assay to study peripheral blood bursa-equivalent cell activation and excessive suppressor cell activity in humoral immunodeficiency.” J Clin Invest 63, no. 5 (May 1979): 868–76. https://doi.org/10.1172/JCI109386.Full Text Link to Item
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Hershfield, M. S., N. M. Kredich, D. R. Ownby, H. Ownby, and R. Buckley. “In vivo inactivation of erythrocyte S-adenosylhomocysteine hydrolase by 2'-deoxyadenosine in adenosine deaminase-deficient patients.” J Clin Invest 63, no. 4 (April 1979): 807–11. https://doi.org/10.1172/JCI109367.Full Text Link to Item
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BUCKLEY, R. H. “CHILD WITH ASTHMA.” Drug Therapy 9, no. 4 (January 1, 1979): 75–80.Link to Item
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Buckley, R. H., and M. B. Kardish. “Lymphocyte responses to pollen allergens: Cell requirements and responses to crude timothy and rye and purified rye antigens.” Journal of Allergy and Clinical Immunology 63, no. 3 (January 1, 1979).
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GROSS, S. J., S. WAKIL, R. J. DAVID, R. G. FAIX, and R. H. BUCKLEY. “ELEVATED IMMUNOGLOBULIN IGA IN MILK FROM MOTHERS DELIVERING PRETERM INFANTS.” Pediatric Research 13, no. 4 (January 1, 1979): 449–449.Link to Item
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Buckley, R. H. “Advances in asthma/allergy.” Pediatric Nursing 5, no. 2 (1979): supplB-D.
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Buckley, R. H. “Advances in asthma/allergy.” Pediatr Nurs 5, no. 2 (1979): supplB-D.Link to Item
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Ownby, D. R., and R. H. Buckley. “Lymphocyte responses to ragweed antigens from different sources.” J Allergy Clin Immunol 63, no. 1 (January 1979): 65–66. https://doi.org/10.1016/0091-6749(79)90164-7.Full Text Link to Item
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Herrod, Henry G., Donald B. Perlman, and Rebecca H. Buckley. “702 EVIDENCE FOR EXCESSIVE T SUPPRESSOR CELL ACTIVITY IN X-LINKED IMMUNODEFICIENCY WITH HYPER-IgM.” Pediatric Research 12 (April 1978): 480–480. https://doi.org/10.1203/00006450-197804001-00707.Full Text
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Koren, H. S., D. B. Amos, and R. H. Buckley. “Natural killing in immunodeficient patients.” J Immunol 120, no. 3 (March 1978): 796–99.Link to Item
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Tiller, T. L., and R. H. Buckley. “Transient hypogammaglobulinemia of infancy: review of the literature, clinical and immunologic features of 11 new cases, and long-term follow-up.” J Pediatr 92, no. 3 (March 1978): 347–53. https://doi.org/10.1016/s0022-3476(78)80417-x.Full Text Link to Item
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BECKER, R. L., and R. H. BUCKLEY. “FUNCTIONAL CHARACTERIZATION OF NATURAL KILLING AGAINST A MOUSE FIBROSARCOMA TARGET.” Federation Proceedings 37, no. 6 (January 1, 1978): 1273–1273.Link to Item
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Buckley, R. H., and W. G. Becker. “Abnormalities in the regulation of human IgE synthesis.” Immunol Rev 41 (1978): 288–314. https://doi.org/10.1111/j.1600-065x.1978.tb01469.x.Full Text Link to Item
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Van Metre, T. E., R. H. Buckley, S. C. Bukantz, K. F. Austen, R. E. Reisman, S. O. Freedman, I. L. Bernstein, et al. “Statement by the Executive Committee.” The Journal of Allergy and Clinical Immunology 62, no. 2 (January 1, 1978): 71. https://doi.org/10.1016/0091-6749(78)90080-5.Full Text
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Sanal, S. O., and R. H. Buckley. “Antibody-dependent cellular cytotoxicity in primary immunodeficiency diseases and with normal leukocyte subpopulations. Importance of the type of target.” J Clin Invest 61, no. 1 (January 1978): 1–10. https://doi.org/10.1172/JCI108907.Full Text Link to Item
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Wells, J. V., R. H. Buckley, M. S. Schanfield, and H. H. Fudenberg. “Anaphylactic reactions to plasma infusions in patients with hypogammaglobulinemia and anti-IgA antibodies.” Clin Immunol Immunopathol 8, no. 2 (September 1977): 265–71. https://doi.org/10.1016/0090-1229(77)90116-7.Full Text Link to Item
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Snyderman, R., E. Rogers, and R. H. Buckley. “Abnormalities of leukotaxis in atopic dermatitis.” J Allergy Clin Immunol 60, no. 2 (August 1977): 121–26. https://doi.org/10.1016/0091-6749(77)90037-9.Full Text Link to Item
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Wilfert, C. M., R. H. Buckley, T. Mohanakumar, J. F. Griffith, S. L. Katz, J. K. Whisnant, P. A. Eggleston, et al. “Persistent and fatal central-nervous-system ECHOvirus infections in patients with agammaglobulinemia.” N Engl J Med 296, no. 26 (June 30, 1977): 1485–89. https://doi.org/10.1056/NEJM197706302962601.Full Text Link to Item
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Buckley, R. H. “Immunoreconstitution.” Pediatr Clin North Am 24, no. 2 (May 1977): 313–28. https://doi.org/10.1016/s0031-3955(16)33421-6.Full Text Link to Item
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Buckley, R. H., J. M. MacQueen, and F. E. Ward. “HLA antigens in primary immunodeficiency diseases.” Clin Immunol Immunopathol 7, no. 3 (May 1977): 305–10. https://doi.org/10.1016/0090-1229(77)90061-7.Full Text Link to Item
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BECKER, W. G., and R. H. BUCKLEY. “ALOPECIA-AREATA, HYPOGAMMAGLOBULINEMIA, CONCANAVALIN A (CON A) HYPORESPONSIVENESS, AND AUTOIMMUNE HEMOLYTIC-ANEMIA.” Clinical Research 25, no. 1 (January 1, 1977): A75–A75.Link to Item
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Ownby, D., H. Herrod, and R. H. Buckley. “Mitogen induced DNA synthetic responses of lymphocyte subpopulations in partial DiGeorge syndrome.” Clinical Research 25, no. 1 (January 1, 1977).
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Buckley, R. H., F. Seymour, S. O. Sanal, D. R. Ownby, and W. G. Becker. “Lymphocyte responses to purified ragweed allergens in vitro. I. Proliferative responses in normal, newborn, agammaglobulinemic, and atopic subjects.” J Allergy Clin Immunol 59, no. 1 (January 1977): 70–78. https://doi.org/10.1016/0091-6749(77)90180-4.Full Text Link to Item
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Whisnant, J. K., and R. H. Buckley. “Successful pyrimethamine-sulfadiazine therapy of pneumocystis pneumonia in infants with X-linked immunodeficiency with hyper-IgM.” Natl Cancer Inst Monogr 43 (October 1976): 211–17.Link to Item
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Buckley, R. H. “The functions and measurement of human B- and T-lymphocytes.” J Invest Dermatol 67, no. 3 (September 1976): 381–90. https://doi.org/10.1111/1523-1747.ep12514711.Full Text Link to Item
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Ownby, D. R., S. Pizzo, L. Blackmon, S. A. Gall, and R. H. Buckley. “Severe combined immunodeficiency with leukopenia (reticular dysgenesis) in siblings: immunologic and histopathologic findings.” J Pediatr 89, no. 3 (September 1976): 382–87. https://doi.org/10.1016/s0022-3476(76)80532-x.Full Text Link to Item
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Buckley, R. H., R. B. Gilbertsen, R. I. Schiff, E. Ferreira, S. O. Sanal, and T. A. Waldmann. “Heterogeneity of lymphocyte subpopulations in severe combined immunodeficiency. Evidence against a stem cell defect.” J Clin Invest 58, no. 1 (July 1976): 130–36. https://doi.org/10.1172/JCI108441.Full Text Link to Item
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Buckley, R. H., K. J. Whisnant, R. I. Schiff, R. B. Gilbertsen, A. T. Huang, and M. S. Platt. “Correction of severe combined immunodeficiency by fetal liver cells.” N Engl J Med 294, no. 20 (May 13, 1976): 1076–81. https://doi.org/10.1056/NEJM197605132942002.Full Text Link to Item
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BECKER, W. G., and R. H. BUCKLEY. “OPTIMAL CONDITIONS TO AVOID SELECTIVE LOSSES OF T CELLS ON BOUYANT DENSITY GRADIENTS.” Pediatric Research 10, no. 4 (January 1, 1976): 383–383.Link to Item
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Buckley, R. H., S. O. Sanal, and D. R. Ownby. “Lymphocyte responses to antigen E in normal and in treated and untreated ragweed sensitive subjects.” Journal of Allergy and Clinical Immunology 57, no. 3 (January 1, 1976).
