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Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta.

Publication ,  Journal Article
Davis, RP; Andersen, ND; Ganapathi, AM; DiBernardo, LR; Hughes, GC
Published in: J Heart Valve Dis
November 2015

Osteogenesis imperfecta (OI) is an inherited connective tissue disorder caused by the defective synthesis of type I collagen. The clinical phenotype is dominated by bone fragility, but cardiovascular tissue involvement has also been reported. Here, the case is described of a 37-year-old man with OI who presented with aortic insufficiency, bicuspid aortic valve, dilated aortic root, and anomalous right coronary artery. The patient was treated successfully with a mechanical valved conduit aortic root replacement and anomalous coronary artery unroofing and reimplantation. This case highlights the feasibility of complex surgical repairs in this population, as well as challenges surrounding the choice of valve prosthesis given the congenital bone fragility and predilection for fractures.

Duke Scholars

Published In

J Heart Valve Dis

ISSN

0966-8519

Publication Date

November 2015

Volume

24

Issue

6

Start / End Page

666 / 668

Location

England

Related Subject Headings

  • Respiratory System
  • 1102 Cardiorespiratory Medicine and Haematology
 

Citation

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ICMJE
MLA
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Davis, R. P., Andersen, N. D., Ganapathi, A. M., DiBernardo, L. R., & Hughes, G. C. (2015). Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta. J Heart Valve Dis, 24(6), 666–668.
Davis, Robert Patrick, Nicholas D. Andersen, Asvin M. Ganapathi, Louis R. DiBernardo, and G Chad Hughes. “Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta.J Heart Valve Dis 24, no. 6 (November 2015): 666–68.
Davis RP, Andersen ND, Ganapathi AM, DiBernardo LR, Hughes GC. Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta. J Heart Valve Dis. 2015 Nov;24(6):666–8.
Davis, Robert Patrick, et al. “Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta.J Heart Valve Dis, vol. 24, no. 6, Nov. 2015, pp. 666–68.
Davis RP, Andersen ND, Ganapathi AM, DiBernardo LR, Hughes GC. Repair of Bicuspid Aortic Valve Syndrome with Anomalous Right Coronary Artery in Osteogenesis Imperfecta. J Heart Valve Dis. 2015 Nov;24(6):666–668.

Published In

J Heart Valve Dis

ISSN

0966-8519

Publication Date

November 2015

Volume

24

Issue

6

Start / End Page

666 / 668

Location

England

Related Subject Headings

  • Respiratory System
  • 1102 Cardiorespiratory Medicine and Haematology