Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy.
Publication
, Journal Article
Schachner, L; Lazarus, GS; Dembitzer, H
Published in: Br J Dermatol
January 1977
A patient with epidermolysis bullosa hereditaria letalis had the characteristic electron microscopic lesions not only in the skin, but also in the gastro-intestinal, genito-urinary and respiratory tracts. Administration of dexamethasone to this patients resulted in a significant decrease in the blistering. Although the patient died, long term survival in this disease is not rare. We report that staining tissue specimens from patients with epidermolysis bullosa with fluorescein-labelled bullous pemphigoid antibody is a reliable method for differentiating between junctional and dystrophic disease.
Duke Scholars
Published In
Br J Dermatol
DOI
ISSN
0007-0963
Publication Date
January 1977
Volume
96
Issue
1
Start / End Page
51 / 58
Location
England
Related Subject Headings
- Urogenital System
- Skin
- Respiratory System
- Infant, Newborn
- Infant
- Humans
- Female
- Epidermolysis Bullosa
- Digestive System
- Dexamethasone
Citation
APA
Chicago
ICMJE
MLA
NLM
Schachner, L., Lazarus, G. S., & Dembitzer, H. (1977). Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy. Br J Dermatol, 96(1), 51–58. https://doi.org/10.1111/j.1365-2133.1977.tb05185.x
Schachner, L., G. S. Lazarus, and H. Dembitzer. “Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy.” Br J Dermatol 96, no. 1 (January 1977): 51–58. https://doi.org/10.1111/j.1365-2133.1977.tb05185.x.
Schachner L, Lazarus GS, Dembitzer H. Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy. Br J Dermatol. 1977 Jan;96(1):51–8.
Schachner, L., et al. “Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy.” Br J Dermatol, vol. 96, no. 1, Jan. 1977, pp. 51–58. Pubmed, doi:10.1111/j.1365-2133.1977.tb05185.x.
Schachner L, Lazarus GS, Dembitzer H. Epidermolysis bullosa hereditaria letalis: pathology, natural history and therapy. Br J Dermatol. 1977 Jan;96(1):51–58.
Published In
Br J Dermatol
DOI
ISSN
0007-0963
Publication Date
January 1977
Volume
96
Issue
1
Start / End Page
51 / 58
Location
England
Related Subject Headings
- Urogenital System
- Skin
- Respiratory System
- Infant, Newborn
- Infant
- Humans
- Female
- Epidermolysis Bullosa
- Digestive System
- Dexamethasone