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BLOCH, K. J., E. W. HESS, C. E. REED, R. H. BUCKLEY, L. M. LICHTENSTEIN, P. H. SCHUR, T. S. EDGINGTON, and M. ZIFF. “CLINICAL IMMUNOLOGY - MEETING REPORT OF COMMITTEE-ON-HOSPITAL-BASED-LABORATORY-AND-CLINICAL-IMMUNOLOGY OF AMERICAN-ASSOCIATION-OF-IMMUNOLOGISTS, 1975.” Clinical Immunology and Immunopathology 5, no. 1 (1976): 159–62.Link to Item
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McGeady, S. J., and R. H. Buckley. “Depression of cell-mediated immunity in atopic eczema.” J Allergy Clin Immunol 56, no. 5 (November 1975): 393–406. https://doi.org/10.1016/0091-6749(75)90133-5.Full Text Link to Item
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Schiff, R. I., D. Mercier, and R. H. Buckley. “Inability of gestational hormones to account for the inhibitory effects of pregnancy plasmas on lymphocyte responses in vitro.” Cell Immunol 20, no. 1 (November 1975): 69–80. https://doi.org/10.1016/0008-8749(75)90085-4.Full Text Link to Item
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Buckley, R. H. “Iron deficiency anemia: its relationship to infection susceptibility and host defense.” J Pediatr 86, no. 6 (June 1975): 993–95. https://doi.org/10.1016/s0022-3476(75)80282-4.Full Text Link to Item
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Johnston, R. B., C. M. Wilfert, R. H. Buckley, L. S. Webb, L. R. DcChatelet, and C. E. McCall. “Enhanced bactericidal activity of phagocytes from patients with chronic granulomatous disease in the presence of sulphisoxazole.” Lancet 1, no. 7911 (April 12, 1975): 824–27. https://doi.org/10.1016/s0140-6736(75)93002-0.Full Text Link to Item
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Meuwissen, H. J., B. Pollara, and R. J. Pickering. “Combined immunodeficiency disease associated with adenosine deaminase deficiency. Report on a workshop held in Albany, New York, October 1, 1973.” J Pediatr 86, no. 2 (February 1975): 169–81. https://doi.org/10.1016/s0022-3476(75)80463-x.Full Text Link to Item
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Buckley, R. H. “Plasma therapy in immunodeficiency diseases.” Birth Defects Orig Artic Ser 11, no. 1 (1975): 347–51.Link to Item
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Buckley, R. H. “Bone marrow and thymus transplantation in ataxia-telangiectasia.” Birth Defects Orig Artic Ser 11, no. 1 (1975): 421–24.Link to Item
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Buckley, R. H. “Clinical and immunologic features of selective IgA deficiency.” Birth Defects Orig Artic Ser 11, no. 1 (1975): 134–42.Link to Item
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Buckley, R. H., and S. A. Fiscus. “Serum IgD and IgE concentrations in immunodeficiency diseases.” J Clin Invest 55, no. 1 (January 1975): 157–65. https://doi.org/10.1172/JCI107906.Full Text Link to Item
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Hess, E. W., C. E. Reed, and R. H. Buckley. “Clinical immunology: meeting report of the committee on hospital based laboratory and clinical immunology of the American Association of Immunologists, 1975.” Journal of Immunology 115, no. 2 (January 1, 1975): 609–10.
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SNYDERMAN, R., and R. H. BUCKLEY. “DEFECTS OF MONOCYTE CHEMOTAXIS IN PATIENTS WITH HYPERIMMUNOGLOBULINEMIA E AND UNDUE SUSCEPTIBILITY TO INFECTION.” Clinical Research 23, no. 1 (January 1, 1975): A25–A25.Link to Item
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SNYDERMAN, R., and R. H. BUCKLEY. “DEFECTS OF MONOCYTE CHEMOTAXIS IN PATIENTS WITH HYPERIMMUNOGLOBULINEMIA-E AND UNDUE SUSCEPTIBILITY TO INFECTION.” Journal of Allergy and Clinical Immunology 55, no. 2 (January 1, 1975): 102–3.Link to Item
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WHISNANT, J. K., E. L. TREADWELL, T. MOHANAKUMAR, C. M. WILFERT, and R. H. BUCKLEY. “PROLONGED CNS VIRAL-INFECTION WITH ECHO 30 IN AN AGAMMAGLOBULINEMIC CHILD WITH INTACT CELL-MEDIATED-IMMUNITY.” Pediatric Research 9, no. 4 (January 1, 1975): 336–336.Link to Item
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WHISNANT, J. K., R. B. GILBERTSEN, R. I. SCHIFF, and R. H. BUCKLEY. “CHRONIC GRAFT VERSUS HOST (G-V-H) DISEASE AFTER FETAL LIVER-TRANSPLANTATION IN SEVERE COMBINED IMMUNODEFICIENCY (SCID).” Clinical Research 23, no. 1 (January 1, 1975): A68–A68.Link to Item
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WHISNANT, J. K., R. I. SCHIFF, R. B. GILBERTSEN, M. S. PLATT, and R. H. BUCKLEY. “FETAL LIVER-TRANSPLANTATION IN SEVERE COMBINED IMMUNODEFICIENCY (SCID) - SUCCESS AND GRAFT VERSUS HOST (G-V-H) DISEASE.” Pediatric Research 9, no. 4 (January 1, 1975): 336–336.Link to Item
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Axelsen, N. H., C. H. Kirkpatrick, and R. H. Buckley. “Precipitins to Candida albicans in chronic mucocutaneous candidiasis studied by crossed immunoelectrophoresis with intermediate gel. Correlation with clinical and immunological findings.” Clin Exp Immunol 17, no. 3 (July 1974): 385–94.Link to Item
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Van der Weyden, M. B., R. H. Buckley, and W. N. Kelley. “Molecular form of adenosine deaminase in severe combined immunodeficiency.” Biochem Biophys Res Commun 57, no. 3 (April 8, 1974): 590–95. https://doi.org/10.1016/0006-291x(74)90587-7.Full Text Link to Item
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Schiff, R. I., R. H. Buckley, R. B. Gilbertsen, and R. S. Metzgar. “Membrane receptors and in vitro responsiveness of lymphocytes in human immunodeficiency.” J Immunol 112, no. 1 (January 1974): 376–86.Link to Item
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Buckley, R. H., and D. T. Rowlands. “Agammaglobulinemia, neutropenia, fever, and abdominal pain.” J Allergy Clin Immunol 51, no. 5 (May 1973): 308–18. https://doi.org/10.1016/0091-6749(73)90133-4.Full Text Link to Item
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Buckley, R. H. “Plasma therapy in immunodeficiency diseases.” Am J Dis Child 124, no. 3 (September 1972): 376–81. https://doi.org/10.1001/archpedi.1972.02110150074014.Full Text Link to Item
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Buckley, R. H., R. I. Schiff, and D. B. Amos. “Blocking of autologous and homologous leukocyte responses by human alloimmune plasmas: a possible in vitro correlate of enhancement.” J Immunol 108, no. 1 (January 1972): 34–44.Link to Item
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Buckley, R. H., B. B. Wray, and E. Z. Belmaker. “Extreme hyperimmunoglobulinemia E and undue susceptibility to infection.” Pediatrics 49, no. 1 (January 1972): 59–70.Link to Item
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Buckley, R. H., D. B. Amos, W. B. Kremer, and D. L. Stickel. “Incompatible bone-marrow transplantation in lymphopenic immunologic deficiency. Circumvention of fatal graft-versus-host disease by immunologic enhancement.” N Engl J Med 285, no. 19 (November 4, 1971): 1035–42. https://doi.org/10.1056/NEJM197111042851901.Full Text Link to Item
