
Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration.
Publication
, Journal Article
Ferrara, J; Gupta, D; Foster, E; Garman, K; Stacy, M
Published in: Mov Disord
April 30, 2008
We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.
Duke Scholars
Published In
Mov Disord
DOI
EISSN
1531-8257
Publication Date
April 30, 2008
Volume
23
Issue
6
Start / End Page
875 / 878
Location
United States
Related Subject Headings
- alpha 1-Antitrypsin Deficiency
- Substantia Nigra
- Oculomotor Muscles
- Neurology & Neurosurgery
- Middle Aged
- Magnetic Resonance Imaging
- Liver Cirrhosis
- Humans
- Hepatolenticular Degeneration
- Globus Pallidus
Citation
APA
Chicago
ICMJE
MLA
NLM
Ferrara, J., Gupta, D., Foster, E., Garman, K., & Stacy, M. (2008). Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration. Mov Disord, 23(6), 875–878. https://doi.org/10.1002/mds.21841
Ferrara, Joseph, Deepak Gupta, Emily Foster, Katherine Garman, and Mark Stacy. “Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration.” Mov Disord 23, no. 6 (April 30, 2008): 875–78. https://doi.org/10.1002/mds.21841.
Ferrara J, Gupta D, Foster E, Garman K, Stacy M. Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration. Mov Disord. 2008 Apr 30;23(6):875–8.
Ferrara, Joseph, et al. “Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration.” Mov Disord, vol. 23, no. 6, Apr. 2008, pp. 875–78. Pubmed, doi:10.1002/mds.21841.
Ferrara J, Gupta D, Foster E, Garman K, Stacy M. Extraocular muscle dystonia due to acquired (non-Wilsonian) hepatocerebral degeneration. Mov Disord. 2008 Apr 30;23(6):875–878.

Published In
Mov Disord
DOI
EISSN
1531-8257
Publication Date
April 30, 2008
Volume
23
Issue
6
Start / End Page
875 / 878
Location
United States
Related Subject Headings
- alpha 1-Antitrypsin Deficiency
- Substantia Nigra
- Oculomotor Muscles
- Neurology & Neurosurgery
- Middle Aged
- Magnetic Resonance Imaging
- Liver Cirrhosis
- Humans
- Hepatolenticular Degeneration
- Globus Pallidus