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A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings

Publication ,  Journal Article
Ly, JD; Subramanian, S; Greene, S; Rajan, D; Kofler, J; Zuccoli, G
Published in: Journal of Pediatric Neurology
January 1, 2018

An 11-year-old girl presented with vomiting, nystagmus, and ataxia. MRI showed a partially enhancing medulla oblongata lesion and an adjacent nonenhancing cystic exophytic lesion. An exophytic brainstem tumor was suspected. Histologically, the lesion was identified as a neurenteric cyst (NC). On retrospective review, the NC was connected to the brainstem by a subtle sinus tract. This led to brainstem inflammation which reversed once the cyst was resected. We describe an unreported case of a patient with a NC at the craniocervical junction connected to the brainstem through a sinus tract and discuss the possible embryological abnormality and imaging features.

Duke Scholars

Published In

Journal of Pediatric Neurology

DOI

EISSN

1875-9041

ISSN

1304-2580

Publication Date

January 1, 2018

Volume

16

Issue

6

Start / End Page

404 / 407

Related Subject Headings

  • Neurology & Neurosurgery
  • 3213 Paediatrics
  • 3209 Neurosciences
  • 11 Medical and Health Sciences
 

Citation

APA
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ICMJE
MLA
NLM
Ly, J. D., Subramanian, S., Greene, S., Rajan, D., Kofler, J., & Zuccoli, G. (2018). A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings. Journal of Pediatric Neurology, 16(6), 404–407. https://doi.org/10.1055/s-0038-1639375
Ly, J. D., S. Subramanian, S. Greene, D. Rajan, J. Kofler, and G. Zuccoli. “A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings.” Journal of Pediatric Neurology 16, no. 6 (January 1, 2018): 404–7. https://doi.org/10.1055/s-0038-1639375.
Ly JD, Subramanian S, Greene S, Rajan D, Kofler J, Zuccoli G. A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings. Journal of Pediatric Neurology. 2018 Jan 1;16(6):404–7.
Ly, J. D., et al. “A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings.” Journal of Pediatric Neurology, vol. 16, no. 6, Jan. 2018, pp. 404–07. Scopus, doi:10.1055/s-0038-1639375.
Ly JD, Subramanian S, Greene S, Rajan D, Kofler J, Zuccoli G. A Neurenteric Cyst Presenting as a Brainstem Tumor: Imaging and Clinical Findings. Journal of Pediatric Neurology. 2018 Jan 1;16(6):404–407.
Journal cover image

Published In

Journal of Pediatric Neurology

DOI

EISSN

1875-9041

ISSN

1304-2580

Publication Date

January 1, 2018

Volume

16

Issue

6

Start / End Page

404 / 407

Related Subject Headings

  • Neurology & Neurosurgery
  • 3213 Paediatrics
  • 3209 Neurosciences
  • 11 Medical and Health Sciences