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Buckley, R. H., W. B. Kremer, D. T. Rowlands, C. C. Huntley, D. B. Amos, and A. T. Huang. “Lymphopenic immunologic deficiency in identical twins: lymphocyte allografting and graft-versus-host disease following treatment with albumin-gradient-separated paternal bone marrow cells.” Clin Exp Immunol 9, no. 3 (September 1971): 289–304.Link to Item
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Marolis, G. B., R. H. Buckley, and J. B. Younger. “Serum immunogbulin cocentrations during normal pregnancy.” Am J Obstet Gynecol 109, no. 7 (April 1, 1971): 971–76. https://doi.org/10.1016/0002-9378(71)90275-4.Full Text Link to Item
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Schwartz, D. P., and R. H. Buckley. “Serum IgE concentrations and skin reactivity to anti-IgE antibody in IgA-deficient patients.” N Engl J Med 284, no. 10 (March 11, 1971): 513–17. https://doi.org/10.1056/NEJM197103112841002.Full Text Link to Item
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Huntley, C. C., J. B. Robbins, A. D. Lyerly, and R. H. Buckley. “Characterization of precipitating antibodies to ruminant serum and milk proteins in humans with selective IgA deficiency.” N Engl J Med 284, no. 1 (January 7, 1971): 7–10. https://doi.org/10.1056/NEJM197101072840102.Full Text Link to Item
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Buckley, R. H., J. B. Younger, and G. W. Brumley. “Evaluation of serum immunoglobulin concentrations in the perinatal period by use of a standardized method of measurement.” J Pediatr 75, no. 6 (December 1969): 1143–48. https://doi.org/10.1016/s0022-3476(69)80370-7.Full Text Link to Item
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Buckley, R. H., and S. C. Dees. “Correlation of milk precipitins with IgA deficiency.” N Engl J Med 281, no. 9 (August 28, 1969): 465–69. https://doi.org/10.1056/NEJM196908282810903.Full Text Link to Item
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Buckley, R. H., S. C. Dees, and W. M. O’Fallon. “Serum immunoglobulins. II. Levels in children subject to recurrent infection.” Pediatrics 42, no. 1 (July 1968): 50–60.Link to Item
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Buckley, R. H., and J. B. Sidbury. “Hereditary alterations in the immune response: coexistence of "agammaglobulinemia", acquired hypogammaglobulinemia and selective immunoglobulin deficiency in a sibship.” Pediatr Res 2, no. 2 (March 1968): 72–84. https://doi.org/10.1203/00006450-196803000-00002.Full Text Link to Item
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Buckley, R. H., S. C. Dees, and W. M. O’Fallon. “Serum immunoglobulins. I. Levels in normal children and in uncomplicated childhood allergy.” Pediatrics 41, no. 3 (March 1968): 600–611.Link to Item
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Buckley, R. H., Z. J. Lucas, B. G. Hattler, C. M. Zmijewski, and D. B. Amos. “Defective cellular immunity associated with chronic mucocutaneous moniliasis and recurrent staphylococcal botryomycosis: immunological reconstitution by allogeneic bone marrow.” Clin Exp Immunol 3, no. 2 (February 1968): 153–69.Link to Item
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Buckley, R. H., and S. C. Dees. “Serum immunoglobulins. 3. Abnormalities associated with chronic urticaria in children.” J Allergy 40, no. 5 (November 1967): 294–303. https://doi.org/10.1016/0021-8707(67)90077-9.Full Text Link to Item
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Buckley, R. H., W. D. Bradford, and S. R. Butcher. “Selective immunoglobulin deficiency associated with thymic alymphoplasia.” Pediatrics 39, no. 4 (April 1967): 506–15.Link to Item
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MILLER, M. E., and R. H. BUCKLEY. “IMMUNOGLOBULIN DEFICIENCIES IN THYMIC ALYMPHOPLASIA.” Pediatrics 40, no. 3P1 (1967): 469.Link to Item
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Metzgar, R. S., and R. H. Buckley. “The development of homologous skin-sensitizing antibodies in experimental thyroiditis.” Int Arch Allergy Appl Immunol 31, no. 2 (1967): 174–83. https://doi.org/10.1159/000229865.Full Text Link to Item
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Buckley, R. H., and S. C. Dees. “Nutritional and antigenic effects of two bovine milk preparations in infants.” J Pediatr 69, no. 2 (August 1966): 238–45. https://doi.org/10.1016/s0022-3476(66)80326-8.Full Text Link to Item
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Buckley, R. H., and R. S. Metzgar. “Reactivity of human IgG antibodies in primate and guinea pig passive anaphylaxis.” International Archives of Allergy and Immunology 29, no. 5 (January 1, 1966): 485–94. https://doi.org/10.1159/000229732.Full Text
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Buckley, R. H., and R. S. Metzgar. “The use of nonhuman primates for studies of reagin.” Journal of Allergy 36, no. 4 (January 1, 1965): 382–96. https://doi.org/10.1016/0021-8707(65)90045-6.Full Text
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Book Sections
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Buckley, R. H., and J. S. Orange. “Primary Immunodeficiency Diseases.” In Middleton’s Allergy: Principles and Practice: Eighth Edition, 2–2:1144–74, 2014. https://doi.org/10.1016/B978-0-323-08593-9.00073-5.Full Text
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Conference Papers
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Thakar, Monica S., Brent Logan, Rebecca H. Buckley, Elie Haddad, Christopher C. Dvorak, Richard J. O’Reilly, Neena Kapoor, et al. “Transplantation Outcomes for Children with Severe Combined Immune Deficiency (SCID) Have Improved over Time: A 36-Year Summary Report By the Primary Immune Deficiency Treatment Consortium (PIDTC).” In Biology of Blood and Marrow Transplantation, 26:S18–19. ELSEVIER SCIENCE INC, 2020.Link to Item
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Baloh, Carolyn H., Michele R. Henson, Anupama Reddy, Rebecca H. Buckley, and Patricia L. Lugar. “A study of cancer incidence in the most common immunodeficiency, common variable immunodeficiency (CVID).” In Journal of Allergy and Clinical Immunology, 143:AB80–AB80. MOSBY-ELSEVIER, 2019.Link to Item
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Kohn, Donald B., Kit L. Shaw, Elizabeth K. Garabedian, Denise A. Carbonaro-Sarracino, Theodore B. Moore, Satiro De Oliveira, Gay M. Crooks, et al. “Autologous Ex Vivo Lentiviral Gene Therapy for the Treatment of Severe Combined Immune Deficiency Due to Adenosine Deaminase Deficiency.” In Journal of Clinical Immunology, 39:S42–44. SPRINGER/PLENUM PUBLISHERS, 2019.Link to Item
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Baloh, Carolyn H., Rebecca Buckley, and Patricia Lugar. “Fertility, Pregnancy, and Progeny Outcomes in a Large Academic Cohort of Patients with Antibody Deficiencies.” In Journal of Clinical Immunology, 39:S135–S135, 2019.Link to Item
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Kohn, Donald B., Kit L. Shaw, Elizabeth Garabedian, Denise A. Carbonaro-Sarracino, Theodore B. Moore, Satiro De Oliveira, Gay M. Crooks, et al. “Autologous ex vivo lentiviral gene therapy for the treatment of Severe Combined Immune Deficiency due to Adenosine Deaminase Deficiency (ADA-SCID) Improves B Cell Function.” In Journal of Clinical Immunology, 39:S44–45, 2019.Link to Item
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Heimall, Jennifer R., Nicola Wright, Holly Miller, Morton J. Cowan, Donald B. Kohn, Sung-Yun Pai, Elie Haddad, et al. “Diagnosis and Pre-Transplant Management of SCID Patients in the Era of Newborn Screening: A Survey of Practices in the Primary Immune Deficiency Treatment Consortium.” In Journal of Clinical Immunology, 38:442–43. SPRINGER/PLENUM PUBLISHERS, 2018.Link to Item
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Baloh, Carolyn H., Anupama Reddy, Rebecca H. Buckley, and Patricia L. Lugar. “Characterization of pediatric onset common variable immunodeficiency (CVID) in a large cohort.” In Journal of Allergy and Clinical Immunology, 141:AB21–AB21. Elsevier BV, 2018. https://doi.org/10.1016/j.jaci.2017.12.068.Full Text
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Berthe, C., S. Bourbonnais, R. E. Parrott, A. St-Denis, M. Dela Cruz, D. De Waele, J. A. Joly, et al. “Aberrant T cell activation and exhaustion develops in poorly reconstituted SCID survivors after transplant and correlates with the absence of conditioning regimen: a Primary Immune Deficiency Treatment Consortium (PIDTC) study.” In Journal of Clinical Immunology, 38:425–26, 2018.Link to Item
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Kuo, Caroline Y., Jennifer M. Puck, Brent R. Logan, Elie Haddad, Geoffrey D. E. Cuvelier, Ziyan Yin, Susan E. Prockop, Rebecca Buckley, Linda M. Griffith, and Donald B. Kohn. “Adenosine Deaminase (ADA)-Deficient Severe Combined Immune Deficiency (SCID): Analysis of Cases Enrolled in Protocols of the Primary Immune Deficiency Treatment Consortium (PIDTC).” In Journal of Clinical Immunology, 38:342–43, 2018.Link to Item
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Patel, Niraj, Jennifer R. Heimall, Beth Younger, Brittany Neelands, David Morris, Rebecca Buckley, and Monica Thakar. “Safety and Efficacy of Hizentra (R) in Pediatric Hematopoietic Stem Cell Recipients.” In Journal of Clinical Immunology, 38:403–403, 2018.Link to Item
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Haddad, Elie, Brent R. Logan, Linda M. Griffith, Rebecca H. Buckley, Roberta E. Parrott, Christopher C. Dvorak, Jennifer Puck, et al. “Genotype, Phenotype and T Cell Counts at One Year Predict Survival and Long Term Immune Reconstitution after Transplantation in Severe Combined Immune Deficiency (SCID)-The Primary Immune Deficiency Treatment Consortium (PIDTC).” In Biology of Blood and Marrow Transplantation, 23:S101–2, 2017.Link to Item
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Leven, Emily A., Patrick Maffucci, Hans D. Ochs, Paul R. Scholl, Rebecca H. Buckley, Ramsay L. Fuleihan, Raif S. Geha, et al. “Hyper IgM Syndrome: a Report from the USIDNET Registry.” In J Clin Immunol, 36:490–501, 2016. https://doi.org/10.1007/s10875-016-0291-4.Full Text Link to Item
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Heimall, Jennifer, Brent R. Logan, Morton J. Cowan, Luigi D. Notarangelo, Jennifer Puck, Thomas Fleisher, Linda M. Griffith, et al. “Poor T Cell Reconstitution at 100 Days after T Cell-Replete Hematopoietic Cell Transplantation (HCT) for SCID Is Associated with Later Risk of Death or Need for 2nd Transplant in the 6901 Prospective Study of the Pidtc.” In Biology of Blood and Marrow Transplantation, 22:S101–2. Elsevier BV, 2016. https://doi.org/10.1016/j.bbmt.2015.11.404.Full Text
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Heimall, Jennifer, Brent R. Logan, Morton J. Cowan, Luigi D. Notarangelo, Linda M. Griffith, Jennifer Puck, Suhag Parikh, et al. “Early Hematopoietic Cell Transplant (HCT) Outcomes of Children with Severe Combined Immunodeficiency Disease (SCID): The First Seventy Four Patients of the Primary Immune Deficiency Treatment Consortium (PIDTC) Prospective Study 6901.” In Biology of Blood and Marrow Transplantation, 21:S289–91. Elsevier BV, 2015. https://doi.org/10.1016/j.bbmt.2014.11.459.Full Text
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Caldwell, Jason W., Talal I. Mousallem, Natalia Dixon, Rebecca H. Buckley, and Suhag H. Parikh. “Dna Ligase IV Deficiency With Novel Compound Heterozygous Mutations.” In Journal of Clinical Immunology, 34:391–391. SPRINGER/PLENUM PUBLISHERS, 2014.Link to Item
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Mousallem, Talal, Jialong Yang, Thomas J. Urban, Hongxia Wang, Roberta E. Parrott, Joseph L. Roberts, Rebecca H. Buckley, Xiaoping Zhong, and David B. Goldstein. “Whole-Exome Sequencing Reveals IKBKB As a Cause of Combined Immunodeficiency.” In Journal of Allergy and Clinical Immunology, 133:AB399–AB399. Elsevier BV, 2014. https://doi.org/10.1016/j.jaci.2013.12.1053.Full Text
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Pai, Sung-Yun, Brent R. Logan, Linda M. Griffith, Rebecca H. Buckley, Roberta E. Parrott, Christopher C. Dvorak, Neena Kapoor, et al. “Retrospective Study of 240 Patients with Severe Combined Immunodeficiency Transplanted from 2000-2009: A Report from the Primary Immune Deficiency Treatment Consortium of North America.” In Biology of Blood and Marrow Transplantation, 20:S24–25. Elsevier BV, 2014. https://doi.org/10.1016/j.bbmt.2013.12.007.Full Text
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Smith, Lauren, Rebecca H. Buckley, and Patricia L. Lugar. “Diagnostic Immunization With Bacteriophage ΦX 174 In Patients With Common Variable Immunodeficiency/Hypogammaglobulinemia.” In Journal of Allergy and Clinical Immunology, 133:AB69–AB69. Elsevier BV, 2014. https://doi.org/10.1016/j.jaci.2013.12.269.Full Text
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Dvorak, Christopher C., Morton J. Cowan, Brent R. Logan, Linda Griffith, Jennifer Puck, Luigi D. Notarangelo, Donald B. Kohn, et al. “The Natural History of Children with Severe Combined Immunodeficiency Disease (SCID): The First Fifty Patients of the Primary Immune Deficiency Treatment Consortium (PIDTC) Prospective Study 6901.” In Biology of Blood and Marrow Transplantation, 19:S161–62. Elsevier BV, 2013. https://doi.org/10.1016/j.bbmt.2012.11.125.Full Text
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Mousallem, Talal, Thomas J. Urban, Joseph L. Roberts, Roberta E. Parrott, David B. Goldstein, and Rebecca H. Buckley. “Next Generation Sequencing May Be More Efficient and Economical Than Targeted Gene Testing in Patients with Primary Immune Deficiency (PID).” In Journal of Allergy and Clinical Immunology, 131:AB52–AB52. Elsevier BV, 2013. https://doi.org/10.1016/j.jaci.2012.12.870.Full Text
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Roberts, J. L., R. H. Buckley, B. Luo, J. Pei, A. Lapidus, S. Peri, Q. Wei, et al. “CD45 Deficiency Caused by Uniparental Disomy, a Novel Cause of Severe Combined Immunodeficiency.” In Journal of Allergy and Clinical Immunology, 129:AB84–AB84. Elsevier BV, 2012. https://doi.org/10.1016/j.jaci.2011.12.639.Full Text
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Szabolcs, Paul, Rebecca Buckley, Robert Duane Davis, Judith Voynow, Jerelyn Moffet, Antony Jeyaraj, and David W. Zaas. “Tandem HLA-Mismatched Cadaveric Unrelated Donor Lung Transplant Followed by CD3-and CD19-Depleted Bone Marrow Transplant From the Same Donor Permits Withdrawal of Systemic Immunosuppression with Graft Acceptance and Functional Immune Reconstitution.” In Blood, 118:460–61. AMER SOC HEMATOLOGY, 2011.Link to Item
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Adeli, M., and R. Buckley. “Occurrence and Significance of Lymphopenia in the NICU, PICU and Well Baby Nursery.” In Journal of Allergy and Clinical Immunology, 125:AB10–AB10. Elsevier BV, 2010. https://doi.org/10.1016/j.jaci.2009.12.071.Full Text
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Buckley, Rebecca H., and J Buren Sidbury. “On Assessing Immunocompetence.” In Journal of Allergy and Clinical Immunology, 123:S3–4. MOSBY-ELSEVIER, 2009.Link to Item
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Buckley, Rebecca H. “Specific Antibody Synthesis in Patients with Immunoglobulin Deficits.” In Journal of Allergy and Clinical Immunology, 123:S3–S3, 2009.Link to Item
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MCWILLIAMS, L., S. MCGOLDRICK, M. RAILEY, and R. BUCKLEY. “Family History and Low Absolute Lymphocyte Count (ALC) as Diagnostic Clues for Severe Combined Immunodeficiency (SCID).” In Journal of Allergy and Clinical Immunology, 121:S166–S166. Elsevier BV, 2008. https://doi.org/10.1016/j.jaci.2007.12.612.Full Text
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RAILEY, M., and R. BUCKLEY. “Long-term Clinical Outcome of Patients with Severe Combined Immunodeficiency (SCID) after Non-Ablative Related Donor Bone Marrow Transplantation.” In Journal of Allergy and Clinical Immunology, 121:S82–S82. Elsevier BV, 2008. https://doi.org/10.1016/j.jaci.2007.12.329.Full Text
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Keller, Michael D., Dong-Feng Chen, Nancy L. Reinsmoen, Na Liu, and Rebecca Buckley. “34-OR.” In Human Immunology, 67:S34–S34. Elsevier BV, 2006. https://doi.org/10.1016/j.humimm.2006.08.042.Full Text
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Boyle, J. M., and R. H. Buckley. “Population Prevalence of Diagnosed Primary Immune Deficiency Diseases in the United States.” In Journal of Allergy and Clinical Immunology, 117:S105–S105. Elsevier BV, 2006. https://doi.org/10.1016/j.jaci.2005.12.422.Full Text
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Palmer, K., T. D. Green, J. L. Roberts, E. Sajaroff, M. Cooney, K. Coyne, D. Chen, N. L. Reinsmoen, and R. H. Buckley. “Clinical and Immunologic Manifestations of Transplacentally Acquired Maternal T-Cells in SCID.” In Journal of Allergy and Clinical Immunology, 117:S108–S108. Elsevier BV, 2006. https://doi.org/10.1016/j.jaci.2005.12.433.Full Text
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Sajaroff, E. O., and R. H. Buckley. “Natural Killer T (NKT) Cell Development in Severe Combined Immunodeficiency (SCID) After T Cell Depleted Haploidentical Bone Marrow Transplantation (BMT).” In Journal of Allergy and Clinical Immunology, 117:S325–S325. Elsevier BV, 2006. https://doi.org/10.1016/j.jaci.2005.12.1282.Full Text
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Robertson, K. A., S. Alturi, K. Neville, M. Davis, F. E. Marshalleck, R. H. Buckley, and R. P. Nelson. “EBV-associated leiomyomas following haploidentical transplantation for X-linked severe combined immunodeficiency disease.” In Biology of Blood and Marrow Transplantation, 11:82–82. Elsevier BV, 2005. https://doi.org/10.1016/j.bbmt.2004.12.241.Full Text
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Chinen, J., J. M. Puck, J. Davis, G. F. Linton, N. L. Whiting-Theobald, P. C. Woltz, R. H. Buckley, and H. L. Malech. “Ex vivo gene therapy of a preadolescent with x-linked severe combined immunodeficiency.” In Blood, 104:120A-120A. AMER SOC HEMATOLOGY, 2004.Link to Item
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Buckley, R. H. “The use of intravenous immunoglobulin for allogeneic stem cell transplantation: the US experience.” In Intravenous Immunoglobulins in the Third Millennium, edited by M. C. Dalakas and P. J. Spath, 81–84. PARTHENON PUBLISHING GROUP LTD, 2004.Link to Item
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Sorrentino, B. P., T. H. Lu, J. Ihle, R. H. Buckley, and J. M. Cunningham. “A clinical attempt to treat JAK3-deficient SCID using retroviral-mediated gene transfer to bone marrow CD34+ cells.” In Molecular Therapy, 7:S449–S449. NATURE PUBLISHING GROUP, 2003.Link to Item
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Kalman, L. V., M. L. Lindegren, L. J. Kobrynski, C. A. Moore, S. A. Rasmussen, R. Vogt, T. Spira, et al. “Framework for assessing impact and identifying public health interventions for severe combined immunodeficiency (SCID).” In American Journal of Human Genetics, 71:376–376, 2002.Link to Item
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Puck, J. M., E. J. Tsail, T. Levin, M. R. Kirby, A. P. Hsu, N. E. Seidel, C. Porada, E. Zanjani, D. M. Bodine, and H. L. Malech. “Development of XSCID gene therapy for posttransplant patients with persistent immune defects.” In Blood Cells Molecules and Diseases, 28:343–343, 2002.Link to Item
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Hsu, A. P., S. M. Anderson, R. Buckley, F. Candotti, G. Uzel, and J. M. Puck. “Genotypic diagnosis of T-B+ SCID by functional assay.” In American Journal of Human Genetics, 69:361–361, 2001.Link to Item
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Buckley, Rebecca H. “Emergence of CD45RA+ and CD62L+ Blood T Cells in Infants with Severe Combined Immunodeficiency (SCID) Given HLA-Identical or Haploidentical T Cell-Depleted Bone Marrow Stem Cells.” In Pediatric Research, 45:8A-8A. Springer Science and Business Media LLC, 1999. https://doi.org/10.1203/00006450-199904020-00056.Full Text
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WINKELSTEIN, J. “Chronic granulomatous disease: Report on a registry of 368 patients.” In Molecular Immunology, 35:795–795. Elsevier BV, 1998. https://doi.org/10.1016/s0161-5890(98)90515-6.Full Text
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Boeck, A., R. I. Schiff, and R. H. Buckley. “Gastroesophageal reflux and severe combined immunodeficiency.” In Journal of Allergy and Clinical Immunology, 97:832–832, 1996.Link to Item
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Broome, C. B., and R. H. Buckley. “Effects of allergy/asthma drugs on IgE synthesis.” In Journal of Allergy and Clinical Immunology, 97:416–416, 1996.Link to Item
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Markert, M. L., C. M. Davis, F. E. Ward, D. D. Kostyu, R. H. Buckley, S. E. Schiff, T. J. Watson, T. M. McLaughin, L. P. Hale, and B. F. Haynes. “Development of normal T-cell function and TCR repertoire after post-natal thymic transplantation for DiGeorge syndrome.” In Journal of Allergy and Clinical Immunology, 97:836–836, 1996.Link to Item
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Roberts, J. L., J. J. OShea, J. M. Puck, and R. H. Buckley. “Deficiency of janus kinase 3 (Jak3) protein in severe combined immunodeficiency (SCID).” In Journal of Allergy and Clinical Immunology, 97:828–828, 1996.Link to Item
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Schiff, S. E., and R. H. Buckley. “Expression of unique cell surface proteins on B cells of patients with severe combined immunodeficiency (SCID).” In Journal of Allergy and Clinical Immunology, 97:977–977, 1996.Link to Item
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Buckley, R. H. “The hyper-IgE syndrome.” In Pediatric Dermatology, edited by A. M. Pierini, R. GarciaDiazdePierini, and R. E. Bustamante, 1073:21–26. ELSEVIER SCIENCE PUBL B V, 1995.Link to Item
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Buckley, R. H. “Breakthroughs in the understanding and therapy of primary immunodeficiency.” In Pediatric Dermatology, edited by A. M. Pierini, R. GarciaDiazdePierini, and R. E. Bustamante, 1073:293–99. ELSEVIER SCIENCE PUBL B V, 1995.Link to Item
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BUCKLEY, R. H., R. I. SCHIFF, S. E. SCHIFF, M. L. MARKERT, L. W. WILLIAMS, T. O. HARVILLE, and J. M. PUCK. “SEVERE COMBINED IMMUNODEFICIENCY (SCID) - GENETIC, PHENOTYPIC AND FUNCTIONAL DIVERSITY IN 79 INFANTS.” In Journal of Allergy and Clinical Immunology, 95:232–232, 1995.Link to Item
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MARKERT, M. L., F. E. WARD, D. KOSTYU, R. H. BUCKLEY, S. E. SCHIFF, J. J. H. BLEESING, C. B. BROOME, et al. “DEVELOPMENT OF T-CELL FUNCTION AFTER POSTNATAL THYMIC TRANSPLANTATION FOR DIGEORGE-SYNDROME.” In Journal of Allergy and Clinical Immunology, 95:142–142, 1995.Link to Item
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TANG, M. L. K., L. W. WILLIAMS, R. I. SCHIFF, M. L. MARKERT, T. O. HARVILLE, and R. H. BUCKLEY. “PNEUMATOSIS-INTESTINALIS IN CHILDREN WITH PRIMARY IMMUNODEFICIENCY.” In Journal of Allergy and Clinical Immunology, 95:237–237, 1995.Link to Item
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WINKELSTEIN, J. A., J. BOYLE, R. H. BUCKLEY, J. T. CURNUTTE, H. DICKLER, J. I. GALLIN, R. B. JOHNSTON, H. D. OCHS, and P. QUIE. “REPORT ON THE NATIONAL-CHRONIC-GRANULOMATOUS-DISEASE-(CGD)-REGISTRY.” In Pediatric Research, 37:A11–A11, 1995.Link to Item
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BUCKLEY, R. H., J. KLUGE, and A. LEVINE. “IGE SYNTHESIS BY B-CELLS FROM IMMUNODEFICIENCY PATIENTS.” In Journal of Allergy and Clinical Immunology, 93:219–219, 1994.Link to Item
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NASH, D. R., A. D. LEVINE, and R. H. BUCKLEY. “B-CELLS FROM MOST PATIENTS WITH EITHER X-LINKED (XL) OR AUTOSOMAL RECESSIVE (AR) FORMS OF SEVERE COMBINED IMMUNODEFICIENCY (SCID) PRODUCE IGE AND OTHER ISOTYPES NORMALLY WHEN STIMULATED WITH ANTI-CD40 MAB AND IL-4.” In Journal of Allergy and Clinical Immunology, 93:273–273, 1994.Link to Item
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SCHIFF, S. E., and R. H. BUCKLEY. “VARIATION IN NATURAL-KILLER (NK) LYMPHOCYTE FUNCTION AMONG THE DIFFERENT MOLECULAR-FORMS OF SEVERE COMBINED IMMUNODEFICIENCY (SCID).” In Journal of Allergy and Clinical Immunology, 93:273–273, 1994.Link to Item
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BUCKLEY, R. H., S. E. SCHIFF, R. I. SCHIFF, J. L. ROBERTS, M. L. MARKERT, W. PETERS, L. W. WILLIAMS, and F. E. WARD. “HAPLOIDENTICAL BONE-MARROW STEM-CELL TRANSPLANTATION IN HUMAN SEVERE COMBINED IMMUNODEFICIENCY.” In Seminars in Hematology, 30:92–104. W B SAUNDERS CO, 1993.Link to Item
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BUCKLEY, R., S. SCHIFF, R. SCHIFF, M. L. MARKERT, L. WILLIAMS, and H. OCHS. “B-CELL FUNCTION AFTER HAPLOIDENTICAL STEM-CELL TRANSPLANTATION IN HUMAN SEVERE COMBINED IMMUNODEFICIENCY (SCID).” In Journal of Immunology, 150:A95–A95. AMER ASSOC IMMUNOLOGISTS, 1993.Link to Item
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BUCKLEY, R. H., S. E. SCHIFF, R. I. SCHIFF, M. L. MARKERT, L. W. WILLIAMS, and F. E. WARD. “CELLULAR THERAPY FOR SEVERE COMBINED IMMUNODEFICIENCY (SCID) - ANALYSIS AT 10 YEARS.” In Journal of Allergy and Clinical Immunology, 91:322–322, 1993.Link to Item
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COUNTY, J., and R. H. BUCKLEY. “T-CELL FUNCTION IN COMMON VARIABLE IMMUNODEFICIENCY (CVID).” In Journal of Allergy and Clinical Immunology, 91:149–149, 1993.Link to Item
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BERLIN, P. J., R. I. SCHIFF, and R. H. BUCKLEY. “ABNORMAL HUMORAL RESPONSE TO PNEUMOCOCCAL IMMUNIZATION IN C2 DEFICIENCY.” In Journal of Allergy and Clinical Immunology, 89:271–271, 1992.Link to Item
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BUCKLEY, R. H., D. L. GOSSAGE, and S. E. SCHIFF. “USE OF 2 PARENT HAPLOIDENTICAL STEM-CELL TRANSPLANTATION TO OVERCOME RESISTANCE TO ENGRAFTMENT IN T-CELL DEFECTS.” In Journal of Allergy and Clinical Immunology, 89:166–166, 1992.Link to Item
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BUCKLEY, R. “IMMUNODEFICIENCY AND ALLERGY.” In Progress in Allergy and Clinical Immunology, Vol 2, Kyoto, 693–97, 1992.Link to Item
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TIONGKO, M. C., and R. H. BUCKLEY. “DECREASED EXPRESSION OF CD45RO AND INCREASED EXPRESSION OF CD23 ON T-CELLS FROM PATIENTS WITH ATOPIC-DERMATITIS.” In Journal of Allergy and Clinical Immunology, 89:200–200, 1992.Link to Item
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OCHS, H. D., R. H. BUCKLEY, R. H. KOBAYASHI, A. L. KOBAYASHI, R. U. SORENSEN, and M. S. HERSHFIELD. “ANTIBODY-RESPONSES TO BACTERIOPHAGE PHI-X174 IN PATIENTS WITH ADENOSINE-DEAMINASE DEFICIENCY.” In Clinical Research, 39:A57–A57. SLACK INC, 1991.Link to Item
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HAYWARD, A. R., S. SCHIFF, and R. H. BUCKLEY. “T-CELL RECONSTITUTION OF SCID RECIPIENTS GRAFTED WITH T-DEPLETED BONE-MARROW.” In Progress in Immune Deficiency Iii, 173:245–46, 1991.Link to Item
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COURNOYER, D., M. SCARPA, K. MOORE, R. H. BUCKLEY, J. W. BELMONT, and C. T. CASKEY. “RETROVIRAL GENE-TRANSFER OF HUMAN ADENOSINE-DEAMINASE INTO HEMATOPOIETIC-CELLS.” In Experimental Hematology Today 1989, 100–106, 1990.Link to Item
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BUCKLEY, R. H. “IGE AND THE PATHOGENESIS OF ATOPIC ECZEMA.” In Progress in Allergy and Clinical Immunology, 336–39, 1989.Link to Item
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CLAASSEN, J. L., A. D. LEVINE, and R. H. BUCKLEY. “INDUCTION OF HUMAN IGE AND IGG SYNTHESIS BY INVITRO STIMULATION OF BLOOD MONONUCLEAR-CELLS (MNC) WITH RECOMBINANT HUMAN INTERLEUKIN-4 (RHIL-4).” In Journal of Allergy and Clinical Immunology, 83:298–298, 1989.Link to Item
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SHEERIN, K. A., and R. H. BUCKLEY. “ANTIBODY-RESPONSES IN THE HYPER IMMUNOGLOBULINEMIA-E (HYPER IGE) SYNDROME.” In Journal of Allergy and Clinical Immunology, 83:288–288, 1989.Link to Item
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Barrett, M. J., S. E. Schiff, P. C. Kidd, and R. H. Buckley. “272 Accelerated development of immunity following transplantation of maternal marrow stem cells into infants with severe combined immunodeficiency (SCID) and transplacentally acquired lymphoid chimerism.” In Journal of Allergy and Clinical Immunology, 81:236–236. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90506-4.Full Text
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Buckley, R. H., S. Schiff, R. Johnson, S. Bigner, and H. D. Ochs. “270 B cell function in severe combined immunodeficiency (SCID) Following HLA-identical and haploidentical marrow transplantation.” In Journal of Allergy and Clinical Immunology, 81:235–235. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90504-0.Full Text
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Claassen, J. L., R. H. Kobayashi, A. L. Kobayashi, M. S. Hershfield, R. I. Schiff, and R. H. Buckley. “276 Antigen-specific humoral and cellular immune responses during treatment of adenosine deaminase deficient severe combined immunodeficiency (ADA-SCID) with polyethylene glycol-modified bovine adenosine deaminase (PEG-ADA).” In Journal of Allergy and Clinical Immunology, 81:237–237. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90510-6.Full Text
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Ebbeling, W. L., L. B. Sehwartz, and R. H. Buckley. “69 Comparison of plasma histamine (H) and tryptase levels following double-blind placebo-controlled food challenges (DBPCFC'S) in patients with asthma (AS) and/or atopic dermatitis (AD).” In Journal of Allergy and Clinical Immunology, 81:186–186. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90306-5.Full Text
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Gaines, A. D., and R. H. Buckley. “339 Deficient responses to polysaccharide antigens and to bacteriophage φ × 174 in association with functional asplenia.” In Journal of Allergy and Clinical Immunology, 81:253–253. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90573-8.Full Text
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Roberts, J. L., D. J. Volkman, and R. H. Buckley. “273 Modified T cell MHC restriction following successful haploidentical bone marrow stem cell transplantation in severe combined immunodeficiency disease (SCID).” In Journal of Allergy and Clinical Immunology, 81:236–236. Elsevier BV, 1988. https://doi.org/10.1016/0091-6749(88)90507-6.Full Text
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HERSHFIELD, M. S., R. H. BUCKLEY, M. L. GREENBERG, A. L. MELTON, R. H. KOBAYASHI, A. L. KOBAYASHI, R. SCHIFF, J. KURTZBERG, M. L. MARKERT, and A. ABUCHOWSKI. “TREATMENT OF ADENOSINE-DEAMINASE DEFICIENCY WITH POLYETHYLENE-GLYCOL MODIFIED ADENOSINE-DEAMINASE (PEG-ADA).” In Clinical Research, 35:A593–A593. SLACK INC, 1987.Link to Item
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MELTON, A., M. S. HERSHFIELD, M. L. GREENBERG, C. HATEM, M. L. MARKERT, J. KURTZBERG, A. ABUCHOWSKI, and R. H. BUCKLEY. “TREATMENT OF ADENOSINE DEAMINASE-DEFICIENT SEVERE COMBINED IMMUNE-DEFICIENCY (ADA-SCID) WITH POLYETHYLENE GLYCOL-MODIFIED BOVINE ADENOSINE-DEAMINASE (PEG-ADA).” In Journal of Allergy and Clinical Immunology, 79:252–252. MOSBY-YEAR BOOK INC, 1987.Link to Item
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EBBELING, W., P. S. GERBER, M. BARRETT, P. KIDD, and R. H. BUCKLEY. “ACQUIRED-IMMUNODEFICIENCY-SYNDROME (AIDS) PRESENTING AS PANHYPOGAMMAGLOBULINEMIA IN 2 INFANTS.” In Journal of Allergy and Clinical Immunology, 79:136–136, 1987.Link to Item
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GERBER, P. S., A. MELTON, S. E. SCHIFF, B. F. HAYNES, and R. H. BUCKLEY. “TREATMENT OF GRAFT-VERSUS-HOST DISEASE (GVHD) IN DIGEORGE SYNDROME WITH ANTI-HUMAN T12 MONOCLONAL-ANTIBODY (T12 MAB).” In Journal of Allergy and Clinical Immunology, 79:251–251, 1987.Link to Item
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WILLIAMS, L. W., H. A. SAMPSON, and R. H. BUCKLEY. “IGG SUBCLASS DEVELOPMENT FOLLOWING SUCCESSFUL BONE-MARROW TRANSPLANTATION (BMT) IN SEVERE COMBINED IMMUNODEFICIENCY DISEASE (SCID).” In Journal of Allergy and Clinical Immunology, 79:187–187, 1987.Link to Item
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MARKERT, M. L., M. S. HERSHFIELD, S. E. SCHIFF, H. A. SAMPSON, R. I. SCHIFF, and R. H. BUCKLEY. “IMMUNODEFICIENCY WITH PURINE SALVAGE PATHWAY ENZYME DEFICIENCIES - EVALUATION OF THERAPIES.” In Journal of Allergy and Clinical Immunology, 77:190–190. MOSBY-YEAR BOOK INC, 1986.Link to Item
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EBBELING, W. L., C. H. INGOLD, L. R. FAHRNER, and R. H. BUCKLEY. “ELEVATED NATURAL-KILLER (NK) CELL-FUNCTION IN COMBINED CARTILAGE HAIR HYPOPLASIA (CHH) AND ROTHMUND-THOMSON SYNDROME (R-TS).” In Journal of Allergy and Clinical Immunology, 77:190–190, 1986.Link to Item
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SCHIFF, S. E., H. A. SAMPSON, and R. H. BUCKLEY. “RESPONSES TO RECIPIENT AND DONOR B-CELLS BY GENETICALLY DONOR T-CELLS FROM HUMAN HAPLOIDENTICAL CHIMERAS.” In Pediatric Research, 20:A299–A299, 1986.Link to Item
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BJORKANDER, J., L. HAMMARSTROM, C. SMITH, R. BUCKLEY, C. CUNNINGHAMRUNDLES, and L. HANSON. “131 Antibody deficiency syndromes with anti-IgA antibodies and successful immunoglobulin prophylaxis.” In Journal of Allergy and Clinical Immunology, 75:137–137. Elsevier BV, 1985. https://doi.org/10.1016/0091-6749(85)90266-0.Full Text
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BUCKLEY, R., S. SCHIFF, D. MILLER, and C. INGOLD. “64 Lymphocyte responses to pollen allergens: Effect of polymerized allergen immunotherapy.” In Journal of Allergy and Clinical Immunology, 75:120–120. Elsevier BV, 1985. https://doi.org/10.1016/0091-6749(85)90199-x.Full Text
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BURKS, A., H. SAMPSON, and R. BUCKLEY. “333 Anaphylactic reactions in common variable agammaglobulinemia (CVA): Detection of IgE and IgG antibodies in an ELISA assay.” In Journal of Allergy and Clinical Immunology, 75:188–188. Elsevier BV, 1985. https://doi.org/10.1016/0091-6749(85)90468-3.Full Text
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GHORY, P., S. SCHIFF, and R. BUCKLEY. “339 Appearance of multiple paraproteins during early engraftment of soy lectin T cell depleted haploidentical bone marrow cells in severe combined immunodeficiency (SCID).” In Journal of Allergy and Clinical Immunology, 75:189–189. Elsevier BV, 1985. https://doi.org/10.1016/0091-6749(85)90474-9.Full Text
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HELM, R., R. BUCKLEY, N. ADKINSONJR, D. SQUILLACE, G. GLEICH, and J. YUNGINGER. “133 Variability in the quantitation of IgE protein in cell culture supernatants.” In Journal of Allergy and Clinical Immunology, 75:138–138. Elsevier BV, 1985. https://doi.org/10.1016/0091-6749(85)90268-4.Full Text
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BUCKLEY, R., S. GARD, R. SCHIFF, and H. SAMPSON. “178 T cells and subsets in a large population of primary immunodeficiency patients.” In Journal of Allergy and Clinical Immunology, 71:133–133. Elsevier BV, 1983. https://doi.org/10.1016/0091-6749(83)90302-0.Full Text
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SCHIFF, R., C. RUDD, R. JOHNSON, and R. BUCKLEY. “181 Individualization of gamma globulin dosage in patients with humoral immunodeficiency.” In Journal of Allergy and Clinical Immunology, 71:134–134. Elsevier BV, 1983. https://doi.org/10.1016/0091-6749(83)90305-6.Full Text
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SINDEL, L., R. BUCKLEY, S. GARD, A. HUANG, F. WARD, R. JOHNSON, and H. KOREN. “180 Severe combined immunodeficiency (SCID) with natural killer (NK) cell predominance: Effects of bone marrow transplantation.” In Journal of Allergy and Clinical Immunology, 71:133–133. Elsevier BV, 1983. https://doi.org/10.1016/0091-6749(83)90304-4.Full Text
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WARREN, R., B. HAYNES, and R. BUCKLEY. “303 Synovial lymphocyte phenotypes in the inflammatory arthritis of x-linked agammaglobulinemia.” In Journal of Allergy and Clinical Immunology, 71:164–164. Elsevier BV, 1983. https://doi.org/10.1016/0091-6749(83)90427-x.Full Text
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SAMPSON, H. A., and R. H. BUCKLEY. “REGULATION OF IGE SYNTHESIS INVITRO - EFFECTS OF MITOGENS AND IRRADIATION OF T-CELLS.” In Journal of Allergy and Clinical Immunology, 65:166–166, 1980.Link to Item
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BUCKLEY, R. H., and M. B. KARDISH. “LYMPHOCYTE-RESPONSES TO POLLEN ALLERGENS - CELL REQUIREMENTS AND RESPONSES TO CRUDE TIMOTHY AND RYE AND PURIFIED RYE ANTIGENS.” In Journal of Allergy and Clinical Immunology, 63:139–40, 1979.Link to Item
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FISER, P. M., and R. H. BUCKLEY. “HUMAN IGE BIOSYNTHESIS INVITRO - STUDIES OF LYMPHOCYTE SUB-POPULATIONS AND CELL-CELL INTERACTIONS.” In Journal of Allergy and Clinical Immunology, 63:145–145, 1979.Link to Item
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HERROD, H. G., J. L. SULLIVAN, R. H. BUCKLEY, G. SCHIFFMAN, H. A. SAMPSON, and R. J. WEDGWOOD. “ANTIBODY DEFICIENCY WITH NEAR-NORMAL IMMUNOGLOBULINS.” In Journal of Allergy and Clinical Immunology, 63:188–188, 1979.Link to Item
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JOSEPHS, S. H., and R. H. BUCKLEY. “ELEVATED SERUM IGD IN CHILDREN WITH HIGH SERUM IGE CONCENTRATIONS.” In Journal of Allergy and Clinical Immunology, 63:137–38, 1979.Link to Item
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BECKER, W., and R. BUCKLEY. “161. In vitro studies of human IgE biosynthesis.” In Journal of Allergy and Clinical Immunology, 61:177–177. Elsevier BV, 1978. https://doi.org/10.1016/0091-6749(78)90401-3.Full Text
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HERROD, H., and R. BUCKLEY. “50. Detection of suppressor cells in human peripheral blood by means of a plaque-forming cell assay.” In Journal of Allergy and Clinical Immunology, 61:143–143. Elsevier BV, 1978. https://doi.org/10.1016/0091-6749(78)90289-0.Full Text
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OWNBY, D. R., and R. H. BUCKLEY. “LYMPHOCYTE SUBPOPULATION RESPONSES TO PURIFIED RAGWEED ANTIGENS INVITRO.” In Annals of Allergy, 38:306–306, 1977.Link to Item
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BUCKLEY, R. H., S. O. SANAL, D. R. OWNBY, W. G. BECKER, and F. SEYMOUR. “LYMPHOCYTE-RESPONSES TO ANTIGEN-E IN NORMAL AND IN TREATED AND UNTREATED RAGWEED-SENSITIVE SUBJECTS.” In Journal of Allergy and Clinical Immunology, 57:202–202, 1976.Link to Item
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MCGEADY, S. J., and R. H. BUCKLEY. “STUDIES OF CELL-MEDIATED IMMUNE FUNCTION IN ATOPIC ECZEMA.” In Journal of Allergy and Clinical Immunology, 53:72–73, 1974.Link to Item
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SCHIFF, R. I., D. MERCIER, and R. H. BUCKLEY. “EFFECTS OF GESTATIONAL HORMONES ON HUMAN LYMPHOCYTE-RESPONSES INVITRO.” In Federation Proceedings, 33:749–749, 1974.Link to Item
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SCHIFF, R., R. BUCKLEY, and R. METZGAR. “Membrane receptors and in vitro responsiveness of lymphocytes in immunodeficiency.” In Journal of Allergy and Clinical Immunology, 51:125–125. Elsevier BV, 1973. https://doi.org/10.1016/s0091-6749(73)80100-9.Full Text
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JOHNSTON, R. B., C. M. WILFERT, L. S. WEBB, R. BUCKLEY, L. R. DECHATELET, and C. E. MCCALL. “ENHANCED BACTERICIDAL ACTIVITY OF LEUKOCYTES FROM CHILDREN WITH CHRONIC GRANULOMATOUS DISEASE (CGD) IN PRESENCE OF SULFISOXAZOLE (SSX).” In Pediatric Research, 7:364–364, 1973.Link to Item
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Buckley, Rebecca H., D Bernard Amos, William P. Kremer, and Delford L. Stickel. “Incompatible bone marrow transplantation in lymphopenic immunologic deficiency.” In Pediatric Research, 5:379–379. Springer Science and Business Media LLC, 1971. https://doi.org/10.1203/00006450-197108000-00034.Full Text
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BUCKLEY, R. H., B. B. WRAY, and E. Z. BELMAKER. “EXTREME HYPERIMMUNOGLOBULINEMIA-E AND UNDUE SUSCEPTIBILITY TO INFECTION.” In Journal of Allergy, 47:108, 1971.Link to Item
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BUCKLEY, R. H., R. I. SCHIFF, and D. B. AMOS. “HUMAN ENHANCING ANTIBODIES IN-VITRO STUDIES.” In Federation Proceedings, 30:A358, 1971.Link to Item
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Kattwinkel, John, and Rebecca H. Buckley. “A Sensitive Microtiter Test for Detecting Rheumatoid Factor in Children.” In Pediatric Research, 4:436–436. Springer Science and Business Media LLC, 1970. https://doi.org/10.1203/00006450-197009000-00012.Full Text
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SCHWARTZ, D. P., R. H. BUCKLEY, and M. H. ROURK. “INFLUENCE OF AGE AND ATOPY ON SKIN REACTIVITY TO ANTI-IGE ANTIBODY IN INFANTS AND CHILDREN.” In Journal of Allergy, 45:124, 1970.Link to Item
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BUCKLEY, R. H. “SPECIFIC ANTIBODY SYNTHESIS IN PATIENTS WITH IMMUNOGLOBULIN DEFICITS.” In Journal of Allergy, 43:187, 1969.Link to Item
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BUCKLEY, R. H., Z. J. LUCAS, B. G. HATTLER, C. M. ZMIJEWSK, and D. B. AMOS. “CELLULAR IMMUNE DEFECT - IMMUNOLOGIC RECONSTITUTION BY ALLOGENEIC BONE MARROW.” In Pediatric Research, 2:299, 1968.Link to Item
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WUBBENA, P. F., and R. H. BUCKLEY. “SALIVARY IMMUNOGLOBULIN A - MILK-SPECIFIC ACTIVITY DETECTED BY AGAR-GEL PRECIPITATION AND CARBODIIMIDE HEMAGGLUTINATION.” In Southern Medical Journal, 61:1341, 1968.Link to Item
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BUCKLEY, R. H., and S. C. DEES. “IMMUNOGLOBULIN ABNORMALITIES ASSOCIATED WITH CHRONIC URTICARIA.” In Journal of Allergy, 39:101, 1967.Link to Item
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SIDBURY, J. B., R. H. BUCKLEY, and P. E. HOCHSTEI. “STUDIES ON DEFECT IN SEPTIC GRANULOMATOSIS.” In Southern Medical Journal, 60:1361, 1967.Link to Item
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BUCKLEY, R. H., and R. S. METZGAR. “SKIN-SENSITIZING ANTIBODIES IN EXPERIMENTAL AUTOIMMUNE THYROIDITIS.” In Journal of Allergy, 37:118, 1966.Link to Item
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BUCKLEY, R. H., and R. S. METZGAR. “USE OF NON-HUMAN PRIMATES FOR STUDIES OF REAGIN.” In Federation Proceedings, 23:402, 1964.Link to Item
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